Databases for assessing the outcomes of the treatment of patients with congenital and paediatric cardiac disease--the perspective of cardiac surgery.

abstract：:Valvar heart disease can be complicated by hemodynamic derangements, depending on the degree of the abnormality. Stenosis causes pressure overload of the chamber draining through the valve and regurgitation results in volume overload. Many lesions have a component of both, resulting in both pressure and volume overloa...

journal_title：Cardiology in the young

authors： Decker JA

更新日期：2014-12-01 00:00:00

abstract：:Adequate arch augmentation for interrupted aortic arch repair is quite important to avoid post-operative recoarctation and bronchial compression. We describe here two successful cases of aortic arch reconstruction using autologous materials such as a pulmonary artery patch and a reversed left subclavian artery flap in...

journal_title：Cardiology in the young

authors： Hasegawa T,Oshima Y,Kadowaki T

更新日期：2014-06-01 00:00:00

abstract：:We describe 3 siblings with muscular ventricular septal defects, two requiring surgical closure. One of their offspring had a rare congenital aneurysm of the muscular ventricular septum, also requiring surgery. Another had a small muscular ventricular septal defect which closed spontaneously. Their father had echocard...

journal_title：Cardiology in the young

authors： Nicolae MI,Summers KM,Radford DJ

更新日期：2007-10-01 00:00:00

abstract：OBJECTIVE:To establish the feasibility and efficacy of closing large patent arterial duct in infants, using the modified and angled variants of the Amplatzer duct occluder. BACKGROUND:Closure of large patent arterial ducts by inserting devices in sick and underweight infants, particularly those weighing around 5 kilog...

journal_title：Cardiology in the young

authors： Vijayalakshmi IB,Chitra N,Rajasri R,Vasudevan K

更新日期：2006-08-01 00:00:00

abstract：BACKGROUND:Challenges remain in the judgement of pathological murmurs in newborns at maternity hospitals, and there are still many simple major CHD patients in developing countries who are not diagnosed in a timely fashion. This study aimed to evaluate the accuracy of cardiac auscultation on neonatal CHD by general pae...

journal_title：Cardiology in the young

authors： Zhao QM,Niu C,Liu F,Wu L,Ma XJ,Huang GY

更新日期：2019-05-01 00:00:00

abstract：:Supravalvular aortic stenosis is associated with the Williams-Beuren syndrome, but it also occurs in a non-syndromatic congenital form. An elastin gene mutation of chromosome 7q11.23 is responsible in both cases. The vascular features are identical. These patients have a higher risk of sudden death, particularly when ...

journal_title：Cardiology in the young

authors： Jakob A,Unger S,Arnold R,Grohmann J,Kraus C,Schlensak C,Stiller B

更新日期：2011-02-01 00:00:00

abstract：:Advances in biomedical engineering have led to three-dimensional (3D)-printed models being used for a broad range of different applications. Teaching medical personnel, communicating with patients and relatives, planning complex heart surgery, or designing new techniques for repair of CHD via cardiac catheterisation a...

journal_title：Cardiology in the young

authors： Forte MNV,Hussain T,Roest A,Gomez G,Jongbloed M,Simpson J,Pushparajah K,Byrne N,Valverde I

更新日期：2019-06-01 00:00:00

abstract：BACKGROUND:CHD is the leading cause of mortality due to birth defects. Array comparative genomic hybridisation (aCGH) detects submicroscopic copy number changes and may improve identification of the genetic basis of CHD. METHODS:This is a retrospective analysis of 1252 patients from a regional referral centre who had ...

journal_title：Cardiology in the young

authors： Hightower HB,Robin NH,Mikhail FM,Ambalavanan N

更新日期：2015-08-01 00:00:00

abstract：:In many parts of the world, mostly low- and middle-income countries, timely diagnosis and repair of congenital heart diseases (CHDs) is not feasible for a variety of reasons. In these regions, economic growth has enabled the development of cardiac units that manage patients with CHD presenting later than would be idea...

journal_title：Cardiology in the young

authors： Iyer PU,Moreno GE,Fernando Caneo L,Faiz T,Shekerdemian LS,Iyer KS

更新日期：2017-12-01 00:00:00

abstract：:Communications between the pulmonary artery and left atrium cause cyanosis. The images document serial haemodynamic changes in such a fistula from fetal life to the postnatal period with a successful transcatheter intervention. ...

journal_title：Cardiology in the young

authors： Sivakumar K,Sean DR

更新日期：2018-10-01 00:00:00

abstract：:The Holt-Oram syndrome was confirmed in an asymptomatic 36-year-old man by a novel TBX5-gene mutation (exon 8 acceptor splicing site, c.663-1G greater than A). Computed tomography showed an atrial septal defect and an anomalous right coronary artery crossing between the aorta and pulmonary arteries. Surgery corrected ...

journal_title：Cardiology in the young

authors： Vianna CB,Miura N,Pereira AC,Jatene MB

更新日期：2011-06-01 00:00:00

abstract：:A 5-year-old girl presented with chronic fatigue and extreme exercise intolerance. After countless doctor visits, investigations, and hospital admissions, striking desaturation during exercise test pointed to a cardiovascular problem. Desaturation as a result of right-to-left shunting through a patent foramen ovale du...

journal_title：Cardiology in the young

authors： Grootaers C,Roggen M,Gewillig M

更新日期：2019-02-01 00:00:00

abstract：:IntroductionDiagnostic and interventional catheter angiography of the heart is frequently used in paediatric cardiology. It is also possible to detect urinary system anomalies with cineurography images that may be obtained during angiocardiography. In this study, the aim was to determine the frequency, distribution, a...

journal_title：Cardiology in the young

authors： Oral O,Toprak MHH,Uysal F,Bostan OM,Cil E

更新日期：2019-02-01 00:00:00

abstract：:Many, if not most, of the controversies regarding the description of the congenitally malformed heart have been resolved over the turn of the 20th century. A group of lesions that remains contentious is the situation in which both arterial trunks, in their greater part, are supported by the morphologically right ventr...

journal_title：Cardiology in the young

authors： Bharucha T,Hlavacek AM,Spicer DE,Theocharis P,Anderson RH

更新日期：2017-01-01 00:00:00

abstract：:There exists a population of adults with undiagnosed coronary arterial lesions due to Kawasaki disease occurring before 1967. We report the clinical features in 6 adult males with coronary arterial lesions caused by presumed Kawasaki disease, whose dates of birth ranged from 1945 to 1963. The age of the diagnosed coro...

journal_title：Cardiology in the young

authors： Tsuda E,Matsuo M,Naito H,Noguchi T,Nonogi H,Echigo S

更新日期：2007-02-01 00:00:00

abstract：:Tetralogy of Fallot is only rarely associated with aortic valvar disease. We present a child who had uncomplicated repair of tetralogy of Fallot at 16 months of age, and who developed mild aortic stenosis three years later, with mild to moderate aortic incompetence being seen two years subsequent to that event. No aor...

journal_title：Cardiology in the young

authors： Galea N,Aquilina O,Grech V

更新日期：2003-06-01 00:00:00

abstract：BACKGROUND:Although survival to hospital discharge among children requiring extracorporeal membrane oxygenation support for medical and surgical cardio-circulatory failure has been reported in international registries, extended survival and re-hospitalisation rates have not been well described in the literature. MATER...

journal_title：Cardiology in the young

authors： Erwin N,Zuk J,Kaufman J,Pan Z,Carpenter E,Mitchell MB,da Cruz EM

更新日期：2013-04-01 00:00:00

abstract：:A female neonate, born at term, presented with complex cardiac anatomy dominated by right isomerism and infra-diaphragmatic totally anomalous pulmonary venous connection. Surgical repair was performed using circulatory arrest under deep hypothermia. In the postoperative period, the patient could not be weaned off mech...

journal_title：Cardiology in the young

authors： Kumar S,Ansari J,Weerasena N

更新日期：2005-12-01 00:00:00

abstract：:We report an unusual case of a 12-month-old boy diagnosed with anomalous origin of a single coronary artery from the pulmonary artery associated with patent ductus arteriosus. The patient survival was attributed to left-to-right shunt (patent ductus arteriosus) allowing for appropriate myocardial perfusion. Successful...

journal_title：Cardiology in the young

authors： Hugues N,Dommerc C,Pretre R

更新日期：2020-07-01 00:00:00

abstract：BACKGROUND:We previously reported four heterozygous missense mutations of MYH7, KCNQ1, MYLK2, and TMEM70 in a single three-generation Chinese family with dual Long QT and hypertrophic cardiomyopathy phenotypes for the first time. However, the clinical course among the family members was various, and the potential myoca...

journal_title：Cardiology in the young

authors： Wang J,Guo RQ,Guo JY,Zuo L,Lei CH,Shao H,Wang LF,Zhang YM,Liu LW

更新日期：2018-09-01 00:00:00

abstract：:A 5-week-old child presented with a cardiac arrest secondary to myocardial ischaemia. Echocardiography demonstrated a single coronary artery arising from the right sinus of Valsalva. The coronary artery branched into left and right arteries, with the left artery then coursing anomalously in the tissue plane between th...

journal_title：Cardiology in the young

authors： Duke C,Rosenthal E,Simpson JM

更新日期：2004-12-01 00:00:00

abstract：:May-Thurner syndrome is a rare clinical entity involving venous obstruction of the left lower extremity. The May-Thurner syndrome is a phenomenon commonly described as an acquired stenosis of the left common iliac vein secondary to compression of the left common iliac vein between the right common iliac artery and the...

journal_title：Cardiology in the young

authors： Vijayalakshmi IB,Setty HS,Narasimhan C

更新日期：2015-04-01 00:00:00

abstract：:Recently, three-dimensional printing of heart models is being used to plan percutaneous and surgical interventions in patients with CHD. We describe a case where we used a three-dimensional print model to plan a complex percutaneous intervention in a patient with coarctation of the aorta. ...

journal_title：Cardiology in the young

authors： Ghisiawan N,Herbert CE,Zussman M,Verigan A,Stapleton GE

更新日期：2016-12-01 00:00:00

abstract：:Catecholaminergic polymorphic ventricular tachycardia is a rare life-threatening arrhythmogenic disorder. An association with paroxysmal atrial fibrillation and other atrial arrhythmias has been described, but in all published cases the initial manifestation of the disease was ventricular arrhythmia. This is the first...

journal_title：Cardiology in the young

authors： Lawrenz W,Krogmann ON,Wieczorek M

更新日期：2014-08-01 00:00:00

abstract：:Partially anomalous pulmonary venous connection of a solitary pulmonary vein in the setting of an intact atrial septum is often subclinical, and the indications for surgical repair are controversial. Here we describe a patient who developed a significant shunt over a period of 10-years. Flow through the anomalously co...

journal_title：Cardiology in the young

authors： Koh M,Uemura H,Kagisaki K

更新日期：2007-10-01 00:00:00

abstract：OBJECTIVES:The objective of this study was to demonstrate the safety and feasibility of using the new Cardia Ultrasept II™ device with interposed Goretex patch referring to the perforation of polyvinyl alcohol membrane. BACKGROUND:Great advances have been made in the development of devices for closure of atrial septal...

journal_title：Cardiology in the young

authors： Mijangos-Vázquez R,García-Montes AJ,Soto-López EM,Guarner-Lans V,Zabal C

更新日期：2018-05-01 00:00:00

abstract：OBJECTIVE:There are several agents used for conscious sedation by various routes in children. The aim of this prospective randomised study is to compare the effectiveness of three commonly used sedatives: intranasal ketamine, intranasal midazolam, and oral chloral hydrate for children undergoing transthoracic echocardi...

journal_title：Cardiology in the young

authors： Alp H,Elmacı AM,Alp EK,Say B

更新日期：2019-09-01 00:00:00

abstract：:Research that is closely connected with the population it is studying and in which the translational value to healthcare is high is a laudable goal, but it is not often achieved. The Australian and New Zealand Fontan Registry has developed a model for involving patients and parents of children with a Fontan circulatio...

journal_title：Cardiology in the young

authors： d'Udekem Y,Forsdick V,du Plessis K

更新日期：2018-04-01 00:00:00

abstract：:A 44-year-old woman was referred to our centre for interventional cardiac catheterisation. The diagnostic work-up after a preceding ischaemic stroke led to the assumption of a patent foramen ovale due to a positive bubble study. Before the planned percutaneous closure of the patent foramen ovale, we performed a second...

journal_title：Cardiology in the young

authors： Doering F,Eicken A,Hess J

更新日期：2014-02-01 00:00:00

abstract：:Improvements in diagnosis and surgical technique for correction have led to an increasing number of women with congenital heart disease reaching the child-bearing age. Pregnancy places considerable strain on the heart and circulation and necessitates marked cardiorespiratory adaptation. Today, with the exception of th...

journal_title：Cardiology in the young

authors： Schmaltz AA,Neudorf U,Winkler UH

更新日期：1999-01-01 00:00:00