Abstract:
OBJECTIVES:The objectives of this study were to describe the approach to stenting arterial shunts in adult congenital patients with single-ventricle physiology and to assess the medium-term clinical and haemodynamic outcomes following stent insertion. BACKGROUND:Adult patients with single-ventricle physiology and pulmonary blood flow dependent on a surgically placed arterial shunt who did not progress to venous palliation are extremely challenging to manage. Progressive cyanosis secondary to narrowing of the shunt has a marked impact on exercise tolerance and results in intolerable well-being for these patients. Stenting arterial shunts in adult patients is one method that can help improve pulmonary blood flow. There is very limited information in the literature about this patient. METHODS:This is a retrospective study for arterial shunts stenting conducted between 2008 and 2016. The peripheral oxygen saturations, the NYHA status, the haemoglobin, and the degree of atrio-ventricular valve regurgitation as assessed on transthoracic echo were compared before and 6-12 months after procedures. RESULTS:There was a short-term improvement in oxygen saturations; the pre-procedure mean was 75.8 (SD 2.55)% (range 70-85%) and post-procedure mean was 83 (SD 2.52)% (range 78-87%), with a p value of 0.04. Haemoglobin level decreased from a pre-procedure mean of 22.06-20.28 g/L 6 months post procedure (range 18.1-24.4 to 13-23.3 g/L), with a p value of 0.44. NYHA class decreased from a mean of 3.2-2.2 post procedure. Left atrial volume for four of the cases did not change (22.6-76.6 ml [mean 48.4 ml] to 29.6-72.9 ml [mean 52 ml], p value: 0.83). CONCLUSIONS:Stenting stenotic arterial shunts is a useful method to gain a medium-term improvement on the oxygen saturation and clinical symptoms, and may act as a useful intermediate step for further management plans.
journal_name
Cardiol Youngjournal_title
Cardiology in the youngauthors
Kasem M,Bentham J,Thomson Jdoi
10.1017/S1047951118001464subject
Has Abstractpub_date
2018-12-01 00:00:00pages
1431-1435issue
12eissn
1047-9511issn
1467-1107pii
S1047951118001464journal_volume
28pub_type
杂志文章abstract::Behçet's disease is a chronic autoimmune disease with vascular complications that are most frequently manifested as thromboembolism in veins and pseudoaneurysm in arteries. We report the case of a 13-year-old boy admitted for clinical and biological signs of rheumatic fever associated with chest pain. The clinical exa...
journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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doi:10.1017/S1047951114001012
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journal_title:Cardiology in the young
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doi:10.1017/S1047951117001287
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journal_title:Cardiology in the young
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doi:10.1017/S1047951113001868
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951102000070
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001708
更新日期:2011-04-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/s1047951103000386
更新日期:2003-04-01 00:00:00
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118002123
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111002113
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journal_title:Cardiology in the young
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doi:10.1017/S1047951106000126
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journal_title:Cardiology in the young
pub_type: 杂志文章,评审
doi:10.1017/S1047951114001231
更新日期:2014-10-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951114001711
更新日期:2015-08-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110000090
更新日期:2010-06-01 00:00:00
abstract::We report the case of a child with cor triatriatum dexter masquerading as Ebstein's anomaly on transthoracic echocardiography. This was attributed to a floppy membrane arising from the right atrium, protruding into the tricuspid valve and pushing the leaflets downwards, giving an impression of Ebstein's anomaly. The i...
journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000023
更新日期:2011-06-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951118001129
更新日期:2018-11-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951104003142
更新日期:2004-06-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951111000679
更新日期:2012-02-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120002097
更新日期:2020-10-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951110001010
更新日期:2010-12-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章,多中心研究
doi:10.1017/S1047951120000141
更新日期:2020-04-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951120003960
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951113002394
更新日期:2015-01-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
doi:10.1017/S1047951115000682
更新日期:2016-03-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
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更新日期:2017-08-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
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更新日期:2013-02-01 00:00:00
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journal_title:Cardiology in the young
pub_type: 杂志文章
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更新日期:2003-02-01 00:00:00