Medical and surgical perspectives of cardiac hypertrophy in Costello syndrome.

Abstract:

:We describe our experience with 2 patients having Costello syndrome, aged 11 and 36 months, who suffered systolic anterior motion of the aortic leaflet of the mitral valve and obstructive cardiac hypertrophy requiring surgery, comparing their cardiac characteristics to those described previously. We conclude that the heterogeneous nature of the cardiac hypertrophy in this syndrome can be considered and managed as the sum of a diffuse hypertrophy accessible to beta-blockade, and an asymmetric hypertrophy accessible to surgical myomectomy.

journal_name

Cardiol Young

journal_title

Cardiology in the young

authors

Kalfa D,Fraisse A,Kreitmann B

doi

10.1017/S1047951109991181

subject

Has Abstract

pub_date

2009-12-01 00:00:00

pages

644-7

issue

6

eissn

1047-9511

issn

1467-1107

pii

S1047951109991181

journal_volume

19

pub_type

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