Abstract:
:Dominantly inherited syndromes of colorectal cancer predisposition are characterized by multifocal neoplasia with an early age of onset. The risk of colorectal cancer is high in affected patients and care of the patients is based on the aims of cancer prevention and cancer cure. At the same time, quality of life should be disturbed as little as possible. Because patients are generally young, the stakes are high. Injudicious decision-making can have unfortunate effects on patients and families. In this article the controversial aspects of surgery in familial adenomatous polyposis and Lynch syndrome are discussed. Specifically the controversies in familial adenomatous polyposis include the timing and the type of surgery while for Lynch syndrome discussion revolves about prophylactic surgery, primary, secondary and tertiary.
journal_name
Fam Cancerjournal_title
Familial cancerauthors
Church JMdoi
10.1007/s10689-016-9886-4subject
Has Abstractpub_date
2016-07-01 00:00:00pages
447-51issue
3eissn
1389-9600issn
1573-7292pii
10.1007/s10689-016-9886-4journal_volume
15pub_type
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