Hypothalamic hamartoma associated with Laurence-Moon-Biedl syndrome. Case report and review of the literature.

Abstract:

:A rare case of a patient with Laurence-Moon-Biedl syndrome associated with hypothalamic hamartoma is described. The English-language literature contains no cases of patients with this association. The clinical manifestations of this syndrome, those of hypothalamic hamartomas, and the appearance of the tumors on magnetic resonance images are discussed.

journal_name

Pediatr Neurosurg

journal_title

Pediatric neurosurgery

authors

Diaz LL,Grech KF,Prados MD

doi

10.1159/000120563

subject

Has Abstract

pub_date

1991-01-01 00:00:00

pages

30-3

issue

1

eissn

1016-2291

issn

1423-0305

journal_volume

17

pub_type

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