Abstract:
:Behçet disease is a systemic vasculitis of unknown etiology that can affect the neurologic system. Neuro-Behçet disease is not well defined in children and adolescents, and the diagnosis is difficult to make in this population as they often present with insufficient symptoms to meet diagnostic criteria. Psychiatric symptoms as the initial manifestation of neuro-Behçet disease has rarely been reported. We describe a 17-year-old boy who presented with acute psychosis and was subsequently diagnosed with neuro-Behçet disease. A rare combination of both cerebral venous thrombosis and parenchymal central nervous system involvement was identified by neuroimaging. Although treatment guidelines for neuro-Behçet disease are limited, the patient made demonstrative clinical and radiographic improvement with a combination of corticosteroids, anticoagulation, and immunosuppressants, including a tumor necrosis factor-α (TNFα) blocking agent.
journal_name
J Child Neuroljournal_title
Journal of child neurologyauthors
Patel P,Steinschneider M,Boneparth A,Lantos Gdoi
10.1177/0883073813504137subject
Has Abstractpub_date
2014-09-01 00:00:00pages
NP86-91issue
9eissn
0883-0738issn
1708-8283pii
0883073813504137journal_volume
29pub_type
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