Congenitally corrected transposition with pulmonary atresia and intact ventricular septum.

abstract：:A two-year-old boy with a background history of Down syndrome and partial atrioventricular septal defect presented with acute respiratory distress requiring intubation and mechanical ventilation. He continued to deteriorate, despite ventilation; direct laryngoscopy, bronchoscopy, and computed tomography demonstrated s...

journal_title：Cardiology in the young

authors： Kelleher EM,Nolke L,McMahon CJ

更新日期：2015-03-01 00:00:00

abstract：:Our long-term follow-up has revealed that symmetrical development of the breasts is significantly impaired in pre-pubescent female patients subsequent to an anterolateral thoracotomy. Although standard posterolateral and anterolateral right-sided thoracotomies are used for correction of "simple" cardiac lesions such a...

journal_title：Cardiology in the young

authors： Schreiber C,Bleiziffer S,Lange R

更新日期：2003-12-01 00:00:00

abstract：:A neonate with transposition of the great arteries and intact ventricular septum presented without pulmonary over-circulation, and subsequently developed pulmonary haemorrhage after corrective surgery. Postoperative CT revealed an aortopulmonary collateral artery arising from the descending aorta, and we performed suc...

journal_title：Cardiology in the young

authors： Sugimoto A,Ota N,Sakamoto K

更新日期：2016-03-01 00:00:00

abstract：BACKGROUND:Risk for neurodevelopmental delay in infants and children with CHD is well established, but longer-term outcomes are equivocal. A meta-analysis was conducted to establish whether cognitive deficits remain beyond childhood - into teenage and young adult years. Methods and results A total of 18 unique samples,...

journal_title：Cardiology in the young

authors： Mills R,McCusker CG,Tennyson C,Hanna D

更新日期：2018-03-01 00:00:00

abstract：:In Respiratory Syncytial Virus infection, the early identification of infants at risk for severe disease in order to potentially decrease morbidity could be considered a major goal. Current guidelines recommend only clinical observation for this purpose in infants without known comorbidities. However, recent evidence ...

journal_title：Cardiology in the young

authors： Rodriguez-Gonzalez M,Benavente-Fernandez I,Castellano-Martinez A

更新日期：2019-11-01 00:00:00

abstract：BACKGROUND:Holt-Oram syndrome is characterised by CHD and limb anomalies. Mutations in TBX5 gene, encoding the T-box transcription factor, are responsible for the development of Holt-Oram syndrome, but such mutations are variably detected in 30-75% of patients. METHODS:Clinically diagnosed eight Holt-Oram syndrome pat...

journal_title：Cardiology in the young

authors： Jhang WK,Lee BH,Kim GH,Lee JO,Yoo HW

更新日期：2015-08-01 00:00:00

abstract：:Research that is closely connected with the population it is studying and in which the translational value to healthcare is high is a laudable goal, but it is not often achieved. The Australian and New Zealand Fontan Registry has developed a model for involving patients and parents of children with a Fontan circulatio...

journal_title：Cardiology in the young

authors： d'Udekem Y,Forsdick V,du Plessis K

更新日期：2018-04-01 00:00:00

abstract：UNLABELLED:Real-time three-dimensional echocardiography can surpass simple cross-sectional echocardiography in providing precise details of cardiac lesions. For the purpose of optimising treatment, we describe our findings with real-time three-dimensional echocardiography when interrogating different types of communica...

journal_title：Cardiology in the young

authors： Bilska KM,Kehrens CM,Riley G,Anderson RH,Marek J

更新日期：2012-04-01 00:00:00

abstract：:Our aim was to determine whether the index of left ventricular mass increases during the acute and subacute phase of Kawasaki disease, and to investigate any relationship between this index and clinical and echocardiographic variables. We performed, therefore, a retrospective study of 66 children with Kawasaki disease...

journal_title：Cardiology in the young

authors： Yu JJ,Kwak BO,Jeon YH,Park YM,Lee R,Chung S,Bae SH,Pyun BY

更新日期：2009-02-01 00:00:00

abstract：:This study was carried out to analyse seasonal variations in live births with congenital heart disease in the overall population of Malta. Included were all patients diagnosed as having congenital heart disease by echocardiography, cardiac catheterization, surgery or post mortem, by 1 year of age, and who were born be...

journal_title：Cardiology in the young

authors： Grech V

更新日期：1999-07-01 00:00:00

abstract：BACKGROUND:Care of children with functionally univentricular hearts is resource-intensive. OBJECTIVES:To analyse pregnancy and early post-natal outcomes of fetuses with functionally univentricular hearts in the setting of a low-middle-income country. METHODS:A retrospective study was conducted during the period of Ja...

journal_title：Cardiology in the young

authors： Vaidyanathan B,Vijayaraghavan A,Thomas S,Sudhakar A

更新日期：2020-12-01 00:00:00

abstract：:An infant developed severe desaturation within a few hours of construction of a modified Blalock-Taussig shunt. Echocardiography revealed that the shunt had become occluded, and this was confirmed angiographically. At catheterisation, therefore, we passed a 0.014" percutaneous transluminal coronary angioplasty wire th...

journal_title：Cardiology in the young

authors： Galal MO,Attas K,Baslaim G

更新日期：2000-11-01 00:00:00

abstract：:We report an unusual case of a 12-month-old boy diagnosed with anomalous origin of a single coronary artery from the pulmonary artery associated with patent ductus arteriosus. The patient survival was attributed to left-to-right shunt (patent ductus arteriosus) allowing for appropriate myocardial perfusion. Successful...

journal_title：Cardiology in the young

authors： Hugues N,Dommerc C,Pretre R

更新日期：2020-07-01 00:00:00

abstract：BACKGROUND:Intra-cardiac repair of congenital cardiac diseases in children with left-right shunt is often associated with acute elevation of pulmonary artery pressure following cardiopulmonary bypass. We studied the correlation between the Glu298Asp polymorphism of the endothelial nitric oxide synthase gene and pulmona...

journal_title：Cardiology in the young

authors： Loukanov T,Hoss K,Tonchev P,Klimpel H,Arnold R,Sebening C,Karck M,Gorenflo M

更新日期：2011-04-01 00:00:00

abstract：AIM:Our aim was to review the outcome of ligation of the persistently patent arterial duct in neonates as performed outside a paediatric cardiothoracic centre by an outreach surgical team. METHODS:A retrospective observational study of all ligations of the persistently patent arterial duct performed in Cambridge betwe...

journal_title：Cardiology in the young

authors： Sivakumar S,Lee L,Tillett A,Wells F,Dunning J,Kelsall AW

更新日期：2007-10-01 00:00:00

abstract：INTRODUCTION:Exercise echocardiography assesses exercise-induced pulmonary hypertension. The upper normal limit of right ventricular systolic pressure during exercise is not well established. Our study aims to investigate the response of right ventricular systolic pressure in relation to aerobic capacity. METHODS AND ...

journal_title：Cardiology in the young

authors： Möller T,Peersen K,Pettersen E,Thaulow E,Holmstrøm H,Fredriksen PM

更新日期：2009-09-01 00:00:00

abstract：:To date, no reference values have been provided for right and left atrial filling in normal children. The aim of our study, therefore, was to characterize measurements of superior caval, hepatic, and pulmonary venous flow using Doppler echocardiography in a large group of normal children to reflect the effects of age,...

journal_title：Cardiology in the young

authors： Ayabakan C,Ozkutlu S

更新日期：2003-04-01 00:00:00

abstract：BACKGROUND:The resection of a subaortic membrane remains far from a curative operation. We sought to examine factors associated with reoperation and the degree of aortic valve regurgitation as a potential long-term source for reoperation. METHODS:All patients who underwent resection of an isolated subaortic membrane b...

journal_title：Cardiology in the young

authors： Binsalamah ZM,Spigel ZA,Zhu H,Kim MB,Chacon-Portillo MA,Adachi I,Imamura M,Mery CM,Mckenzie ED,Fraser CD,Heinle JS

更新日期：2019-11-01 00:00:00

abstract：BACKGROUND:Kawasaki disease, which is characterised by systemic vasculitides accompanied by acute fever, is regularly treated by intravenous immunoglobulin to avoid lesion formation in the coronary artery; however, the mechanism of intravenous immunoglobulin therapy is unclear. Hence, we aimed to analyse the global exp...

journal_title：Cardiology in the young

authors： Zhang L,Song QF,Jin JJ,Huang P,Wang ZP,Xie XF,Gu XQ,Gao XJ,Jia HL

更新日期：2017-11-01 00:00:00

abstract：OBJECTIVES:To assess the volume and range of diagnosis in new patients referred to paediatric cardiac outpatient clinics. METHODS:Data was collected prospectively, using a proforma completed at all outpatient clinics over a period of three months. RESULTS:There were 526 new referrals, representing an increase of almo...

journal_title：Cardiology in the young

authors： Murugan SJ,Thomson J,Parsons JM,Dickinson DF,Blackburn ME,Gibbs JL

更新日期：2005-02-01 00:00:00

abstract：BACKGROUND:Few data are available on the neuropsychological, behavioural, or structural brain imaging outcomes in adolescents who underwent corrective surgery in infancy for tetralogy of Fallot. METHODS:In this single-centre cross-sectional study, we enrolled 91 adolescents (13-16 years old) with tetralogy of Fallot a...

journal_title：Cardiology in the young

authors： Bellinger DC,Rivkin MJ,DeMaso D,Robertson RL,Stopp C,Dunbar-Masterson C,Wypij D,Newburger JW

更新日期：2015-02-01 00:00:00

abstract：:We present an example of corrected transposition with twisted discordant atrioventricular connections in which both fetal and postnatal echocardiograms were obtained. We correlate the fetal echocardiograms with the postnatal echocardiograms, placing emphasis on the echocardiographic clues to the diagnosis which were p...

journal_title：Cardiology in the young

authors： Abdullah M,Yoo SJ,Hornberger L

更新日期：2000-10-01 00:00:00

abstract：INTRODUCTION:Infants undergoing stage 1 palliation for hypoplastic left heart syndrome may have post-operative feeding difficulties. Although the cause of feeding difficulties in these patients is multi-factorial, residual arch obstruction may affect gut perfusion, contributing to feeding intolerance. We hypothesised t...

journal_title：Cardiology in the young

authors： Chaves AH,Baker-Smith CM,Rosenthal GL

更新日期：2020-03-01 00:00:00

abstract：:Severe right ventricular failure complicated a postoperative systemic inflammatory response in a 33-year-old woman after surgical repair of congenital cardiac malformations. Volume loading, and high doses of catecholamines, failed to produce improvement, but treatment with vasopressin improved all haemodynamic paramet...

journal_title：Cardiology in the young

authors： Vida VL,Mack R,Castañeda AR

更新日期：2005-02-01 00:00:00

abstract：:In this report, a unique case of a symptomatic vascular ring formed by right aortic arch, aberrant left subclavian artery, and left ligamentum arteriosus in which there is atresia of the proximal left subclavian artery is described. Imaging modalities were non-diagnostic and the patient was sent to surgery based on st...

journal_title：Cardiology in the young

authors： Powell SK,Patel JK,Ebenroth ES

更新日期：2019-01-01 00:00:00

abstract：:We describe a three-year-old boy who presented with recurrent expectoration of bronchial casts six months following creation of a fenestrated lateral tunnel Fontan circulation for pulmonary atresia with intact ventricular septum. Cardiac catheterization demonstrated elevated central venous pressure with two areas of s...

journal_title：Cardiology in the young

authors： McMahon CJ,Nihill MR,Reber A

更新日期：2001-05-01 00:00:00

abstract：:Anomalous origin of a coronary artery from the aorta is a potentially serious anomaly that occurs in about 0.1-0.2% of the population. This percentage is small; however, it translates into about 4000 annual births with these anomalies. The clinical presentation of these anomalies is rare, and hence most are and will r...

journal_title：Cardiology in the young

authors： Hoffman JI

更新日期：2014-10-01 00:00:00

abstract：:We report an extremely rare case of a 14-month-old girl who was diagnosed with a single right coronary artery with coronary artery fistula communicating with the right ventricle and congenital absence of left coronary artery. Angiography showed a dilated and tortuous single right coronary artery draining into the righ...

journal_title：Cardiology in the young

authors： Yoldaş T,Beyazal M,Örün UA

更新日期：2019-11-01 00:00:00

abstract：:Single-nucleotide polymorphisms in miRNA-machinery genes may alter the biogenesis of miRNAs affecting disease susceptibility. In this case-control study, we aimed to evaluate the impact of three single-nucleotide polymorphisms (DICER rs1057035, DROSHA rs10719, and XPO5 rs11077) and their combined effect in a genetic r...

journal_title：Cardiology in the young

authors： Borghini A,Vecoli C,Mercuri A,Turchi S,Andreassi MG

更新日期：2021-01-11 00:00:00

abstract：:Myocardial ischaemia and infarction in pulmonary atresia and intact ventricular septum with right ventricular-dependent coronary circulation is a well-established complication. We report an interesting case of an acquired aneurysm in the ventricular septum in a patient who underwent staged palliation. ...

journal_title：Cardiology in the young

authors： Patel AR,Farrell P,Harris M,Gaynor JW,Gillespie MJ

更新日期：2012-04-01 00:00:00