Abstract:
:Our presentation of four cases demonstrates the essential features of limb-body wall complex (LBWC), representing a compound anomaly pattern in body-wall defects. The diagnosis of this entity is based on two of the three following characteristics: (1) exencephaly/encephalocele and facial clefts; (2) thoraco- and/or abdominoschisis; and (3) limb defects. A definite association with internal anomalies and severe kyphoscoliosis makes a more distinct concept of the pathogenesis reasonable. Limb-body wall malformations result from a malfunction of the ectodermal placodes involving the early embryonic folding process. The poor prognosis of LBWC calls for early antenatal diagnosis.
journal_name
Pediatr Surg Intjournal_title
Pediatric surgery internationalauthors
Pumberger W,Schaller A,Bernaschek Gdoi
10.1007/s003830000497subject
Has Abstractpub_date
2001-07-01 00:00:00pages
486-90issue
5-6eissn
0179-0358issn
1437-9813journal_volume
17pub_type
杂志文章abstract::The need for contralateral inguinal exploration in children during unilateral inguinal hernia repair remains controversial. We questioned whether an elective preoperative sonographic examination of the contralateral inguinal canal was accurate enough to prevent unnecessary exploration of the asymptotic side. Sonograph...
journal_title:Pediatric surgery international
pub_type: 杂志文章
doi:10.1007/BF00180090
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journal_title:Pediatric surgery international
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abstract::Robotic assisted minimal invasive surgery (RMIS) is a new resource popular in some surgical specialties but not yet in pediatric surgery. There are numerous advantages of robotic surgical technology in adult patients well documented in the literature. The purpose of this study is to define the feasibility, safety, and...
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journal_title:Pediatric surgery international
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abstract:INTRODUCTION:Three-dimensional (3D) imaging instead of two-dimensional (2D) computed tomography (CT) for diagnosis and preoperative planning in infants and young children with complex liver tumors is a promising technique for precision hepatectomy. METHODS:This study was a retrospective analysis of 26 infants and youn...
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journal_title:Pediatric surgery international
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abstract::In neonates requiring operation for necrotizing enterocolitis (NEC), the complications due to enterostomy (ES) and the need for another operation to restore continuity have prompted several surgeons to employ primary anastomosis (PA) after resection as the operative strategy of choice. Our objective was to compare pri...
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pub_type: 杂志文章,评审
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journal_title:Pediatric surgery international
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journal_title:Pediatric surgery international
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更新日期:2001-03-01 00:00:00
abstract::Pseudoexstrophy is a rare variant of the exstrophy/epispadias complex, comprised of the musculoskeletal defects of classic exstrophy but with an intact bladder and urethra. We present a case of a neonate with left-sided gastroschisis and pseudoexstrophy, the first reported combination of these two anomalies. The anoma...
journal_title:Pediatric surgery international
pub_type: 杂志文章
doi:10.1007/s00383-004-1217-4
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更新日期:2011-09-01 00:00:00
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pub_type: 杂志文章
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journal_title:Pediatric surgery international
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doi:10.1007/s00383-008-2279-5
更新日期:2009-01-01 00:00:00
abstract::When presentation is delayed, intussusceptions may be difficult to reduce using standard enema regimens. Our endeavour to minimize the need for surgery in an environment where failed reductions are common has led to the development of an aggressive, non-operative method of reducing intussusceptions. One hundred and si...
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pub_type: 杂志文章
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pub_type: 杂志文章
doi:10.1007/s00383-015-3798-5
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journal_title:Pediatric surgery international
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journal_title:Pediatric surgery international
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