Primary hypergammaglobulinemic purpura associated with IgG2 deficiency. A case report.

Abstract:

:Hypergammaglobulinemic purpura is a rare disease in children. We report a case of a 12 year-old girl with a history of frequent infections. We found the presence of IgG2 deficiency despite polyclonal hypergammaglobulinemia. An IgG subclass determination should be obtained in every child with polyclonal hypergammaglobulinemia and features of immunodeficiency.

journal_name

Clin Exp Rheumatol

authors

Venuta A,Penza R,Cellini M,Garetti E,Bergomi A,Pastorelli S,Massolo F

subject

Has Abstract

pub_date

1995-09-01 00:00:00

pages

663-5

issue

5

eissn

0392-856X

issn

1593-098X

journal_volume

13

pub_type

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