Segmental defect of the intestinal musculature associated with ileal atresia and biliary atresia.

abstract：PURPOSE:There is a known association between Cornelia de Lange syndrome (CdLS) and congenital diaphragmatic hernia (CDH), with CDH being the cause of death in 5%-20% of CdLS cases. We aimed to identify and describe patients with CDLS and CDH. We hypothesized that CdLS would be associated with high-risk CDH and poor out...

journal_title：Journal of pediatric surgery

authors： Gupta VS,Khan AM,Ebanks AH,Lally PA,Lally KP,Harting MT,Congenital Diaphragmatic Hernia Study Group.

更新日期：2020-06-11 00:00:00

abstract：:A lateral skin-flap perineoplasty has been used in 15 patients born with an absent anal canal. The aim behind the introduction of this modification was the prevention of mucosal prolapse. On early assessment, this has been achieved in 11 of the cases. This represents a 50% improvement on our previous results. ...

journal_title：Journal of pediatric surgery

authors： Davies MR,Cywes S

更新日期：1984-10-01 00:00:00

abstract：:Granular cell tumor of the biliary tree is a rare benign tumor that occurs most commonly in young African-American girls. Granular cell tumor rarely is included in the differential diagnosis of biliary obstruction, yet complete surgical excision is curative. The authors report a case of granular cell tumor of the bili...

journal_title：Journal of pediatric surgery

authors： Reynolds EM,Tsivis PA,Long JA

更新日期：2000-04-01 00:00:00

abstract：BACKGROUND:The aim of this study was to evaluate detailed changes of gastroesophageal reflux disease (GERD) in children before and after laparoscopic Nissen fundoplication (LNF) utilizing esophageal combined pH-multichannel intraluminal impedance (pH/MII) measurements. PATIENTS AND METHODS:Thirteen patients with neuro...

journal_title：Journal of pediatric surgery

authors： Fukahori S,Yagi M,Ishii S,Asagiri K,Saikusa N,Hashizume N,Yoshida M,Masui D,Sakamoto S,Tsuruhisa S,Kurahachi T,Tanaka Y

更新日期：2016-08-01 00:00:00

abstract：:Thirty-six patients with benign neonatal sacrococcygeal teratoma (SCT) were treated in our medical center from 1972 to 1990. Mean gestational age was 38.6 +/- 3.3 weeks with a mean birth weight of 3,484.0 +/- 938.5 g. Twenty-nine patients (89%) were females. The majority of the tumors (75%) contained cystic components...

journal_title：Journal of pediatric surgery

authors： Bilik R,Shandling B,Pope M,Thorner P,Weitzman S,Ein SH

更新日期：1993-09-01 00:00:00

abstract：:There are compelling physiologic arguments for correcting certain malformations before birth. Although fetal surgery has been successful in sheep and lower animals, it has proven difficult in primates because the gravid uterus is exquisitely sensitive to induction of preterm labor and abortion. Because the feasibility...

journal_title：Journal of pediatric surgery

authors： Harrison MR,Anderson J,Rosen MA,Ross NA,Hendrickx AG

更新日期：1982-04-01 00:00:00

abstract：:The authors report on 2 patients with congenital chylous ascites who underwent successful lymphatic duct ligation after a laparoscopic lymphoid dye test. Fetal ascites had been detected in both cases, and both babies were born with marked abdominal swelling. Given that conservative treatment by medium-chain triglyceri...

journal_title：Journal of pediatric surgery

authors： Mitsunaga T,Yoshida H,Iwai J,Matsunaga T,Kouchi K,Ohtsuka Y,Okada T,Hishiki T,Ohnuma N

更新日期：2001-11-01 00:00:00

abstract：OBJECTIVE:The aim of this study is to report prospective data of pediatric cases that underwent percutaneous tracheostomy (PT) to show that PT is a safe and feasible procedure in children even in small infants. PATIENTS AND METHODS:PT was done in 51 consecutive patients. Demographic data, indications, complications an...

journal_title：Journal of pediatric surgery

authors： Gollu G,Ates U,Can OS,Kendirli T,Yagmurlu A,Cakmak M,Aktug T,Dindar H,Bingol-Kologlu M

更新日期：2016-10-01 00:00:00

abstract：:There were 30 infants, under 1 yr of age, in refractory congestive heart failure, who underwent surgical correction for coarctation of the aorta. The series was divided into two groups, depending on the type of surgical procedure performed: Group 1, 17 patients end-to-end anastomosis; Group 2, 13 patients aortic angio...

journal_title：Journal of pediatric surgery

authors： Allen RG,Maria-Garcia J,Nayek G

更新日期：1980-12-01 00:00:00

abstract：INTRODUCTION:Full thickness rectal prolapse (FTRP) tends to be self-limiting in children and is usually managed expectantly. However, it may persist and therefore requires surgical correction. There is no consensus upon operative management, and no one procedure has uniformly good outcomes. The aim of this study was to...

journal_title：Journal of pediatric surgery

authors： Campbell AM,Murphy J,Charlesworth PB,Bhan C,Jarvi K,Power N,Ward HC,Williams NS

更新日期：2013-03-01 00:00:00

abstract：PURPOSE:Thyroid receptor alpha-1 (TR-alpha1) and thyroid receptor beta-1 (TR-beta1) are thought to be essential for the fetal and postnatal development of the lung. The authors investigated gene level expression of TR-alpha1 and TR-beta1 in the lung of nitrofen-induced congenital diaphragmatic hernia (CDH) using revers...

journal_title：Journal of pediatric surgery

authors： Teramoto H,Guarino N,Puri P

更新日期：2001-11-01 00:00:00

abstract：BACKGROUND/PURPOSE:Payers have established unplanned returns as quality measures tied to reimbursement. We sought to identify patient characteristics and surgical factors associated with unplanned returns and postoperative complications following intraabdominal pediatric urologic procedures. Only one study has emergenc...

journal_title：Journal of pediatric surgery

authors： Wallace A,Rodriguez MV,Gundeti MS

更新日期：2019-10-01 00:00:00

abstract：:We report two cases of total colonic aganglionosis in which the ileocecal valve and right colon were preserved. The aganglionic ileal segment is removed leaving behind only a very short prececal remnant, which is anastomosed end-to-back to the remaining ileum. An ileal loop (of approximately 20 cm in length) is isolat...

journal_title：Journal of pediatric surgery

authors： Sauer H,Klos I

更新日期：1989-05-01 00:00:00

abstract：BACKGROUND:Histopathologic findings of advanced neuroblastoma after intensive induction chemotherapy have not been studied well. METHODS:In the present study, all of the surgical specimens from 19 patients who had advanced abdominal neuroblastoma and were pretreated intensively with the protocol of the Study Group of ...

journal_title：Journal of pediatric surgery

authors： Miyauchi J,Matsuoka K,Oka T,Kamii Y,Honna T,Bessho F,Sasaki S,Melanowska J,Tsuchida Y

更新日期：1997-11-01 00:00:00

abstract：PURPOSE:Heterotaxy syndrome is associated with intestinal abnormalities. We sought to define the gastrointestinal anatomy and determine both the risk of volvulus and benefit of screening upper gastrointestinal fluoroscopy (UGI) in these patients. METHODS:Medical records from 2003 until 2011 at Children's Hospital Los ...

journal_title：Journal of pediatric surgery

authors： Papillon S,Goodhue CJ,Zmora O,Sharma SS,Wells WJ,Ford HR,Upperman JS,Wang KS,Bushman GA,Kim R,Pierce JR

更新日期：2013-01-01 00:00:00

abstract：PURPOSE:The objective of this study is to use anorectal manometry for functional assessment of early postoperative results after corrective surgery for anorectal malformations (ARMs) in children and compare manometric observations with age-matched controls. Parents were counseled and management strategies were planned ...

journal_title：Journal of pediatric surgery

authors： Kumar S,Al Ramadan S,Gupta V,Helmy S,Debnath P,Alkholy A

更新日期：2010-09-01 00:00:00

abstract：:The occurrence of Hirschsprung's disease, with histologically verified colonic aganglionosis, in only 1 of 2 prematurely born and presumed identical (monozygotic) twins is reported. The occurrence of monozygotic twinning was supported by the observed sharing of a single and common placenta and by ABO and HLA identity ...

journal_title：Journal of pediatric surgery

authors： Moore TC,Landers DB,Lachman RS,Ament ME

更新日期：1979-04-01 00:00:00

abstract：BACKGROUND/PURPOSE:Portoenterostomy is an accepted method of achieving bile drainage in biliary atresia, but there is a paucity of data, including formal quality-of-life (QoL) studies, on long-term survivors. This report includes survival analysis and QoL studies from the world's largest series of cases treated in Japa...

journal_title：Journal of pediatric surgery

authors： Howard ER,MacLean G,Nio M,Donaldson N,Singer J,Ohi R

更新日期：2001-06-01 00:00:00

abstract：:A brief resume of the highlights in the history of oesophageal atresia is presented. This is followed by research into the etiology, ontogeny and embryology, and microbiological studies. A revised classification of risk factors with consequent survival statistics is presented. Lessons learned in the management of the ...

journal_title：Journal of pediatric surgery

authors： Spitz L

更新日期：2006-10-01 00:00:00

abstract：:Trauma is the leading cause of death for children over 1 year of age. This study was undertaken to identify the patterns of injury among children admitted to a regional pediatric trauma center. During a 34-month period, 3,472 injured children were consecutively admitted to a regional pediatric trauma center. Data were...

journal_title：Journal of pediatric surgery

authors： Peclet MH,Newman KD,Eichelberger MR,Gotschall CS,Guzzetta PC,Anderson KD,Garcia VF,Randolph JG,Bowman LM

更新日期：1990-01-01 00:00:00

abstract：AIM:The aim of the study is to report feasibility and safety of endoscopic esophageal substitution in infants with pure esophageal atresia and wide gap tracheoesophageal fistula with a minimum one year follow-up. MATERIALS AND METHODS:This prospective study was conducted from January 2012 for twenty four consecutive m...

journal_title：Journal of pediatric surgery

authors： Chowdhary SK,Kandpal DK,Agarwal D,Balan S,Jerath N,Sibal A,Broor SL

更新日期：2016-03-01 00:00:00

abstract：BACKGROUND:In the absence of robust data from low- and middle-income countries (LMICs), most disease burden estimates and related resource allocation choices are based on historic Northern demographics. We hypothesize that significant discrepancies exist between directly reported LMIC data and surrogate high-income cou...

journal_title：Journal of pediatric surgery

authors： Toobaie A,Yousef Y,Balvardi S,St-Louis E,Baird R,Guadagno E,Poenaru D

更新日期：2019-05-01 00:00:00

abstract：PURPOSE:The aim of this study was to determine how to manage children with recurrence of intussusception. METHODS:Medical records of patients treated for intussusception from 1976 to 2008 at the Queen Sirikit National Institute of Child Health were reviewed. Information on patients who developed recurrent intussuscept...

journal_title：Journal of pediatric surgery

authors： Niramis R,Watanatittan S,Kruatrachue A,Anuntkosol M,Buranakitjaroen V,Rattanasuwan T,Wongtapradit L,Tongsin A

更新日期：2010-11-01 00:00:00

abstract：:Thromboembolic events in the pediatric age group occur most commonly in neonates, and newborns of diabetic mothers are particularly at risk. We report a newborn with right renal vein and inferior vena cava thrombosis who apparently embolized across the foramen ovale antenatally with resultant right brachial artery occ...

journal_title：Journal of pediatric surgery

authors： Duncan BW,Adzick NS,Longaker MT,Edwards JR,Nelson RM,Koerper MA

更新日期：1991-06-01 00:00:00

abstract：BACKGROUND/PURPOSE:Diaphragmatic agenesis (DA) is a distinct clinical entity with poorer survival rate compared with patients with posterolateral diaphragmatic hernia. The large defect in DA is repaired frequently with a synthetic patch in the neonatal period. Well-known, long-term complications include recurrent herni...

journal_title：Journal of pediatric surgery

authors： Samarakkody U,Klaassen M,Nye B

更新日期：2001-11-01 00:00:00

abstract：:Tubular colonic duplications are exceedingly rare. The authors present an unusual case of a boy with a persistent prostatorectal fistula resulting from a tubular colorectal duplication. The current case is unique for 2 reasons: (1) the presence of a fistula without any concomitant genitourinary anomalies and (2) the e...

journal_title：Journal of pediatric surgery

authors： Kokoska ER,Steinhardt GF,Tomita SS,Weber TR

更新日期：1999-10-01 00:00:00

abstract：PURPOSE:Hirschsprung-associated enterocolitis (HAEC) is a serious complication of Hirschsprung's disease (HD), with generalized sepsis and high mortality rate. Although the surgical correction of HD is mostly successful, challenges remain in the management of children with repeated episodes of enterocolitis. The author...

journal_title：Journal of pediatric surgery

authors： Zhang JS,Li L,Hou WY,Liu SL,Diao M,Zhang J,Ming AX,Cheng W

更新日期：2014-05-01 00:00:00

abstract：BACKGROUND/PURPOSE:Human immunodeficiency virus (HIV) disease is an increasingly common infection in children in sub-Sahara Africa. Rectal fistulation is one such condition with which these patients present to the paediatric surgeon. This appeared to be an exclusively female condition until 2 male patients were treated...

journal_title：Journal of pediatric surgery

authors： Wiersma R

更新日期：2003-01-01 00:00:00

abstract：BACKGROUND/PURPOSE:Hydatid disease of the spleen is a rare disease, and it occurs in 1% to 8% of all children with hydatid disease. That difference in frequency depends on the social and economic status of the patients and the country. The aim of our study is to reveal its diagnosis and treatment. METHODS:From 1985 to...

journal_title：Journal of pediatric surgery

authors： Kalinova K,Stefanova P,Bosheva M

更新日期：2006-07-01 00:00:00

abstract：:We present an approach to safely expose the hepatic hilum for revision procedures after left lobe living donor liver transplantation. A 14-year-old adolescent girl who had undergone left lobe living donor liver transplantation experienced repeated episodes of cholangitis. Because treatment with interventional techniqu...

journal_title：Journal of pediatric surgery

authors： Honda M,Takeichi T,Ohya Y,Okumura K,Lee KJ,Yamamoto H,Asonuma K,Inomata Y

更新日期：2012-03-01 00:00:00