Abstract:
:An unusual variant of congenital dyserythropoietic anaemia is described presenting as mild haemolytic anaemia with multinucleated erythroblasts in the marrow of the proband. The outcome of her non-consanguineous pregnancy was a third trimester, in utero, fetal demise. The hydropic fetus had dyserythropoiesis with circulating multinucleated erythroblasts, and haemosiderosis. Re-evaluation of the proband revealed a variant of congenital dyserythropoietic anaemia with an inheritance pattern, and with morphological, serological and biochemical features which are not consistent with any of the three described variants of congenital dyserythropoietic anaemias.
journal_name
Br J Haematoljournal_title
British journal of haematologyauthors
Roberts DJ,Nadel A,Lage J,Rutherford CJdoi
10.1111/j.1365-2141.1993.tb03119.xsubject
Has Abstractpub_date
1993-07-01 00:00:00pages
549-51issue
3eissn
0007-1048issn
1365-2141journal_volume
84pub_type
杂志文章abstract::Thirty-four patients with refractory multiple myeloma were treated with 4-d continuous infusions of vincristine and adriamycin in combination with 4-d pulsed high-dose dexamethasone (VAD). Of 31 evaluable patients, 16 entered a complete remission (50%) and three a partial remission (10%). No difference in response rat...
journal_title:British journal of haematology
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journal_title:British journal of haematology
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journal_title:British journal of haematology
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journal_title:British journal of haematology
pub_type: 杂志文章
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pub_type: 杂志文章
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更新日期:1996-06-01 00:00:00
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journal_title:British journal of haematology
pub_type: 杂志文章
doi:10.1111/j.1365-2141.1982.tb03937.x
更新日期:1982-12-01 00:00:00
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pub_type: 杂志文章,随机对照试验
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更新日期:2019-05-01 00:00:00
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pub_type: 杂志文章,评审
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