Case 245: Erdheim-Chester Disease.

Abstract:

:History A 53-year-old man experienced headache and double vision that progressed over 1 year. After a traumatic fall, he was hospitalized, and proptosis was identified at physical examination. Laboratory tests were remarkable for leukocytosis. Hematocrit level, thyroid stimulating hormone level, autoimmune antibody level, erythrocyte sedimentation rate, and C-reactive protein level were normal. Computed tomography (CT) of the head revealed bilateral intraconal masses, for which magnetic resonance (MR) imaging of the orbits was subsequently performed ( Fig 1 ). CT imaging of the chest and abdomen ( Fig 2 ) revealed periaortic and retroperitoneal stranding. Perinephric biopsy was performed, and a diagnosis of immunoglobulin G4 (IgG4)-related disease was made based on identification of a few plasma cells per high-power field that were positive for IgG4. Orbital biopsy was then performed, but the results were inconclusive for IgG4-related disease. The patient was discharged and given steroid therapy for presumed IgG4-related disease. [Figure: see text][Figure: see text][Figure: see text][Figure: see text][Figure: see text][Figure: see text] Several months later, the patient returned to our institution with progressive symptoms despite ongoing steroid treatment. His case was reviewed by several specialists to develop alternative treatments for IgG4-related disease. After review of the available images, a neuroradiology fellow (M.D.M.) performed history taking and a physical examination and subsequently recommended radiography of the lower extremities ( Fig 3 ). [Figure: see text][Figure: see text].

journal_name

Radiology

journal_title

Radiology

authors

Mamlouk MD,Aboian MS,Glastonbury CM

doi

10.1148/radiol.2017141151

subject

Has Abstract

pub_date

2017-09-01 00:00:00

pages

910-917

issue

3

eissn

0033-8419

issn

1527-1315

journal_volume

284

pub_type

杂志文章
  • Dobutamine response and myocardial infarct transmurality: functional improvement after coronary artery bypass grafting--initial experience.

    abstract::The Investigational Review Board approved the protocol, and all patients provided signed informed consent. The protocol was compliant with HIPAA. The purpose of the study was to prospectively test the hypothesis that addition of low-dose dobutamine and quantification of inotropic reserve in segments with 1%-50% infarc...

    journal_title:Radiology

    pub_type: 临床试验,杂志文章

    doi:10.1148/radiol.2403051150

    authors: Bove CM,DiMaria JM,Voros S,Conaway MR,Kramer CM

    更新日期:2006-09-01 00:00:00

  • Desirability of roentgen esophageal examination immediately after pneumatic dilatation for achalasia.

    abstract::Although infrequent, esophageal rupture is a serious complication of pneumatic dilatation for the treatment of achalasia. Because of an experience with delayed recognition of esophageal perforation in a patient with achalasia, we now examine the esophagus using a water-soluble contrast medium immediately following eve...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/130.3.589

    authors: Stewart ET,Miller WN,Hogan WJ,Dodds WJ

    更新日期:1979-03-01 00:00:00

  • The base view in vertebral angiography. An aid in the diagnosis of extraaxial cerebellopontine angle tumors.

    abstract::Though the advent of computed tomography has improved the detection of posterior fossa lesions, there are times when it can not be used to differentiate between an intra- and extraaxial lesion, particularly when the mass is anteriorly located. Base view angiography can be used to make this distinction, accurately loca...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/124.1.157

    authors: Pinto RS,George AE,Kricheff II,Naidich TP,Fox A

    更新日期:1977-07-01 00:00:00

  • Ultrasound localization of occult breast lesions.

    abstract::High-resolution real-time ultrasound with either a 7.5- or 10-MHz transducer was used to localize 7/9 nonpalpable breast masses previously detected by mammography and to determine where the biopsy needle should be inserted. ...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.151.3.6718740

    authors: Laing FC,Jeffrey RB,Minagi H

    更新日期:1984-06-01 00:00:00

  • Crohn disease: prone-angled compression view in radiographic evaluation.

    abstract::A prone-angled compression radiographic view was compared with traditional radiographs in 17 patients with suspected Crohn disease. The angled view was clearly superior to the posteroanterior view in visualization of disease in the terminal ileum and small bowel and was superior to spot radiographs in six of 10 patien...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.187.2.8475310

    authors: Yue NC,Jones B

    更新日期:1993-05-01 00:00:00

  • Cancer of the glottis: prognostic factors in radiation therapy.

    abstract::The authors conducted a multivariate analysis of the prognostic factors in 96 patients with early glottic cancer treated by radiation therapy. Of these, 73 had T1 and 23 had T2 tumor. The primary tumor was controlled in 82% of T1 and 74% of T2 lesions. Actuarial five-year survival rates were 87% for T1 and 74% for T2....

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.149.1.6611940

    authors: Mantravadi RV,Liebner EJ,Haas RE,Skolnik EM,Applebaum EL

    更新日期:1983-10-01 00:00:00

  • The origin of the left gastric artery.

    abstract::Five hundred celiac angiograms were reviewed to evaluate the frequency of clinically significant variations in the origin of the left gastric artery. In 13 of 500 cases, the left gastric artery arose anomalously most often as a direct branch of the aorta; in 14 of 500 cases, the left gastric artery primarily supplied ...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/126.3.623

    authors: Naidich JB,Naidich TP,Sprayregen S,Hyman RA,Pudlowski RM,Stein HL

    更新日期:1978-03-01 00:00:00

  • Patient radiation dose associated with uterine artery embolization.

    abstract:PURPOSE:To evaluate the estimated absorbed radiation doses to the ovaries and skin entrance during uterine artery embolization (UAE) for leiomyomas. MATERIALS AND METHODS:Radiation dose was measured in 20 patients who underwent UAE for leiomyomas. Measurements were obtained by placing lithium fluoride dosimeters both ...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.214.1.r00ja24121

    authors: Nikolic B,Spies JB,Lundsten MJ,Abbara S

    更新日期:2000-01-01 00:00:00

  • Acute cholecystitis at T2-weighted and manganese-enhanced T1-weighted MR cholangiography: preliminary study.

    abstract::Twelve patients with symptoms of acute cholecystitis underwent heavily T2-weighted and mangafodipir trisodium-enhanced T1-weighted magnetic resonance (MR) cholangiography and cholescintigraphy before they underwent cholecystectomy. On T2-weighted MR cholangiographic images, morphologic evidence of outflow obstruction ...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiol.2272020207

    authors: Kim KW,Park MS,Yu JS,Chung JP,Ryu YH,Lee SI,Lee KS,Yoon SW,Lee KH

    更新日期:2003-05-01 00:00:00

  • Posttraumatic arterial priapism in children: management with embolization.

    abstract:PURPOSE:To evaluate selective embolization for management of posttraumatic priapism in preadolescent boys and color Doppler sonography for diagnosis of the causative lesion and for planning embolization. MATERIALS AND METHODS:Five preadolescent boys with posttraumatic priapism underwent selective angiography and embol...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.196.1.7784590

    authors: Miller SF,Chait PG,Burrows PE,Steckler RE,Khoury AE,McLorie GA,Connolly BL,Pereira JK

    更新日期:1995-07-01 00:00:00

  • Imaging of the gallbladder, 1987.

    abstract::Gallbladder disease, and the patients with symptoms suggestive of gallbladder disease, remains a widespread clinical problem that requires investigation by imaging techniques. Sonography, and to a lesser extent cholescintigraphy, has facilitated the evaluation of these patients and allows the diagnosis of cholelithias...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.163.3.3554340

    authors: Cooperberg PL,Gibney RG

    更新日期:1987-06-01 00:00:00

  • Coronary angiographic and scintigraphic findings in experimental cardiac contusion.

    abstract::Clinical, angiographic, scintigraphic and pathologic observations in myocardial contusion were correlated. Radionuclide imaging of the injured heart with 99mTc-Sn-polyphosphate provides an accurate diagnosis in acute, even mild, myocardial contusion. The study can be carried out without danger to the critically ill pa...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/116.3.679

    authors: Chiu CL,Roelofs JD,Go RT,Doty DB,Rose EF,Christie JH

    更新日期:1975-09-01 00:00:00

  • Stage I nonseminomatous germ cell tumors of the testis: radiologic follow-up after orchidectomy.

    abstract::One hundred and forty-seven patients with clinical stage I nonseminomatous germ cell tumors of the testis were entered into a follow-up program after orchidectomy. Follow-up consisted of regular clinical examinations, estimations of the serum markers beta human chorionic gonadotropin and alpha-fetoprotein, chest radio...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.164.3.2441430

    authors: Williams MP,Husband JE,Heron CW

    更新日期:1987-09-01 00:00:00

  • Reading protocol for dynamic contrast-enhanced MR images of the breast: sensitivity and specificity analysis.

    abstract:PURPOSE:To prospectively determine sensitivity and specificity of breast magnetic resonance (MR) imaging in a screening and symptomatic population by using independent double reading, with histologic or cytologic results or a minimum 18-month follow-up as the standard. MATERIALS AND METHODS:Informed consent and ethica...

    journal_title:Radiology

    pub_type: 杂志文章,多中心研究

    doi:10.1148/radiol.2363040735

    authors: Warren RM,Pointon L,Thompson D,Hoff R,Gilbert FJ,Padhani A,Easton D,Lakhani SR,Leach MO,UK Magnetic Resonance Imaging in Breast Screening (MARIBS) Study Group.

    更新日期:2005-09-01 00:00:00

  • Angiographic ablation of parathyroid adenomas: lessons from a 10-year experience.

    abstract::Angiographic ablation of parathyroid adenomas with ionic contrast material was performed in 24 patients with persistent hyperparathyroidism who had undergone at least one prior unsuccessful surgical resection; 23 had mediastinal adenomas. The success rate was 83% at 1 month after ablation and 71% at both 5 and 9 years...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.165.3.3685340

    authors: Miller DL,Doppman JL,Chang R,Simmons JT,O'Leary TJ,Norton JA,Spiegel AM,Marx SJ,Aurbach GD

    更新日期:1987-12-01 00:00:00

  • Computed tomography of suspected caval thrombosis secondary to proximal extension of phlebitis from the leg.

    abstract::While computed tomography (CT) is an accepted procedure for investigation of the inferior vena cava (IVC), little attention has been given to its use in IVC thrombosis secondary to proximal extension of thrombi within the lower venous system. Four cases are presented and several advantages of CT over standard contrast...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.140.2.7255720

    authors: Vujic I,Stanley J,Tyminski LJ

    更新日期:1981-08-01 00:00:00

  • Digital subtraction laryngography.

    abstract::Digital subtraction laryngography was used to evaluate laryngeal function in 8 patients: 4 with normal larynxes and 4 with laryngeal disease. Subtracted digital images provided a dynamic display of the extent and symmetry of vocal cord excursions and pyriform sinus inflation, and the vocal cord resting position was al...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.147.3.6342030

    authors: Brown BM,Enzmann DR,Hopp ML,Castellino RA

    更新日期:1983-06-01 00:00:00

  • Breast tumors: computer-assisted quantitative assessment with color Doppler US.

    abstract:PURPOSE:To compare quantified measurements with color Doppler ultrasonography (US) with those obtained with conventional duplex US in the differential diagnosis of suspect lesions in the breast. MATERIALS AND METHODS:A computer-assisted protocol was used to calculate the color pixel density (CPD) and the mean color va...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.192.3.8058950

    authors: Huber S,Delorme S,Knopp MV,Junkermann H,Zuna I,von Fournier D,van Kaick G

    更新日期:1994-09-01 00:00:00

  • Thermography, mammography, and clinical examination in breast cancer screening. Review of 16,000 studies.

    abstract::Breast cancer screening detected 139 biopsy-proved malignancies in 16,000 slef-selected women (8.7/1,000). In these, xeroradiography detected 78% (109), clinical examination 55% (76), and thermography 39% (54). In all 16,000 women, the thermogram was interpreted as positive in 17.9% (2,864). The greatest effectiveness...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/122.1.123

    authors: Feig SA,Shaber GS,Schwartz GF,Patchefsky A,Libshitz HI,Edeiken J,Nerlinger R,Curley RF,Wallace JD

    更新日期:1977-01-01 00:00:00

  • White matter degeneration with Unverricht-Lundborg progressive myoclonus epilepsy: a translational diffusion-tensor imaging study in patients and cystatin B-deficient mice.

    abstract:PURPOSE:To study white matter (WM) changes in patients with Unverricht-Lundborg progressive myoclonus epilepsy (EPM1) caused by mutations in the cystatin B gene and in the cystatin B-deficient (Cstb-/-) mouse model and to validate imaging findings with histopathologic analysis of mice. MATERIALS AND METHODS:Informed c...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiol.13122458

    authors: Manninen O,Koskenkorva P,Lehtimäki KK,Hyppönen J,Könönen M,Laitinen T,Kalimo H,Kopra O,Kälviäinen R,Gröhn O,Lehesjoki AE,Vanninen R

    更新日期:2013-10-01 00:00:00

  • Application of duplex US for characterization of endoleaks in abdominal aortic stent-grafts: report of five cases.

    abstract::Endoleaks were detected with helical computed tomographic (CT) angiography in five patients after placement of an aortobiliac stent-graft. The leaks were subsequently evaluated with duplex ultrasonography (US) and, in four patients, with conventional aortography as well. CT angiography revealed a total of seven endole...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiol.2253011806

    authors: Greenfield AL,Halpern EJ,Bonn J,Wechsler RJ,Kahn MB

    更新日期:2002-12-01 00:00:00

  • Reflex sympathetic dystrophy in the foot: clinical and scintigraphic criteria.

    abstract::To establish strict clinical criteria for reflex sympathetic dystrophy (RSD) of the foot and to characterize any associated scintigraphic pattern, the authors performed three-phase radionuclide bone scanning in 51 patients prospectively referred because RSD was a diagnostic consideration. To establish sensitivity and ...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.184.2.1620860

    authors: Holder LE,Cole LA,Myerson MS

    更新日期:1992-08-01 00:00:00

  • Reversible cystic disease associated with pulmonary tuberculosis: radiologic findings.

    abstract:PURPOSE:The authors describe radiologic findings of cystic lung disease associated with pulmonary tuberculosis. MATERIALS AND METHODS:Three immunocompetent women with pulmonary tuberculosis were seen with acute respiratory failure and diffuse bilateral pulmonary opacity depicted at admission chest radiography. The wom...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.204.1.9205240

    authors: Ko KS,Lee KS,Kim Y,Kim SJ,Kwon OJ,Kim JS

    更新日期:1997-07-01 00:00:00

  • Fungal sinusitis: diagnosis with CT and MR imaging.

    abstract::Of 293 patients who underwent computed tomography (CT), surgery, and pathologic examination for chronic sinusitis, 25 had a diagnosis of fungal sinusitis at pathologic examination. Of these, 22 had foci of increased attenuation at CT (in four patients the mean representative CT number [Hounsfied unit] was 122.2 HU [SD...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.169.2.3174990

    authors: Zinreich SJ,Kennedy DW,Malat J,Curtin HD,Epstein JI,Huff LC,Kumar AJ,Johns ME,Rosenbaum AE

    更新日期:1988-11-01 00:00:00

  • Preparation of 52Fe and its use in a 52Fe/52mMn generator.

    abstract::Clinically useful quantities of 52Fe have been prepared at the Brookhaven Linac Isotope Producer (BLIP) by bombarding manganese or nickel targets with medium energy protons. After chemical separation, 52Fe is loaded onto a generator column from which carrier-free 52Mn is eluted. The 52mMn generator is potentially usef...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/132.2.475

    authors: Ku TH,Richards P,Stang LG Jr,Prach T

    更新日期:1979-08-01 00:00:00

  • Multiphase CT Angiography Improves Prediction of Intracerebral Hemorrhage Expansion.

    abstract::Purpose To determine the prevalence of the spot sign and the accuracy of using the spot sign to predict intracerebral hemorrhage (ICH) expansion with standardized multiphase computed tomographic (CT) angiography. Materials and Methods This prospective observational cohort study included 123 consecutive patients with a...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiol.2017162839

    authors: Rodriguez-Luna D,Coscojuela P,Rodriguez-Villatoro N,Juega JM,Boned S,Muchada M,Pagola J,Rubiera M,Ribo M,Tomasello A,Demchuk AM,Goyal M,Molina CA

    更新日期:2017-12-01 00:00:00

  • Vacuum phenomenon simulating meniscal or cartilaginous injury of the knee at MR imaging.

    abstract::In five patients undergoing magnetic resonance imaging of the knee after athletic injuries, the authors identified a vacuum phenomenon that simulated medial meniscal or joint compartment cartilaginous abnormality. A cadaveric knee was injected with air, and the findings were re-created. The presence of air or gas betw...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.180.2.2068320

    authors: Shogry ME,Pope TL Jr

    更新日期:1991-08-01 00:00:00

  • Thin-walled cystic lesions in bronchioalveolar carcinoma.

    abstract::In a retrospective study, thin-walled cystic lesions were identified in four patients with proved bronchioalveolar carcinoma (BAC). The radiographic appearances are described, and possible mechanisms of formation of the lesions are discussed. Although such appearances due to BAC have rarely been described in the liter...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.185.2.1329140

    authors: Weisbrod GL,Towers MJ,Chamberlain DW,Herman SJ,Matzinger FR

    更新日期:1992-11-01 00:00:00

  • Does radiologist recommendation for follow-up with the same imaging modality contribute substantially to high-cost imaging volume?

    abstract:PURPOSE:To retrospectively measure repeat rates for high-cost imaging studies, determining their causes and trends, and the impact of radiologist recommendations for a repeat examination on imaging volume. MATERIALS AND METHODS:This HIPAA-compliant study had institutional review board approval, with waiver of informed...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiol.2423051754

    authors: Lee SI,Saokar A,Dreyer KJ,Weilburg JB,Thrall JH,Hahn PF

    更新日期:2007-03-01 00:00:00

  • Major geometric variations between multiple high-dose-rate applications of brachytherapy in cancer of the cervix: frequency and types of variation.

    abstract:PURPOSE:To evaluate major geometric variations in multiple intracavitary applications for carcinoma of the cervix. MATERIALS AND METHODS:Orthogonal radiographs were reviewed of 17 consecutive patients with carcinoma of the cervix treated with 70 applications of high-dose-rate brachytherapy. In seven patients, consciou...

    journal_title:Radiology

    pub_type: 杂志文章

    doi:10.1148/radiology.195.2.7724760

    authors: Kim RY,Meyer JT,Plott WE,Spencer SA,Meredith RF,Jennelle RL,Salter MM

    更新日期:1995-05-01 00:00:00