Spinal rhabdomyosarcoma in a child with lipomyelomeningocele.

Abstract:

:Malignant tumors arising within dysrhaphic malformations are very rare and are mostly teratomas; so far, only one rhabdomyosarcoma has been reported in this context. We report another case of a girl with lipomyelomeningocele who developed a lumbar rhabdomyosarcoma 2 years after birth and primary closure of the neural tube defect. We present clinical, radiological and pathological findings, discuss possible mechanisms of malignant transformation and review the literature.

journal_name

Pediatr Neurosurg

journal_title

Pediatric neurosurgery

authors

Wagner W,Koch D

doi

10.1159/000083742

keywords:

subject

Has Abstract

pub_date

2004-11-01 00:00:00

pages

293-6

issue

6

eissn

1016-2291

issn

1423-0305

pii

83742

journal_volume

40

pub_type

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