Abstract:
:A family with 12 children, 6 of whom had Sjögren-Larsson syndrome, was studied clinically. On CT, all six siblings with the disease had patchy regions of white matter hypodensity, most marked in the frontal lobes, which were confluent in the more severe cases. The ventricles were not enlarged and no other abnormality was demonstrated. The CTs of the 6 unaffected siblings and the mother, who was also unaffected by the disease, were normal.
journal_name
Neuroradiologyjournal_title
Neuroradiologyauthors
Gomori JM,Leibovici V,Zlotogorski A,Wirguin I,Haham-Zadeh Sdoi
10.1007/BF00350440subject
Has Abstractpub_date
1987-01-01 00:00:00pages
557-9issue
6eissn
0028-3940issn
1432-1920journal_volume
29pub_type
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