Follow-up magnetic resonance imaging in Hallervorden-Spatz disease.

Abstract:

:Bilateral high signal emitting areas in the globus pallidus surrounded by low signal emitting areas have been described as a typical MRI finding in Hallervorden-Spatz disease (HSD). We made a diagnosis of HSD in an 11-year-old girl with progressive dystonia of 4 years duration who showed these typical MRI abnormalities. An initial MRI at the age of 9 was normal. Pathological confirmation of these typical MRI findings has not yet been described, but earlier reports as well as our case suggest that MRI may be helpful in making a clinical diagnosis of HSD. This case further shows that MRI may be normal in an early stage of the disease.

journal_name

Clin Neurol Neurosurg

authors

Brouwer OF,Laboyrie PM,Peters AC,Vielvoye GJ

doi

10.1016/0303-8467(92)90023-v

keywords:

subject

Has Abstract

pub_date

1992-01-01 00:00:00

pages

S57-60

eissn

0303-8467

issn

1872-6968

journal_volume

94 Suppl

pub_type

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