Cardiac surgery for Kartagener syndrome.

Abstract:

:Two patients (one girl, one boy) with Kartagener syndrome (situs inversus, bronchiectasis, sinusitis), despite pulmonary problems and associated congenital cardiac anomalies, were operated on at the ages of 4 years and 7 years, respectively. They had had previous palliative treatment at the age of 3 months and 1.3 years, respectively. Both postoperative periods after total correction were without significant complications. Long-term follow-up was available for 9 and 19 years, respectively, with no manifestations of heart insufficiency. Both patients are physically active, and neither requires cardiac medication. Patients with Kartagener syndrome and associated congenital cardiac anomalies can successfully undergo multiple cardiac operations with good long-term outcome.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Tkebuchava T,von Segesser LK,Niederhäuser U,Bauersfeld U,Turina M

doi

10.1007/s002469900115

subject

Has Abstract

pub_date

1997-01-01 00:00:00

pages

72-3

issue

1

eissn

0172-0643

issn

1432-1971

journal_volume

18

pub_type

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