Mal de Meleda with Congenital Cataract: A Novel Case Report.

Abstract:

:Mal de meleda (MdM), a rare autosomal recessive genodermatosis is characterized by erythema and hyperkeratosis of the palms and soles with a sharp demarcation and that progress with age (progrediens) and extend to the dorsal aspects of the hands and feet (transgrediens). It has been associated with various conditions albeit rarely with congenial cataract. Ocular lens and the skin have the same embryological origins. We hereby present this novel case report of Mal de meleda in association with congenital posterior subcapsular cataract which to the best of our knowledge has not been reported from India before.

journal_name

Indian J Dermatol

authors

Sethi A,Janda JK,Sharma N,Malhotra SK

doi

10.4103/0019-5154.159655

subject

Has Abstract

pub_date

2015-09-01 00:00:00

pages

524

issue

5

eissn

0019-5154

issn

1998-3611

pii

IJD-60-524a

journal_volume

60

pub_type

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