Abstract:
:A third case of Hb J Iran is reported. The propositus is of Russian-Armenian origin and was investigated for hematuria. The electrophoretic behavior and the characterization of primary structure are described. Hb J Iran is stable and has normal functional properties. High resolution Nuclear Magnetic Resonance spectra suggest the presence of structural perturbations in the heme pocket of the variant. Solubility studies of Hb S/Hb J Iran mixture indicated that His beta 77 belongs to a contact region of deoxy Hb S polymers.
journal_name
Hemoglobinjournal_title
Hemoglobinauthors
Delanoe-Garin J,Rhoda MD,Craescu CT,Bardakjian J,Blouquit Y,Lacombe C,Arous N,Poyart C,Ganeval D,Girot Rdoi
10.3109/03630268608996868subject
Has Abstract,Author List Incompletepub_date
1986-01-01 00:00:00pages
365-78issue
4eissn
0363-0269issn
1532-432Xjournal_volume
10pub_type
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