Abstract:
RATIONALE:Malformative uropathies represent a major cause of Chronic Kidney Disease (CKD) in children. Genitourinary system is the most frequent and sever affected in Prune-Belly syndrome cases. That is why the findings of early diagnosis and vigilant monitoring for these situations remain a major challenge for the medical team. PATIENT CONCERNS:We present the clinical course of a 10 years old child with diagnosis of Prune-Belly syndrome. A urinary tract abnormality was suspected starting 25 weeks of gestation, when a routine ultrasound showed oligohydramnios, increased size urinary bladder, bilateral hydronephrosis and megaureters, thin abdominal wall. DIAGNOSIS:Prenatal suspicion of Prune-Belly syndrome plays a deciding role in renal disease progression. A detailed clinical exam at birth established the diagnosis of Prune-Belly syndrome. Renal ultrasound confirmed bilateral grade III hydronephrosis and megaureters, with empty bladder, suggesting an obstruction at this level. A persistent urachus was confirmed by catheterization. Later it was used for imaging study that showed bilateral high grade reflux. INTERVENTIONS:The main goal of any treatment is to preserve kidney function. Treatment options depend on the clinical picture. The pregnancy was closely monitorized, but fetal distress appeared so early labor was induced at 32 weeks. At beginning a temporary catheter was placed into the urachus which expressed urine. The urachus drain was left in place until the age of 6 weeks, when a bilateral ureterostomy was performed. Skeletal and genital malformations were present too; the child has undergone several surgeries to solve these abnormalities. OUTCOMES:At the age of 10 years, he is a well-adapted child. He has had fewer than 3 urinary tract infections per year. Long term follow-up showed a relatively slow decline in the estimated Glomerular Filtration Rate in our child (62 ml/1.73m/min). LESSONS:This case suggests that induced early labor could prove beneficial for early upper urinary tract decompression through earlier access to surgery. This is an option especially in situations or region where vesicoureteric or vesicoamniotic shunt placement is not available.
journal_name
Medicine (Baltimore)journal_title
Medicineauthors
Cornel A,Duicu C,Delean D,Bulata B,Starcea Mdoi
10.1097/MD.0000000000016745subject
Has Abstractpub_date
2019-08-01 00:00:00pages
e16745issue
33eissn
0025-7974issn
1536-5964pii
00005792-201908160-00024journal_volume
98pub_type
杂志文章相关文献
MEDICINE文献大全abstract:BACKGROUND:Recently, many kinds of cages for cervical fusion have been developed to avoid the related complications caused by tricortical iliac crest graft. The existing literature has reported the excellent clinical efficacy and superior fusion rate. However, various types of cages have their own disadvantages. Which ...
journal_title:Medicine
pub_type: 临床试验,杂志文章
doi:10.1097/MD.0000000000017935
更新日期:2019-11-01 00:00:00
abstract::This study aims to explore the principles of clinical classification and individualized treatment of basicranial artery injuries based on its anatomical correlation.The data of 172 patients with various types of basicranial artery injuries were retrospectively analyzed. Among these patients, 128 patients were male and...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000014732
更新日期:2019-03-01 00:00:00
abstract::The aim of the present study was to assess the effect of Endostar and temozolomide or dacarbazine plus 5-fluorouracil (5-FU) in patients with advanced pancreatic neuroendocrine tumors (pNETs).Phase II study of 14 patients with locally advanced or metastatic well-differentiated pNETs treated between April 2013 and Sept...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000012750
更新日期:2018-11-01 00:00:00
abstract::We investigated the role of F-18 fluorodeoxyglucose (FDG)-positron emission tomography (PET)/computed tomography (CT) for the differential diagnosis of malignant and benign pleural effusion. We studied 36 consecutive patients with histologically proven cancer (excluding malignant mesothelioma) who underwent FDG-PET/CT...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000001010
更新日期:2015-07-01 00:00:00
abstract::Enterovirus (EV) infection is common among children and adolescents. Few studies have investigated the relationship of depression after EV infection. This study explores an association between EV infection and subsequent depression in children and adolescents and assesses the risk of depression after EV infection with...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000005983
更新日期:2017-02-01 00:00:00
abstract:INTRODUCTION:Benign prostatic hyperplasia, bladder outlet obstruction, and overactive bladder are major causes of lower urinary tract symptoms (LUTS). Tumor compression of the urinary bladder resulting in LUTS was clinically observed. Gastrointestinal stromal tumors (GISTs) presenting with LUTS have not been reported b...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000018103
更新日期:2019-12-01 00:00:00
abstract:BACKGROUND:The relative efficacy of antihypertensive drugs/combinations is not well known. Identifying the most effective ones and the patients' characteristics associated with best performance of the drugs will improve management of hypertensive patients. OBJECTIVE:To assess the blood pressure (BP) reduction attribut...
journal_title:Medicine
pub_type: 杂志文章,meta分析,评审
doi:10.1097/MD.0000000000004071
更新日期:2016-07-01 00:00:00
abstract::Endothelial dysfunction and chronic inflammatory process are prevalent in patients with end-stage renal disease (ESRD) on maintenance hemodialysis (HD). The aim of this study was to evaluate the acute and short-term effects of online hemodiafiltration (OL-HDF) versus conventional HD on endothelial function and inflamm...
journal_title:Medicine
pub_type: 杂志文章,随机对照试验
doi:10.1097/MD.0000000000003440
更新日期:2016-04-01 00:00:00
abstract::Cherubism is a rare, nonneoplastic, self-limiting fibro-osseous that occurs in children. Affected children usually appear normal at birth. Lesions are characterized by the replacement of bone with fibrovascular tissue containing many multinucleated giant cells. Most studies have reported cherubism to be familial and w...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000002120
更新日期:2015-12-01 00:00:00
abstract:RATIONALE:Garden type I femoral neck fractures are incomplete stable fractures with impaction in valgus fractures that the question of whether there exists Garden type I femoral neck fracture is currently uncertain. There is still disagreement on the existence of the Garden type I fractures. PATIENT CONCERNS:Herein we...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000012876
更新日期:2018-10-01 00:00:00
abstract:BACKGROUND:A carcinoma ex pleomorphic adenoma (CXPA) is an epithelial malignancy arising in or from a benign pleomorphic salivary adenoma. The parotid gland is the most common location of CXPAs. Minor salivary gland CXPAs of the nasal cavity are exceedingly rare, with only 6 documented in the literature. METHODS AND R...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000005004
更新日期:2016-09-01 00:00:00
abstract::It is known that many medical adverse events can be caused by nonsteroidal anti-inflammatory drugs (NSAIDs); however, epidemiologic evidence has not granted an affirmative relationship between NSAID use and the risk of end-stage renal disease (ESRD). We aimed to investigate the relationship in a Chinese population bet...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000001362
更新日期:2015-09-01 00:00:00
abstract::Meta-analyses have found conflicting results with respect to the use of progesterone or progesterone plus estrogen as luteal phase support for in vitro fertilization (IVF) protocols involving gonadotropins and/or gonadotropin-releasing hormone analogs. The aim of the present study was to perform an updated meta-analys...
journal_title:Medicine
pub_type: 杂志文章,meta分析,评审
doi:10.1097/MD.0000000000000459
更新日期:2015-02-01 00:00:00
abstract::Recent advances in breast cancer management might make the use of postmastectomy radiotherapy (PMRT) redundant in the treatment of pT1/T2N1 patients. We investigated the impact of PMRT on disease-free survival (DFS) in these patients who have a low risk of locoregional recurrence (LRR) after contemporary multidiscipli...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000001259
更新日期:2015-08-01 00:00:00
abstract::The importance of bedside assistants has been well established in various robotic procedures. However, the effect of assistants on the surgical outcomes of thyroid surgery remains unclear. We investigated the effects of a dedicated robot assistant (DRA) in robotic thyroidectomy. We also evaluated the learning curve of...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000022133
更新日期:2020-09-04 00:00:00
abstract::To investigate the differences in bone mineral density between patients with liver cirrhosis and healthy control, and to analyze the risk factors of hepatic osteoporosis in patients with HBV related liver cirrhosis.A total of 189 patients with liver cirrhosis and 207 health controls were enrolled. The bone mineral den...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000016628
更新日期:2019-08-01 00:00:00
abstract:RATIONALE:Small-cell lung cancer (SCLC) is a common pathological type of lung cancer, but appendiceal metastasis of SCLC was rare. At present, clinical studies on the maintenance therapy of SCLC have not reached a significant conclusion. PATIENT CONCERNS:We reported on a 52-year-old man who diagnosed as extensive stag...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000015333
更新日期:2019-04-01 00:00:00
abstract::Drug dependence, which can exist concurrently with chronic pain, is seen as one of the major causes of rapidly increasing medical expenses. However, drug dependence in patients with chronic pain has not been evaluated. The aim of this study was to identify the risk factors for drug dependence in patients with chronic ...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000012748
更新日期:2018-10-01 00:00:00
abstract:BACKGROUND:Many observational studies have reported an association between weight fluctuation and all-cause mortality. However, the conclusions obtained from these studies have been unclear. OBJECTIVE:The current meta-analysis aimed to clarify the association between weight fluctuation and all-cause mortality. DATA S...
journal_title:Medicine
pub_type: 杂志文章,meta分析
doi:10.1097/MD.0000000000017513
更新日期:2019-10-01 00:00:00
abstract:BACKGROUND:the difference in the risk of thyroid malignancy for patients with multinodular goiter (MNG) and solitary nodular goiter (SNG) remains controversial. Although total thyroidectomy (TT) is the current preferred surgical option for MNG, permanent hypothyroidism in these patients may be a concern. Therefore, we ...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000004194
更新日期:2016-07-01 00:00:00
abstract::In a review of endocarditis caused by fastidious, slow-growing gram-negative rods, similarities in the spectrum of disease overshadow differences among cases grouped by specific organisms. Cardiobacterium hominis, Actinobacillus actinomycetemcomitans and Haemophilus species usually seed previously damaged cardiac valv...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/00005792-197903000-00003
更新日期:1979-03-01 00:00:00
abstract::The aim of this study was to identify any changes that occur in the retinal nerve fiber layer (RNFL) and ganglion cell-inner plexiform layer (GC-IPL) in patients with exudative age-related macular degeneration (AMD) during treatment with anti-vascular endothelial growth factor (VEGF) injections.Patients were enrolled ...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000019955
更新日期:2020-04-01 00:00:00
abstract::We conducted the current study to investigate the clinical, laboratory, and histologic features at presentation and the outcome of renal sarcoidosis (RS). Exhaustive retrospective data were collected by the French Sarcoidosis Group. Forty-seven adult patients were assessed (30 male/17 female, M/F ratio: 1.76). Median ...
journal_title:Medicine
pub_type: 杂志文章,多中心研究
doi:10.1097/MD.0b013e31819de50f
更新日期:2009-03-01 00:00:00
abstract:RATIONALE:Hepatoblastoma is a rare malignancy. Approximately 100 cases are diagnosed yearly in the United States. The highest incidence occurs in infants and in children younger than 5 years. Cases involving patients older than 5 years are very rare. We describe the case of a patient who was diagnosed with hepatoblasto...
journal_title:Medicine
pub_type: 杂志文章,评审
doi:10.1097/MD.0000000000005858
更新日期:2017-01-01 00:00:00
abstract:BACKGROUND:Ischemic stroke often leads to lifelong disability or death in stroke patients. It is one of the most common causes of death and disability worldwide, so it is a global health problem. The objective of this protocol is to provide the methods for using overview and network meta-analysis to identify the more e...
journal_title:Medicine
pub_type: 杂志文章,meta分析
doi:10.1097/MD.0000000000015384
更新日期:2019-04-01 00:00:00
abstract:INTRODUCTION:Hemorrhagic shock and encephalopathy syndrome (HSES) is a type of acute encephalopathy mainly seen in infants. It is a syndrome encompassing an onset of high fever, disturbance of consciousness, convulsion, and shock that rapidly progresses to watery diarrhea and liver and renal dysfunctions. It is extreme...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000015012
更新日期:2019-04-01 00:00:00
abstract:RATIONALE:Splenosis is the heterotopic auto-transplantation of the splenic tissues. Gastric splenosis in a rare location mimics a gastrointestinal stromal tumor (GIST). Gastric splenosis with hemangioma has not been reported throughout the literature. PATIENT CONCERNS:We report a case of a 74-year-old schistosomiasis ...
journal_title:Medicine
pub_type: 杂志文章,评审
doi:10.1097/MD.0000000000011461
更新日期:2018-07-01 00:00:00
abstract::We evaluated the utility of left atrial volume index (LAVI) and markers of coagulation and hemostatic activation (MOCHA) in cryptogenic stroke (CS) patients to identify those more likely to have subsequent diagnosis of atrial fibrillation (AF), malignancy or recurrent stroke during follow-up.Consecutive CS patients wh...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000013830
更新日期:2018-12-01 00:00:00
abstract:BACKGROUND:Extracorporeal shockwave lithotripsy (ESWL) has gained worldwide popularity as one of the most commonly used minimally invasive management of urinary tract stones. The objective of this study was to evaluate the efficacy and safety of ESWL for patients with kidney stones (KS). MATERIALS AND METHODS:This pro...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000021910
更新日期:2020-09-18 00:00:00
abstract::The aim of this study was to investigate the relationships between blood-brain barrier (BBB) dysfunction, intrathecal IgG synthesis, and brain glucose consumption as detectable by means of serum/cerebrospinal fluid (CSF) albumin index (Qalb) and IgG index [(CSF IgG/serum IgG) × Serum albumin/CSF albumin)] and 2-deoxy-...
journal_title:Medicine
pub_type: 杂志文章
doi:10.1097/MD.0000000000004206
更新日期:2016-09-01 00:00:00