Abstract:
:A case of Rasmussen encephalitis with bilateral involvement and onset at age 2 years is reviewed. Rasmussen encephalitis is a rare progressive disease that causes intractable seizures, cognitive decline, and inflammatory changes in the brain. The neurologic involvement is characteristically unilateral. Bilateral involvement in this case was suspected within 5 months of presentation and was confirmed by bilateral frontal lobe biopsies. The severity and progression of the disease in this case was remarkable and resulted in the patient's death by age 5 years, despite numerous attempted therapeutic interventions. Autopsy findings confirmed the diagnosis of Rasmussen encephalitis with bilateral involvement.
journal_name
Epilepsiajournal_title
Epilepsiaauthors
Tobias SM,Robitaille Y,Hickey WF,Rhodes CH,Nordgren R,Andermann Fdoi
10.1046/j.1528-1157.2003.36602.xsubject
Has Abstractpub_date
2003-01-01 00:00:00pages
127-30issue
1eissn
0013-9580issn
1528-1167pii
epi36602journal_volume
44pub_type
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