Clinical findings for a group of infants and young children with auditory neuropathy.

Abstract:

OBJECTIVE:To examine the prevalence of auditory neuropathy in a group of infants at risk for hearing impairment and to present an overview of the clinical findings for affected children. DESIGN:Results for 20 subjects who showed repeatable cochlear microphonic potentials in the absence of click-evoked auditory brain stem responses are included in this study. Behavioral and steady state evoked potential thresholds were established in each case. Where possible, otoacoustic emission and speech perception results (unaided and aided) also were obtained. RESULTS:One in 433 (0.23%) of the children in our series had evidence of auditory neuropathy. The audiometric findings for these subjects varied significantly, with behavioral thresholds ranging from normal to profound levels. Discrimination skills were also variable. Approximately half of the subjects showed little understanding, or even awareness, of speech inputs in both the unaided and aided conditions. There were, however, a number of children who could score at significant levels on speech discrimination tasks and who benefited from the provision of amplification. CONCLUSION:The results suggest that auditory neuropathy is more common in the infant population than previously suspected. The effects of neuropathy on auditory function appear to be idiosyncratic, producing significant variations in both the detection and discrimination of auditory signals. As such, the management of children with this disorder must allow for individual differences.

journal_name

Ear Hear

journal_title

Ear and hearing

authors

Rance G,Beer DE,Cone-Wesson B,Shepherd RK,Dowell RC,King AM,Rickards FW,Clark GM

doi

10.1097/00003446-199906000-00006

subject

Has Abstract

pub_date

1999-06-01 00:00:00

pages

238-52

issue

3

eissn

0196-0202

issn

1538-4667

journal_volume

20

pub_type

杂志文章
  • Identification of neonatal hearing impairment: auditory brain stem responses in the perinatal period.

    abstract:OBJECTIVES:1) To describe the auditory brain stem response (ABR) measurement system and optimized methods used for study of newborn hearing screening. 2) To determine how recording and infant factors related to the screening, using well-defined, specific ABR outcome measures. DESIGN:Seven thousand one hundred seventy-...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-200010000-00006

    authors: Sininger YS,Cone-Wesson B,Folsom RC,Gorga MP,Vohr BR,Widen JE,Ekelid M,Norton SJ

    更新日期:2000-10-01 00:00:00

  • Effects of presentation level on phoneme and sentence recognition in quiet by cochlear implant listeners.

    abstract:OBJECTIVE:The objectives of this study were to characterize the effects of presentation level on speech recognition in quiet by cochlear implant users with the Nucleus 22 SPEAK and Clarion v1.2 CIS speech-processing strategies, and to relate speech recognition at low presentation levels to stimulus audibility as measur...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/01.AUD.0000090340.09847.39

    authors: Donaldson GS,Allen SL

    更新日期:2003-10-01 00:00:00

  • Reducing Simulated Channel Interaction Reveals Differences in Phoneme Identification Between Children and Adults With Normal Hearing.

    abstract:OBJECTIVES:Channel interaction, the stimulation of overlapping populations of auditory neurons by distinct cochlear implant (CI) channels, likely limits the speech perception performance of CI users. This study examined the role of vocoder-simulated channel interaction in the ability of children with normal hearing (cN...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000615

    authors: Jahn KN,DiNino M,Arenberg JG

    更新日期:2019-03-01 00:00:00

  • Pre- and Postoperative Binaural Unmasking for Bimodal Cochlear Implant Listeners.

    abstract:OBJECTIVES:Cochlear implants (CIs) are increasingly recommended to individuals with residual bilateral acoustic hearing. Although new hearing-preserving electrode designs and surgical approaches show great promise, CI recipients are still at risk to lose acoustic hearing in the implanted ear, which could prevent the ab...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000420

    authors: Sheffield BM,Schuchman G,Bernstein JGW

    更新日期:2017-09-01 00:00:00

  • Children's recognition of spectrally degraded cartoon voices.

    abstract:OBJECTIVES:Although the spectrally degraded input provided by cochlear implants (CIs) is sufficient for speech perception in quiet, it poses problems for talker identification. The present study examined the ability of normally hearing (NH) children and child CI users to recognize cartoon voices while listening to spec...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0b013e3182a468d0

    authors: van Heugten M,Volkova A,Trehub SE,Schellenberg EG

    更新日期:2014-01-01 00:00:00

  • Hearing aid patients in private practice and public health (Veterans Affairs) clinics: are they different?

    abstract:OBJECTIVE:In hearing aid research, it is commonplace to combine data across subjects whose hearing aids were provided in different service delivery models. There is reason to question whether these types of patients are always similar enough to justify this practice. To explore this matter, this investigation evaluated...

    journal_title:Ear and hearing

    pub_type: 杂志文章,多中心研究

    doi:10.1097/01.aud.0000188188.01311.0b

    authors: Cox RM,Alexander GC,Gray GA

    更新日期:2005-12-01 00:00:00

  • Predictive properties of the video head impulse test: measures of caloric symmetry and self-report dizziness handicap.

    abstract:OBJECTIVES:The purpose of this investigation was to determine whether a predictable relationship existed between self-reported dizziness handicap and video Head Impulse Test (vHIT) results in a large sample of patients reporting to a dizziness clinic. Secondary objectives included describing the characteristics of the ...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000047

    authors: McCaslin DL,Jacobson GP,Bennett ML,Gruenwald JM,Green AP

    更新日期:2014-09-01 00:00:00

  • Evoked potentials: computer-automated threshold-tracking procedure using an objective detection criterion.

    abstract::A computer-automated, threshold-tracking procedure was developed for measuring evoked response thresholds on-line. The procedure utilizes an objective detection criterion (correlation) to evaluate whether a response is absent or present. Sound intensity is adjusted according to a modified PEST (parameter estimation by...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:

    authors: Salvi RJ,Ahroon W,Saunders SS,Arnold SA

    更新日期:1987-06-01 00:00:00

  • Peripheral Auditory Involvement in Childhood Listening Difficulty.

    abstract:OBJECTIVES:This study tested the hypothesis that undetected peripheral hearing impairment occurs in children with idiopathic listening difficulties (LiDs), as reported by caregivers using the Evaluation of Children"s Listening and Processing Skills (ECLiPS) validated questionnaire, compared with children with typically...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000899

    authors: Hunter LL,Blankenship CM,Lin L,Sloat NT,Perdew A,Stewart H,Moore DR

    更新日期:2020-06-25 00:00:00

  • Hearing in time: evoked potential studies of temporal processing.

    abstract::This article reviews the temporal aspects of human hearing as measured using the auditory evoked potentials. Interaural timing cues are essential to the detection and localization of sound sources. The temporal envelope of a sound--how it changes in amplitude over time--is crucially important for speech perception. Ti...

    journal_title:Ear and hearing

    pub_type: 杂志文章,评审

    doi:10.1097/AUD.0b013e31827ada02

    authors: Picton T

    更新日期:2013-07-01 00:00:00

  • Developmental effects and spatial hearing in young children with normal-hearing sensitivity.

    abstract:OBJECTIVES:Previous research suggests that young children have significant difficulty recognizing speech in the presence of background noise as compared with older children and adults. However, limited research exists that examines the developmental effects of speech recognition in noise in separate age groups of young...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0b013e318258c616

    authors: Schafer EC,Beeler S,Ramos H,Morais M,Monzingo J,Algier K

    更新日期:2012-11-01 00:00:00

  • Otodental dysplasia: a five year study.

    abstract::Peripheral auditory sensitivity is documented over a 5-year period on 4 cases with otodental dysplasia. Age of onset is noted for the proband and indicates that onset of this progressive hearing loss occurs as early as the first decade. Findings suggest that the hearing loss plateaus by the fourth decade, resulting in...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-198103000-00007

    authors: Cook RA,Cox JR,Jorgenson RJ

    更新日期:1981-03-01 00:00:00

  • Labeling of musical interval size by cochlear implant patients and normally hearing subjects.

    abstract:OBJECTIVE:To compare the performance of cochlear implant patients and normal-hearing subjects on a musical interval labeling task, and to determine whether information regarding musical interval size is available to cochlear implant patients under realistic everyday listening conditions. DESIGN:Two Nucleus cochlear im...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-199710000-00002

    authors: Pijl S

    更新日期:1997-10-01 00:00:00

  • Perception of rhythmic and sequential pitch patterns by normally hearing adults and adult cochlear implant users.

    abstract:OBJECTIVE:This study compares the musical perception of 17 adult recipients of the Nucleus cochlear implant using two different formant extraction processing strategies (F0F1F2 and MPEAK). DESIGN:Over a 12 mo period, participants were alternately switched between two strategies every 3 mo. Performance was evaluated us...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-199706000-00008

    authors: Gfeller K,Woodworth G,Robin DA,Witt S,Knutson JF

    更新日期:1997-06-01 00:00:00

  • The influence of RECD transducer when deriving real-ear sound pressure level.

    abstract:OBJECTIVE:The main aim of the present study was to compare the derived and directly measured real-ear hearing instrument performance for a range of commonly used hearing instruments. A secondary aim was to compare the real-ear to coupler difference (RECD) measured using the ER-3A insert earphone and a selection of hear...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/01.aud.0000224123.22568.82

    authors: Munro KJ,Millward KE

    更新日期:2006-08-01 00:00:00

  • Effects of reference interaural time and intensity differences on binaural performance in listeners with normal and impaired hearing.

    abstract:OBJECTIVE:The purpose of this research was to measure the effects of reference interaural time and intensity differences on binaural performance in listeners with normal hearing and impaired hearing for a number of different binaural tests. Experiment 1 measures the dependence of binaural detection and discrimination p...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-199508000-00001

    authors: Koehnke J,Culotta CP,Hawley ML,Colburn HS

    更新日期:1995-08-01 00:00:00

  • Multisite Randomized Controlled Trial to Compare Two Methods of Tinnitus Intervention to Two Control Conditions.

    abstract:OBJECTIVES:In this four-site clinical trial, we evaluated whether tinnitus masking (TM) and tinnitus retraining therapy (TRT) decreased tinnitus severity more than the two control groups: an attention-control group that received tinnitus educational counseling (and hearing aids if needed; TED), and a 6-month-wait-list ...

    journal_title:Ear and hearing

    pub_type: 杂志文章,多中心研究,随机对照试验

    doi:10.1097/AUD.0000000000000330

    authors: Henry JA,Stewart BJ,Griest S,Kaelin C,Zaugg TL,Carlson K

    更新日期:2016-11-01 00:00:00

  • Immediate and Short-Term Therapeutic Results Between Direction-Changing Positional Nystagmus with Short- and Long-Duration Groups.

    abstract:OBJECTIVES:Clinicians sometimes treat patients with relatively long-duration geotropic direction-changing positional nystagmus (DCPN), without latency. Recently, the concept of a "light cupula" in the lateral canal that reveals persistent geotropic DCPN has been introduced. In the present study, we investigated the imm...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000232

    authors: Ban JH,Kim MB,Hong SM

    更新日期:2016-03-01 00:00:00

  • The effect of differential listening experience on the development of expressive and receptive language in children with bilateral cochlear implants.

    abstract:OBJECTIVES:Growing evidence suggests that children who are deaf and use cochlear implants (CIs) can communicate effectively using spoken language. Research has reported that age of implantation and length of experience with the CI play an important role in a predicting a child's linguistic development. In recent years,...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000023

    authors: Hess C,Zettler-Greeley C,Godar SP,Ellis-Weismer S,Litovsky RY

    更新日期:2014-07-01 00:00:00

  • Spectral-Temporal Modulated Ripple Discrimination by Children With Cochlear Implants.

    abstract:OBJECTIVES:A postlingually implanted adult typically develops hearing with an intact auditory system, followed by periods of deafness (or near deafness) and adaptation to the implant. For an early implanted child whose brain is highly plastic, the auditory system matures with consistent input from a cochlear implant. I...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000463

    authors: Landsberger DM,Padilla M,Martinez AS,Eisenberg LS

    更新日期:2018-01-01 00:00:00

  • Different Associations between Auditory Function and Cognition Depending on Type of Auditory Function and Type of Cognition.

    abstract:OBJECTIVES:Previous studies strongly suggest that declines in auditory threshold can lead to impaired cognition. The aim of this study was to expand that picture by investigating how the relationships between age, auditory function, and cognitive function vary with the types of auditory and cognitive function considere...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000700

    authors: Danielsson H,Humes LE,Rönnberg J

    更新日期:2019-09-01 00:00:00

  • Use of probe tube microphone measurements in hearing aid selection for children: some initial clinical experiences.

    abstract::Some initial experiences are described in which ear canal probe tube microphone measurements are used to determine hearing aid settings for children. Decisions are based upon ideas developed by Seewald and Ross (in Amplification for the Hearing Impaired, New York: Grune & Stratton, 1988: 213-267) and Seewald, Ross, an...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-198910000-00002

    authors: Hawkins DB,Morrison TM,Halligan PL,Cooper WA

    更新日期:1989-10-01 00:00:00

  • Effects of the number of channels and speech-to-noise ratio on rate of connected discourse tracking through a simulated cochlear implant speech processor.

    abstract:OBJECTIVE:To investigate the effects of number of channels and speech-to-noise ratio on connected discourse tracking (CDT) through simulations of cochlear implant speech processing. Previous studies have used citation-form vowel and consonant materials or simple sentences. CDT rates were expected to be less likely to b...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-200110000-00007

    authors: Faulkner A,Rosen S,Wilkinson L

    更新日期:2001-10-01 00:00:00

  • Detectability of transient and sinusoidal otoacoustic emissions.

    abstract::An analysis is presented of the detectability of the two types of otoacoustic emissions being considered for use in clinical tests of hearing. It is estimated that, for equal emission levels and equal probability of error, measurement of distortion-product emissions can be made at least 30 times faster than transient-...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-199210000-00008

    authors: Zurek PM

    更新日期:1992-10-01 00:00:00

  • Speech recognition ability of children with unilateral sensorineural hearing loss as a function of amplification, speech stimuli and listening condition.

    abstract::The purpose of this investigation was to examine three types of audiological recommendations [unaided, CROS (contralateral routing of signals) and personal FM system] and their impact upon speech recognition ability of children with unilateral sensorineural hearing loss. Each of these recommendations was tested under ...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-199008000-00003

    authors: Kenworthy OT,Klee T,Tharpe AM

    更新日期:1990-08-01 00:00:00

  • Speech-in-speech listening on the LiSN-S test by older adults with good audiograms depends on cognition and hearing acuity at high frequencies.

    abstract:OBJECTIVES:The main objective was to investigate age-related differences on the listening in spatialized noise-sentences (LiSN-S) test in adults with normal audiometric thresholds in most of the speech range. A second objective was to examine the contributions of auditory, cognitive, and linguistic abilities to LiSN-S ...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000096

    authors: Besser J,Festen JM,Goverts ST,Kramer SE,Pichora-Fuller MK

    更新日期:2015-01-01 00:00:00

  • Acoustic radiation produced by B-71, B-72, and KH 70 bone vibrators.

    abstract::The amount of acoustic radiation produced by two samples of a Radioear B-71, B-72, and Pracitronic KH 70 bone vibrator was determined for 30 normal-hearing subjects at 4000 Hz. The mean amount of acoustic radiation was very similar for both samples of each vibrator type but significantly (p less than 0.05) different b...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-198610000-00010

    authors: Frank T,Crandell CC

    更新日期:1986-10-01 00:00:00

  • Signal to noise constraints on maximum length sequence auditory brain stem responses.

    abstract::In conventional auditory brain stem response (ABR) testing, the stimulus rate must be low enough that the responses do not overlap. By using stimulus patterns derived from the pseudorandom binary series known as maximum length sequences (MLSs), it is possible to stimulate at mean rates of hundreds of clicks per second...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/00003446-199212000-00004

    authors: Marsh RR

    更新日期:1992-12-01 00:00:00

  • Cost-Effective Hearing Conservation: Regulatory and Research Priorities.

    abstract::Hearing conservation programs (HCPs) mandated by the US Occupational Safety and Health Administration (OSHA) cost about $350/worker/year. Are they cost-effective? A cross-sectional model of the US adult population with and without HCPs incorporates (1) the American Medical Association's method for estimating binaural ...

    journal_title:Ear and hearing

    pub_type: 社论

    doi:10.1097/AUD.0000000000000523

    authors: Dobie RA

    更新日期:2018-07-01 00:00:00

  • Auditory Impairments in HIV-Infected Children.

    abstract:OBJECTIVES:In a cross-sectional study of human immunodeficiency virus (HIV)-infected adults, the authors showed lower distortion product otoacoustic emissions (DPOAEs) in HIV+ individuals compared with controls as well as findings consistent with a central auditory processing deficit in HIV+ adults on antiretroviral th...

    journal_title:Ear and hearing

    pub_type: 杂志文章

    doi:10.1097/AUD.0000000000000276

    authors: Maro II,Fellows AM,Clavier OH,Gui J,Rieke CC,Wilbur JC,Chambers RD,Jastrzembski BG,Mascari JE,Bakari M,Matee M,Musiek FE,Waddell RD,von Reyn CF,Palumbo PE,Moshi N,Buckey JC

    更新日期:2016-07-01 00:00:00