Retroperitoneal nodal aplasia, asplenia, chylous effusion and lymphatic dysplasia: an acquired immunodeficiency syndrome?

Abstract:

:Two adult patients (one in Italy and the other in the USA) are described with similar findings of paraaortic nodal aplasia, asplenism, multiple serous and chylous effusions, and retroperitoneal lymphatic dysplasia. Although the clinical courses are incomplete, this unusual constellation of signs in the setting of normal peripheral lymph trunks suggest an acquired rather than inborn anomaly and possibly a variant acquired immunodeficiency syndrome.

journal_name

Lymphology

journal_title

Lymphology

authors

Carini L,Meregaglia LD,Galli C,Segalini G,Strada M,Jones J,Witte MH,Witte CL

subject

Has Abstract

pub_date

1985-03-01 00:00:00

pages

31-6

issue

1

eissn

0024-7766

issn

2522-7963

journal_volume

18

pub_type

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