Group 5 Pulmonary Hypertension: The Orphan's Orphan Disease.

Abstract:

:Pulmonary hypertension is a complex disorder with multiple etiologies; the World Health Organization classification system divides pulmonary hypertension patients into 5 groups based on the underlying cause and mechanism. Group 5 pulmonary hypertension is a heterogeneous group of diseases that encompasses pulmonary hypertension secondary to multifactorial mechanisms. For many of the diseases, the true incidence, etiology, and treatment remain uncertain. This article reviews the epidemiology, pathogenesis, and management of many of the group 5 pulmonary hypertension disease states.

journal_name

Cardiol Clin

journal_title

Cardiology clinics

authors

Kalantari S,Gomberg-Maitland M

doi

10.1016/j.ccl.2016.04.004

subject

Has Abstract

pub_date

2016-08-01 00:00:00

pages

443-9

issue

3

eissn

0733-8651

issn

1558-2264

pii

S0733-8651(16)30017-0

journal_volume

34

pub_type

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