Cerebral X-linked adrenoleukodystrophy: follow-up with magnetic resonance imaging.

Abstract:

OBJECTIVE:To report a case of childhood cerebral X-linked adrenoleukodystrophy (X-ADL), emphasizing the magnetic resonance imaging (MRI) findings at initial evaluation and at the follow-up. CASE REPORT:Five year-old boy, who was asymptomatic, presented with diagnosis of X-ADL for MRI evaluation. The initial brain MRI showed a focal area of enhancement at the splenium of the corpus calosum. One year later, the follow-up MRI showed a progression of the corpus calosus lesion, as well as other lesions in the parietal and occipital lobes. CONCLUSION:The brain MRI follow-up of patients with X-ADL is important to show the progression of the lesions.

journal_name

Arq Neuropsiquiatr

authors

Gasparetto EL,Rosa JM,Davaus T,de Carvalho Neto A

doi

10.1590/s0004-282x2006000600030

subject

Has Abstract

pub_date

2006-12-01 00:00:00

pages

1033-5

issue

4

eissn

0004-282X

issn

1678-4227

pii

S0004-282X2006000600030

journal_volume

64

pub_type

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