Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature.

Abstract:

:Pai syndrome is a rare congenital disorder, and there are few reports about the long-term prognosis of mental development and surgical results. Here, we report a patient with Pai syndrome who was followed up from birth up to the age of 8 years. Additionally, we review 32 articles and discuss the long-term prognosis of Pai syndrome. In our case, an intracranial lipoma grew a little, but neither epilepsy nor intellectual disabilities occurred. However, she showed attention-deficit/hyperactivity disorder. Furthermore, her nasal airway was gradually obstructed by a residual intranasal polyp.

authors

Imai Y,Kure S,Nara C,Takagi N,Tachi M

doi

10.1177/1055665618771419

subject

Has Abstract

pub_date

2019-02-01 00:00:00

pages

273-279

issue

2

eissn

1055-6656

issn

1545-1569

journal_volume

56

pub_type

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