The functions of RPS19 and their relationship to Diamond-Blackfan anemia: a review.

Abstract:

:The relatively new study of ribosomal proteins has allowed for greater understanding of protein synthesis; however the connection between ribosomal proteins' roles and that of disease pathophysiology has not yet been established. RPS19 is a ribosomal protein linked to Diamond-Blackfan anemia whose functions have begun to be elucidated. We review here the known roles of RPS19 in both ribosome construction and other extra-ribosomal functions and discuss their relationship to Diamond-Blackfan anemia.

journal_name

Mol Genet Metab

authors

Morimoto K,Lin S,Sakamoto K

doi

10.1016/j.ymgme.2006.11.004

subject

Has Abstract

pub_date

2007-04-01 00:00:00

pages

358-62

issue

4

eissn

1096-7192

issn

1096-7206

pii

S1096-7192(06)00362-3

journal_volume

90

pub_type

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