Abstract:
:Valvar heart disease can be complicated by hemodynamic derangements, depending on the degree of the abnormality. Stenosis causes pressure overload of the chamber draining through the valve and regurgitation results in volume overload. Many lesions have a component of both, resulting in both pressure and volume overload. Increased wall stress causes myocardial stretching and fibrosis, resulting in scarring; a nidus for arrhythmia development. Arrhythmias can complicate the clinical picture and increase the morbidity and mortality in patients with both congenital and acquired valvar disease. In adults with congenital heart disease, arrhythmias are the most common cause of sudden death, followed by heart failure. Valvar stenosis and insufficiency certainly contribute to this. This article highlights the need for arrhythmia surveillance for high-risk valvar lesions.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Decker JAdoi
10.1017/S1047951114001978subject
Has Abstractpub_date
2014-12-01 00:00:00pages
1064-70issue
6eissn
1047-9511issn
1467-1107pii
S1047951114001978journal_volume
24pub_type
杂志文章abstract:OBJECTIVES:To describe the echocardiographic features, underlying causes, and outcome of fetuses with dilated cardiomyopathy. DESIGN:A retrospective observational study between 1983 and 2003 at a tertiary centre for fetal cardiology. PATIENTS:Affected fetuses were identified using a computerised database. We included...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951105000855
更新日期:2005-08-01 00:00:00
abstract::In approximately 5% of patients with idiopathic recurrent pericarditis, the disease usually follows a chronic relapsing course, and children can develop dependence and side effects of prolonged high-dose corticosteroid regimens. In this setting anakinra, a recombinant human interleukin-1 competitive receptor antagonis...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951118002020
更新日期:2019-02-01 00:00:00
abstract::We report a patient with Down's syndrome referred to our Department of Echocardiography for evaluation after an episode of tachyarrhythmia. We diagnosed Ebstein's malformation. As far as we know, this association has been reported previously on only three occasions. We review these previous cases, describe our echocar...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:
更新日期:2003-08-01 00:00:00
abstract:BACKGROUND:Temporary percutaneous epicardial pacing wires are routinely placed in children following cardiac surgery. There is uncertainty in clinical practice about the optimum timing for their removal, and practice varies widely both within and between different institutions. AIM:The aim of our study was to describe...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107001035
更新日期:2007-10-01 00:00:00
abstract::A hyperinflammatory response to COVID-19 is being described in children. While this presents, and responds to management, similar to that of Kawasaki Disease it is being coined a new entity. But is it really? We explore how this phenomenon may be Kawasaki Disease with a new trigger. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120001432
更新日期:2020-07-01 00:00:00
abstract::The SARS-CoV-2 (COVID-19) pandemic has challenged our initial predictions of its ramifications, both short and long term. Cardiovascular manifestations of COVID-19 in children remain a topic of investigation as literature is lacking. We describe new onset atrial fibrillation in a child with a history of COVID-19 infec...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003893
更新日期:2020-10-19 00:00:00
abstract::The arterial switch operation has become the preferred procedure for surgical management of transposition, defined on the basis of concordant atrioventricular and discordant ventriculo-arterial connections. We conducted a retrospective evaluation of our experience in 61 infants with this segmental combination, seen fr...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107001746
更新日期:2008-02-01 00:00:00
abstract::We present a young soldier presenting with aborted sudden cardiac death, who was found to have concomitant hypertrophic cardiomyopathy and Wolff-Parkinson-White syndrome. Along with pathological haemodynamic features of hypertrophic cardiomyopathy, an easily-inducible re-entrant tachycardia was clearly documented in o...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118002123
更新日期:2019-02-01 00:00:00
abstract::Plastic bronchitis is a severe complication after a Fontan procedure, with an estimated incidence around 1-2% and poor prognosis. We present the cases of four patients with plastic bronchitis after a total cavopulmonary connection with a stenosis of the left pulmonary artery that was stented successfully. In three of ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113002163
更新日期:2015-01-01 00:00:00
abstract:OBJECTIVES:There is no consensus or theoretical explanation regarding the optimal location for the fenestration during the Fontan operation. We investigated the impact of the location of the fenestration on Fontan haemodynamics using a three-dimensional Fontan model in various physiological conditions. METHODS:A three...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117000099
更新日期:2017-09-01 00:00:00
abstract::The Fellowship Program of the Department of Cardiology at Boston Children's Hospital seeks to train academically oriented leaders in clinical care and laboratory and clinical investigation of cardiovascular disease in the young. The core clinical fellowship involves 3 years in training, comprising 24 months of clinica...
journal_title:Cardiology in the young
pub_type: 历史文章,杂志文章
doi:10.1017/S1047951116001712
更新日期:2016-12-01 00:00:00
abstract:BACKGROUND:Patients with CHD exhibit reduced isometric muscle strength and muscle mass; however, little is known how these parameters relate. Therefore, the aim was to investigate the relation between isometric limb muscle strength and muscle mass for patients in comparison to age- and sex-matched control subjects. ME...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120004709
更新日期:2021-01-18 00:00:00
abstract::Two paediatric congenital heart disease patients presented with a brief history of low-grade fever without any focal symptoms. Their clinical features and laboratory tests were unremarkable; however, their blood cultures were positive that prompted further work-up. Infective endocarditis should be considered in any pa...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795112000195X
更新日期:2020-09-01 00:00:00
abstract::Dysfunction of the autonomic nervous system, or dysautonomia, is an uncommon disease. Postural orthostatic tachycardia syndrome is one of the several types of dysautonomia. Postural orthostatic tachycardia syndrome, also known as chronic orthostatic intolerance, is the most common but least severe of the dysautonomic ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001198
更新日期:2010-12-01 00:00:00
abstract::To determine whether cardiac catheterisation procedures for low birth weight neonatesr < or = 2.5 kg carries a greater risk of complications compared with neonates > 2.5 kg, we conducted a single-centre retrospective case–control study. From 01/03 to 01/09, 46 consecutive neonates < 2.5 kg at the time of cardiac cathe...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112002247
更新日期:2013-10-01 00:00:00
abstract:BACKGROUND:Complete transposition is the most common form of neonatal cyanotic heart disease. The management of this condition has changed markedly in the last decade and there appears to be a significant variation between centres in terms of pre-operative management. OBJECTIVES/METHODS:We surveyed all paediatric card...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s104795110000812x
更新日期:2000-09-01 00:00:00
abstract:OBJECTIVE:To determine styles of coping, that is personal ways of dealing with problems, and social support, or support from the social environment, in a cohort of adults with congenital heart disease. METHODS:We subjected 362 patients with congenital heart disease, aged from 20 to 46 years, belonging to five diagnost...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951104002033
更新日期:2004-04-01 00:00:00
abstract::Endocarditis of congenital coronary fistulas in the cardiac chambers is rare, especially in the paediatric age group. We describe the case of a 9-year-old boy with a fistula from the dilated right coronary artery to the junction of the superior caval vein to the right atrium, complicated by endocarditis. Treatment con...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117001846
更新日期:2018-02-01 00:00:00
abstract:BACKGROUND:Fetal echocardiography is the main modality of prenatal diagnosis of CHD. This study was done to describe the trends and benefits associated with prenatal diagnosis of complex CHD at a tertiary care centre. METHODS:Retrospective chart review of patients with complex CHD over an 18-year period was performed....
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118002147
更新日期:2018-12-26 00:00:00
abstract:BACKGROUND:Perceived correlation between the coronary arterial anatomy in patients with complete transposition, and the outcome of the arterial switch procedure, has made preoperative identification of their patterns standard practice. PURPOSE:Our purpose was to assess the accuracy of preoperative echocardiographic id...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951102000537
更新日期:2002-05-01 00:00:00
abstract:OBJECTIVE:To evaluate heart rate variability by Holter monitoring in type 1 diabetic children compared with a healthy control group and determine the factors modifying heart rate variability. METHODS:This was designed as a prospective study comparing 28 patients, diagnosed with type 1 diabetes and under follow-up, wit...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113001224
更新日期:2014-10-01 00:00:00
abstract:BACKGROUND:There is a great need for echocardiographic criterions for accurate diagnosis of carditis in acute rheumatic fever. AIM:To test the efficacy of proposed echocardiographic criterions for the diagnosis of carditis. MATERIALS AND METHODS:We studied 333 patients suspected of having acute rheumatic fever, under...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951108003107
更新日期:2008-12-01 00:00:00
abstract::Purpose The aim of this study was to determine whether the exercise tolerance test can provide diagnostic and prognostic information regarding children and young adults and help predict outcome. METHODS:A total of 87 patients, aged 7-29 years (median 13, mean 13.4) were selected retrospectively. They underwent exerci...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117000233
更新日期:2017-09-01 00:00:00
abstract::We report a case in which a meandering right pulmonary vein connecting to the left atrium is associated with hypoplasia of the right lung, horseshoe lung, abnormal pulmonary lobation, and abnormal branching of the pulmonary arteries. We discuss its relationship to the so-called scimitar variant, and to the scimitar sy...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951106000461
更新日期:2006-06-01 00:00:00
abstract:BACKGROUND:SCN5A encodes sodium-channel α-subunit Nav1.5. The mutations of SCN5A can lead to hereditary cardiac arrhythmias such as the long-QT syndrome type 3 and Brugada syndrome. Here we sought to identify novel mutations in a family with arrhythmia. METHODS:Genomic DNA was isolated from blood of the proband, who w...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117002980
更新日期:2018-05-01 00:00:00
abstract:BACKGROUND:The physiological importance of the lateral tunnel stenosis in the Fontan pathway for children with single ventricle physiology can be difficult to determine. The impact of the stenosis and stent implantation on total cavopulmonary connection resistance has not been characterized, and there are no clear guid...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114002765
更新日期:2016-01-01 00:00:00
abstract::Body mass index, race/ethnicity, and payer status are associated with operative mortality in congenital heart disease (CHD). Interactions between these predictors and impacts on longer term outcomes are less well understood. We studied the effect of body mass index, race/ethnicity, and payer on 1-year outcomes followi...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003911
更新日期:2020-11-19 00:00:00
abstract::Conotruncal heart defects are considered to be one of the most common types of birth defect worldwide. Genetic disturbances in folate metabolism such as Thymidylate synthase may increase risk for conotruncal heart defects. We evaluated two common Thymidylate synthase polymorphisms, including the 28 bp tandem repeat in...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118002184
更新日期:2018-12-21 00:00:00
abstract:UNLABELLED:Introduction The optimal perioperative feeding strategies for neonates with CHD are unknown. In the present study, we describe the current feeding practices across a multi-institutional cohort. METHODS:Inclusion criteria for this study were as follows: all neonates undergoing cardiac surgery admitted to the...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951115002474
更新日期:2015-12-01 00:00:00
abstract::Congenital heart disease is a significant cause of morbidity and mortality in the newborn. Its diagnosis may lead to a crisis in the affected families; there are the perceived implications of having an abnormality of so vital an organ. To that may be added the assumed guilt or blame, grief and at times anger, frequent...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/s104795110000696x
更新日期:1998-07-01 00:00:00