Coexistence of Behcet's disease and chronic myelomonocyte leukemia with trisomy 8: a case report and review of the literature.

Abstract:

:Behçet's disease (BD) is a multisystem inflammatory vasculitis of unknown etiology and pathogenesis. Coexistence of BD along with hematological malignancies is extremely rare. We describe a patient diagnosed with BD and chronic myelomonocytic leukaemia (CMML) with trisomy 8. This case suggests that trisomy 8 may be involved in the concurrent manifestation of myelodysplastic syndrome (MDS) and BD with gastrointestinal ulcers.

journal_name

Clin Exp Rheumatol

authors

Mantzourani MG,Chantziara K,Thanopoulou I,Variami H,Vaiopoulos G,Pangalis GA

subject

Has Abstract

pub_date

2009-03-01 00:00:00

pages

S85-7

issue

2 Suppl 53

eissn

0392-856X

issn

1593-098X

pii

2722

journal_volume

27

pub_type

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