Xanthoma striatum palmare and biliary tract atresia: An unusual association.

abstract：:Cutaneous histiocytosis may take two principal forms. It is either a benign proliferative process or a relentless, progressive process with a poor prognosis. In histiocytic medullary reticulosis, histiocytes demonstrate nuclear atypia and the outcome is uniformly fatal. Benign cephalic histiocytosis X causes lesions s...

journal_title：Pediatric dermatology

authors： Roper SS,Spraker MK

更新日期：1985-11-01 00:00:00

abstract：:We report a 5-month-old girl diagnosed with bullous pemphigoid who initially did not respond to systemic corticosteroids and dapsone but rapidly improved after the addition of intravenous immunoglobulin (IVIG) infusions. A literature search revealed anecdotal cases of infantile bullous pemphigoid treated with IVIG, al...

journal_title：Pediatric dermatology

authors： Tekin B,Yücelten AD

更新日期：2015-09-01 00:00:00

abstract：:Congenital midline cervical cleft is a rare anomaly of the ventral neck that heretofore has not been reported in the dermatology literature. We present a case of a midline cervical cleft that was diagnosed and managed at an early age. We also review the literature and discuss its clinical and histologic features, trea...

journal_title：Pediatric dermatology

authors： Eastlack JP,Howard RM,Frieden IJ

更新日期：2000-03-01 00:00:00

abstract：:X-linked chronic granulomatous disease (CGD), a defect of leukocyte bactericidal capacity, was seen in three generations of a large kindred. The association of discoid lupus erythematosus (DLE) with CGD was noted. Recurrent antigenic stimulation leading to autoantibody formation may explain the apparently increased fr...

journal_title：Pediatric dermatology

authors： Barton LL,Johnson CR

更新日期：1986-11-01 00:00:00

abstract：:Acquired progressive lymphangioma (APL), or benign lymphangioendothelioma, is an unusual entity derived from vascular structures. Clinically and histopathologically it may resemble Kaposi's sarcoma and well-differentiated angiosarcoma, causing a diagnostic problem. We report an individual with APL initially diagnosed ...

journal_title：Pediatric dermatology

authors： Salman A,Sarac G,Can Kuru B,Cinel L,Yucelten AD,Ergun T

更新日期：2017-11-01 00:00:00

abstract：:A newborn boy presented with a progressively infiltrating and painful congenital ulcerated plaque on the back of his left foot. A partial excision was performed and histopathologic examination confirmed a diagnosis of a plexiform fibrohistiocytic tumor. This rare tumor usually appears in children and adolescents, with...

journal_title：Pediatric dermatology

authors： Nieto D,Feito M,Rueda JM,Rodríguez A,Berjón A,López JC,de Lucas R

更新日期：2018-11-01 00:00:00

abstract：:Although papulonecrotic tuberculid is an uncommon cutaneous manifestation of tuberculosis (TB) associated with Mycobacterium tuberculosis infection, the simultaneous occurrence of papulonecrotic tuberculid and erythema induratum is even rarer. Papulonecrotic tuberculid occurs predominantly in young adults and is chara...

journal_title：Pediatric dermatology

authors： Kim GW,Park HJ,Kim HS,Chin HW,Kim SH,Ko HC,Kim MB,Kim BS

更新日期：2013-03-01 00:00:00

abstract：:Autosomal recessive congenital ichthyosis is a genetically and phenotypically heterogenous group of scaling skin disorders. We describe a patient with ARCI caused by homozygous variants in NIPAL4, in whom the dermatologic phenotype and an associated arthropathy, markedly improved with ustekinumab. ...

journal_title：Pediatric dermatology

authors： Poulton C,Gration D,Murray K,Baynam G,Halbert A

更新日期：2019-11-01 00:00:00

abstract：:Linear immunoglobulin A bullous dermatosis (LABD) is an autoimmune blistering disease that most commonly presents in preschool-aged children. There have been few neonatal reports, all of which had life-threatening aerodigestive complications requiring mechanical intervention and systemic therapy. We present a case of ...

journal_title：Pediatric dermatology

authors： Julapalli MR,Brandon KL,Rosales CM,Grover RK,Plunkett RW,Metry DW

更新日期：2012-09-01 00:00:00

abstract：:We report a girl with lipophagic lobular panniculitis of unknown origin located on her ankles leading to circumferential fat atrophy of the ankles, a condition usually referred to as "annular lipoatrophy of the ankles." According to our patient's features and five additional cases reported so far, we conclude that thi...

journal_title：Pediatric dermatology

authors： Corredera C,Iglesias M,Hernández-Martín A,Colmenero I,Dilme E,Torrelo A

更新日期：2011-03-01 00:00:00

abstract：:The human papillomavirus (HPV) infects the squamous epithelium of the skin and produces common warts, plantar warts, and flat warts, which occur commonly on the hands, face, and feet. The objective of this study was to determine the presence of HPV in warts in children in order to associate the virus with the disease....

journal_title：Pediatric dermatology

authors： Giannaki M,Kakourou T,Theodoridou M,Syriopoulou V,Kabouris M,Louizou E,Chrousos G

更新日期：2013-11-01 00:00:00

abstract：:A 9-year-old girl newly diagnosed with systemic lupus erythematosus (SLE) developed a localized linear papulovesicular eruption over the right dorsal hand and ulnar forearm. The skin findings were clinically suggestive of herpes zoster, lichen striatus, or lichen planus-lupus erythematosus overlap. However, histologic...

journal_title：Pediatric dermatology

authors： Roholt NS,Lapiere JC,Wang JI,Bernstein LJ,Woodley DT,Eramo LR

更新日期：1995-06-01 00:00:00

abstract：:When vulvar lichen sclerosus occurs in prepubertal children it is widely believed that it is likely to remit at puberty. However when it occurs in adult women it is accepted that remission is unlikely and that in addition untreated or inadequately treated disease may be complicated by significant disturbance of vulvar...

journal_title：Pediatric dermatology

authors： Smith SD,Fischer G

更新日期：2009-11-01 00:00:00

abstract：:Benign cephalic histiocytosis is a rare skin condition consisting of small tan papules on the face and upper trunk that is believed not to be associated with internal organ involvement. The infiltrating histiocytes are not Langerhans' cells (LCs). We report a 5-year-old girl who presented with diabetes insipidus 1 yea...

journal_title：Pediatric dermatology

authors： Weston WL,Travers SH,Mierau GW,Heasley D,Fitzpatrick J

更新日期：2000-07-01 00:00:00

abstract：:Dyskeratosis congenita (DC) is an unusual inherited disease characterized by the triad of mucosal leukoplakia, nail dystrophy, and skin pigmentation. Hyperkeratosis of the palms and soles is another reported skin finding. This hyperkeratosis can lead to fissures, chronic erosion, and deep ulcerations. These atypical w...

journal_title：Pediatric dermatology

authors： Quintana-Castanedo L,Feito-Rodríguez M,Pérez-Conde I,Maseda-Pedrero R,Chiloeches-Fernández C,de Lucas Laguna R

更新日期：2020-11-01 00:00:00

abstract：:Henoch-Schönlein purpura (HSP) is an acute systemic vasculitis with unknown etiology, although several studies have found HSP to be related to cytokines such as tumor necrosis factor α, interleukin (IL)-1, and adhesion molecules. In the present study we determined the levels of cytokines such as IL-18 and endothelin-1...

journal_title：Pediatric dermatology

authors： Mahajan N,Kapoor D,Bisht D,Singh S,Minz RW,Dhawan V

更新日期：2013-11-01 00:00:00

abstract：:Our objective was to establish the aerobic and anaerobic microbiology of nonbullous impetigo (NI) in children. We used a retrospective review of clinical microbiology laboratory and patients' records. Specimens were obtained from 40 patients with NI lesions and showed bacterial growth. Aerobic or facultative anaerobic...

journal_title：Pediatric dermatology

authors： Brook I,Frazier EH,Yeager JK

更新日期：1997-05-01 00:00:00

abstract：:From January 2010 to December 2012, 296 skin biopsies were performed in pediatric patients using only local anesthesia (cream and infiltration). The biopsies were divided into three groups: biopsies of skin neoplasms, biopsies of skin rashes and biopsies of follicular-centered lesions. Our data demonstrate the possibi...

journal_title：Pediatric dermatology

authors： D'Acunto C,Raone B,Neri I,Passarini B,Patrizi A

更新日期：2015-05-01 00:00:00

abstract：:Normolipemic plane xanthoma normally occurs in adults. We report the atypical instance of a 9-year-old boy who developed disseminated, flat, yellow-brown plaques up to 2 to 3 cm without any complaints. The histology showed the hallmarks of xanthoma, including the presence of CD68+ foam cells and Touton giant cells. No...

journal_title：Pediatric dermatology

authors： Hofmann M,Zappel K,Trefzer U,Audring H,Albrecht-Nebe H,Sterry W,Blume-Peytavi U

更新日期：2005-03-01 00:00:00

abstract：:Cerebriform intradermal nevus is a rare form of cutis verticis gyrata. Clinically it manifests as a scalp deformity resembling the surface of the brain, with cerebriform morphologic characteristics. Degeneration into malignant melanoma has been reported. Herein, a cerebriform intradermal nevus of the scalp in a 7-year...

journal_title：Pediatric dermatology

authors： Yazici AC,Ikizoglu G,Baz K,Polat A,Ustunsoy D

更新日期：2007-03-01 00:00:00

abstract：:Although the prognosis of maculopapular cutaneous mastocytosis (MPCM), also referred to as urticaria pigmentosa, is often benign, clinicians lack evidence to reliably predict those at risk of associated systemic manifestations. We sought to elucidate clinical markers of disease severity to provide better treatment and...

journal_title：Pediatric dermatology

authors： Barnes M,Van L,DeLong L,Lawley LP

更新日期：2014-05-01 00:00:00

abstract：:An 8-year-old girl had pseudoxanthoma elasticum (PXE) with the characteristic skin and ocular findings. She had no associated systemic symptoms and no family history of PXE. The disease was most likely inherited in an autosomal recessive fashion. It is reviewed with regard to etiology, inheritance, diagnosis, and, par...

journal_title：Pediatric dermatology

authors： Hacker SM,Ramos-Caro FA,Beers BB,Flowers FP

更新日期：1993-03-01 00:00:00

abstract：:Discoid lupus erythematosus (DLE) is rare in childhood. We report the case of a 5-year-old girl who presented with erythematous scaly plaques, with scarring alopecia, involving approximately 40% of her scalp. Histopathology confirmed the diagnosis of DLE. Treatment with intravenous methylprednisolone, hydroxychloroqui...

journal_title：Pediatric dermatology

authors： Miettunen PM,Bruecks A,Remington T

更新日期：2009-05-01 00:00:00

abstract：OBJECTIVES:To identify clinical factors associated with complications of periocular infantile hemangioma (IH) and monitor improvement in complication rates post-treatment. METHODS:Retrospective cohort study. Eighty-nine patients diagnosed with periocular IH at a pediatric dermatology clinic of a tertiary care center b...

journal_title：Pediatric dermatology

authors： Zhao J,Huang AH,Rainer BM,Kryatova MS,Eghrari AO,Wang J,Puttgen KB,Cohen BA

更新日期：2019-11-01 00:00:00

abstract：:Langerhans cell histiocytosis (LCH) is a rare disorder characterized by clonal proliferation of Langerhans cells in the skin. A molluscum-like presentation of cutaneous LCH is rare but important to consider for examination and management. We present an atypical molluscum-like LCH case and review the literature for com...

journal_title：Pediatric dermatology

authors： Karpman MS,AlJasser MI,Lam JM

更新日期：2017-09-01 00:00:00

abstract：:Mutations in the p63 gene have been identified in five human disorders characterized by varying degrees of limb anomalies, ectodermal dysplasia, and facial clefts. We report a new point mutation in the p63 gene in a family in which the mother was initially diagnosed with Rapp-Hodgkin syndrome and her two offspring man...

journal_title：Pediatric dermatology

authors： Steele JA,Hansen H,Arn P,Kwong PC

更新日期：2005-09-01 00:00:00

abstract：BACKGROUND:Fibroblastic connective tissue nevi (FCTN) are benign skin conditions characterized by bland spindle cells infiltrating the reticular dermis and the upper subcutis with preservation of adnexal structures. A subset of FCTN expresses CD34, which may cause difficulties in the differential diagnosis, in particul...

journal_title：Pediatric dermatology

authors： Bouaoud J,Fraitag S,Soupre V,Mitrofanoff M,Boccara O,Galliot C,Bodemer C,Picard A,Khonsari RH

更新日期：2018-09-01 00:00:00

abstract：BACKGROUND:Children with congenital melanocytic nevi (CMN) were historically managed with surgical removal to lower the risk of malignant transformation. The evolving literature over the last decade has indicated a significantly lower risk than previously estimated. Indications for excision currently revolve around aes...

journal_title：Pediatric dermatology

authors： Mosa A,Ho ES,Heinelt M,Wong K,Neuhaus K

更新日期：2019-11-01 00:00:00

abstract：:We report two cases of focal preauricular dermal dysplasia and review the available literature. Focal preauricular dermal dysplasia is a form of aplasia cutis congenita in which atrophic skin lesions occur in a stereotypical bilateral distribution in the preauricular region. Although focal preauricular dermal dysplasi...

journal_title：Pediatric dermatology

authors： Krathen MS,Rosenbach M,Yan AC,Crawford GH

更新日期：2008-05-01 00:00:00

abstract：:Generalized chronic cutaneous lupus including lupus panniculitis in childhood is rare and usually occurs in the setting of genetic complement deficiencies. The association with antiphospholipid syndrome is even more rare. We report a 13-year-old girl with extensive lupus panniculitis since the age of 8 months and no e...

journal_title：Pediatric dermatology

authors： Nousari HC,Kimyai-Asadi A,Santana HM,Diglio GM,Tausk FA,Cohen BA

更新日期：1999-07-01 00:00:00