Osteogenesis imperfecta with joint contractures: bruck syndrome.

Abstract:

:We describe an Egyptian boy with osteogenesis imperfecta who was born with thumb contractures and bilateral antecubital pterygia. He was seen at 16 months of age with femur and tibial fractures, thoracic vertebral compression fractures, scoliosis and Wormian bones. The findings are consistent with a diagnosis of Bruck syndrome.

journal_name

Pediatr Radiol

journal_title

Pediatric radiology

authors

Blacksin MF,Pletcher BA,David M

doi

10.1007/s002470050309

subject

Has Abstract

pub_date

1998-02-01 00:00:00

pages

117-9

issue

2

eissn

0301-0449

issn

1432-1998

journal_volume

28

pub_type

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