Abstract:
:In many parts of the world, mostly low- and middle-income countries, timely diagnosis and repair of congenital heart diseases (CHDs) is not feasible for a variety of reasons. In these regions, economic growth has enabled the development of cardiac units that manage patients with CHD presenting later than would be ideal, often after the window for early stabilisation - transposition of the great arteries, coarctation of the aorta - or for lower-risk surgery in infancy - left-to-right shunts or cyanotic conditions. As a result, patients may have suffered organ dysfunction, manifest signs of pulmonary vascular disease, or the sequelae of profound cyanosis and polycythaemia. Late presentation poses unique clinical and ethical challenges in decision making regarding operability or surgical candidacy, surgical strategy, and perioperative intensive care management.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Iyer PU,Moreno GE,Fernando Caneo L,Faiz T,Shekerdemian LS,Iyer KSdoi
10.1017/S1047951117002591subject
Has Abstractpub_date
2017-12-01 00:00:00pages
S31-S39issue
S6eissn
1047-9511issn
1467-1107pii
S1047951117002591journal_volume
27pub_type
杂志文章,评审abstract::We report a case of unroofed coronary sinus not associated with the persistent left superior vena cava. Definite diagnosis of the unroofed coronary sinus was obtained by trans-oesophageal echocardiography, which revealed the unroofed portion with left-to-right shunt. Real-time three-dimensional trans-oesophageal echoc...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113002400
更新日期:2015-01-01 00:00:00
abstract::Untreated congenital long QT syndrome may result in potentially lethal ventricular tachycardia. In the most common type, risk of such an event has been linked to exercise. This originally resulted in very restrictive guidelines for sports participation in affected individuals. Although the complex interactions of a sp...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951116002225
更新日期:2017-01-01 00:00:00
abstract::Myocardial ischaemia and infarction in pulmonary atresia and intact ventricular septum with right ventricular-dependent coronary circulation is a well-established complication. We report an interesting case of an acquired aneurysm in the ventricular septum in a patient who underwent staged palliation. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111001120
更新日期:2012-04-01 00:00:00
abstract:OBJECTIVE:Our aim was to investigate the change in diameter of holes within the oval fossa, and the role of aneurismal formation in reducing the size of the hole, in patients diagnosed during infancy with isolated defects in the floor of the fossa. PATIENTS:In a retrospective study, we included 100 patients diagnosed ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951107001692
更新日期:2008-02-01 00:00:00
abstract:OBJECTIVE:To document the echocardiographic features of tetralogy of Fallot during fetal and postnatal life. Correlation of echocardiographic findings with the requirement for early intervention prior to definitive repair. DESIGN:Retrospective observational study. SETTING:A tertiary fetal cardiology unit. PATIENTS:F...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:
更新日期:2003-06-01 00:00:00
abstract::Recently, three-dimensional printing of heart models is being used to plan percutaneous and surgical interventions in patients with CHD. We describe a case where we used a three-dimensional print model to plan a complex percutaneous intervention in a patient with coarctation of the aorta. ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116001827
更新日期:2016-12-01 00:00:00
abstract:OBJECTIVE:The objective of this study was to detect structural and functional changes in the left and right ventricles in obese Egyptian adolescents. Methods and results Anthropometric and echocardiographic parameters, including tissue Doppler imaging, were obtained from 70 obese adolescents with average body mass inde...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111001910
更新日期:2012-08-01 00:00:00
abstract::Aneurysm of the sinus of Valsalva is a rare congenital cardiac anomaly. It occurs as an outpouching that progresses like a windsock, and it may rupture producing aortic regurgitation, cardiac tamponade, congestive heart failure, conduction abnormalities, and stroke. We describe a case of rupture of the sinus of Valsal...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951116001621
更新日期:2017-04-01 00:00:00
abstract:BACKGROUND:Syncope is common in children and adolescents and most commonly represents neurocardiogenic syncope. No information has been reported regarding the effect of syncope on health-related quality of life in children. METHODS:This was a retrospective cohort study of patients seen in the Heart Institute Syncope C...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112000133
更新日期:2012-10-01 00:00:00
abstract:BACKGROUND:Progress in the management of complex congenital heart disease (CHD) led to an improvement in survival rates of adults with a Fontan-like circulation. The objective of this study was to assess the subjective health status and quality of life of this population. METHODS AND RESULTS:Patients aged more than 18...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003431
更新日期:2020-10-26 00:00:00
abstract:OBJECTIVE:We aimed to apply systems engineering principles to address hospital-acquired infections in the paediatric intensive care setting. DESIGN:Mixed method approach involving four steps: perform time-motion study of cardiac intensive care unit (CICU) care processes, establish a meaningful schema to classify obser...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003777
更新日期:2020-11-10 00:00:00
abstract:AIM:In present study, we aimed to evaluate the changes in valvular regurgitations in mid-term follow-up of children with first attack acute rheumatic fever diagnosed after updated Jones criteria. MATERIALS AND METHODS:The medical records of the children diagnosed with acute rheumatic fever between June 2015 and Novemb...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951119003317
更新日期:2020-03-01 00:00:00
abstract:OBJECTIVE:To describe the gross motor development of infants who had undergone cardiac surgery in the neonatal or early infant period. METHODS:Gross motor performance was assessed when infants were 4, 8, 12, and 16 months of age with the Alberta Infant Motor Scale. This scale is a discriminative gross motor outcome me...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951112000121
更新日期:2012-10-01 00:00:00
abstract::Chest pain in adolescents is rarely associated with cardiac disease. Adolescents with medically unexplained chest pain usually have high levels of anxiety and depression. Psychological stress may trigger non-cardiac chest pain. This study evaluated risk factors that particularly characterise adolescence, such as major...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951116002109
更新日期:2017-08-01 00:00:00
abstract::A 10-month-old infant with severe tricuspid valve disease due to staphylococcal bacterial endocarditis, underwent surgical replacement of the valve. The new valve was fashioned using an autologous pericardial patch. Over 3 years of follow-up, the new valve has functioned satisfactorily, with moderately elevated right ...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001903
更新日期:2011-08-01 00:00:00
abstract::Sialidosis, a rare autosomal recessive disorder, is caused by a deficiency of NEU1 encoded enzyme alpha-N-acetyl neuraminidase. We report a premature male with neonatal-onset type II sialidosis which was associated with left ventricular dysfunction. The clinical presentation and subsequent progression which culminated...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120004953
更新日期:2021-01-28 00:00:00
abstract:OBJECTIVE:To evaluate heart rate variability by Holter monitoring in type 1 diabetic children compared with a healthy control group and determine the factors modifying heart rate variability. METHODS:This was designed as a prospective study comparing 28 patients, diagnosed with type 1 diabetes and under follow-up, wit...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113001224
更新日期:2014-10-01 00:00:00
abstract::Right atrial isomerism is associated with complex cardiac malformations, particularly single-ventricle lesions; right atrial isomerism is rarely associated with aorto-pulmonary collateral arteries. We report a foetal diagnosis of right atrial isomerism, with an unbalanced atrioventricular septal defect, pulmonary sten...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003649
更新日期:2020-11-26 00:00:00
abstract::Kawasaki disease constitutes an acute febrile vasculitis of unknown aetiology. It is considered the most common cause of acquired cardiac failure in children. Although standard treatment comprises intravenous immunoglobulin and aspirin, some children exhibit refractory disease, necessitating the use of alternative the...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111001260
更新日期:2012-08-01 00:00:00
abstract::Two paediatric congenital heart disease patients presented with a brief history of low-grade fever without any focal symptoms. Their clinical features and laboratory tests were unremarkable; however, their blood cultures were positive that prompted further work-up. Infective endocarditis should be considered in any pa...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S104795112000195X
更新日期:2020-09-01 00:00:00
abstract::Cognitive, functional, educational achievement and behavioural measures were employed to assess neurobehavioral status in 57 of 60 participants who were initially enrolled in the Baltimore-Washington Infant Study, and who survived surgical correction of complete transposition (concordant atrioventricular and discordan...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/s1047951100006867
更新日期:1998-07-01 00:00:00
abstract:OBJECTIVES:The objectives of this study were to describe the approach to stenting arterial shunts in adult congenital patients with single-ventricle physiology and to assess the medium-term clinical and haemodynamic outcomes following stent insertion. BACKGROUND:Adult patients with single-ventricle physiology and pulm...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118001464
更新日期:2018-12-01 00:00:00
abstract:BACKGROUND:Diaphragm dysfunction following surgery for congenital heart disease is a known complication leading to delays in recovery and increased post-operative morbidity and mortality. We aimed to determine the incidence of and risk factors associated with diaphragm plication in children undergoing cardiac surgery a...
journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951119002671
更新日期:2020-01-01 00:00:00
abstract::With the advent of improved medical and surgical care in congenital heart disease, there has been an increase in the number of patients who survive into adulthood, giving rise to a new patient population 'Adults with congenital heart disease'. In the past, morbidity and mortality were the primary concerns for this gro...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951113000747
更新日期:2014-02-01 00:00:00
abstract:BACKGROUND:Early weight trends after cardiac surgery in infants from low- and middle-income countries where the majority are undernourished have not been defined. We studied the early post-operative weight trends to identify specific factors associated with early weight loss and poor weight gain after discharge followi...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951119002944
更新日期:2020-01-01 00:00:00
abstract::The mitral-aortic intervalvular fibrosa is an area of fibrous continuity between the mitral and aortic valves. We present the first case of a congenital pseudoaneurysm in this region, detected prenatally as an isolated cardiac defect, which was followed-up conservatively postnatally. The diagnosis was confirmed by ech...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951117000890
更新日期:2017-05-29 00:00:00
abstract::Research that is closely connected with the population it is studying and in which the translational value to healthcare is high is a laudable goal, but it is not often achieved. The Australian and New Zealand Fontan Registry has developed a model for involving patients and parents of children with a Fontan circulatio...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951117001494
更新日期:2018-04-01 00:00:00
abstract::Many, if not most, of the controversies regarding the description of the congenitally malformed heart have been resolved over the turn of the 20th century. A group of lesions that remains contentious is the situation in which both arterial trunks, in their greater part, are supported by the morphologically right ventr...
journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951116001190
更新日期:2017-01-01 00:00:00
abstract:INTRODUCTION:Little is known about the quality of life, health, family, education, and employment status among adult men with repaired tetralogy of Fallot. MATERIAL AND METHODS:A total of 68 men who underwent repair of tetralogy of Fallot between 1971 and 1991 were studied. Fifty-three patients answered the SF-36 heal...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111001934
更新日期:2012-08-01 00:00:00
abstract::An acute injury to a coronary artery was recognized during the surgical construction of the Fontan circulation. Surgical manipulation of the site of injury was not successful in restoring normal myocardial blood flow. A stent was therefore placed intraoperatively under direct vision, with restoration of normal coronar...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951104001180
更新日期:2004-02-01 00:00:00