Abstract：
BACKGROUND:Cardiac involvement may precede the onset of muscular manifestations in Becker muscular dystrophy (BMD), but Wolff-Parkinson-White (WPW) syndrome has not been reported as initial cardiac manifestation of BMD. CASE STUDY:In a 43-year-old, HIV-negative male, WPW syndrome was diagnosed at age 26 years upon a routine surface ECG, carried out for recurrent palpitations since childhood. Since then, WPW syndrome was occasionally found on repeated cardiologic follow-up investigations. From age 27 years, he developed proximal muscle weakness predominantly of the lower limbs, a positive Gower sign, and a waddling gait. Needle electromyograms were repeatedly myogenic, and upon reinvestigation at age 42 years, a deletion of exons 45-47 in the dystrophin gene was detected. Radiofrequency catheter ablation, initially refused by the patient, was scheduled again but no accessory pathways were detected on electrophysiological investigations. CONCLUSION:This case suggests that intermittent WPW syndrome may be a cardiac manifestation of BMD and that cardiac involvement may precede the development of evident skeletal muscle abnormalities.
journal_name
Herzjournal_title
Herzauthors
Finsterer J,Stöllberger C,Quasthoff Sdoi
10.1007/s00059-008-3023-6subject
Has Abstractpub_date
2008-06-01 00:00:00pages
307-10issue
4eissn
0340-9937issn
1615-6692journal_volume
33pub_type
杂志文章相关文献
HERZ文献大全abstract：BACKGROUND:The emerging term "visceral adiposity index (VAI)" was reported to be closely correlated with glycemic disturbances and diabetes risk. However, whether VAI could predict future type 2 diabetes mellitus (DM) is unknown. Here, we aimed to assess the predictive value of VAI for DM in a Chinese population via a ...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-014-4175-1
更新日期：2015-05-01 00:00:00
abstract：:The impaired cardiac performance in patients with congestive cardiac failure may be improved by the introduction of inotropic therapy. Dopamine and dobutamine are both potent cardiac stimulants although their haemodynamic profile is different. Dobutamine would appear to be the more appropriate choice in cardiac failur...
journal_title：Herz
pub_type： 杂志文章
doi：
更新日期：1983-02-01 00:00:00
abstract：:Eosinophilic myocarditis is caused by activation of eosinophilic granulocytes whereby there is a release of eosinophilic granules. Quite a few of the released compounds, especially eosinophilic cationic proteins, have a tissue-damaging effect also in the myocardium. Eosinophilia may be due to hypersensitivity, parasit...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-012-3701-2
更新日期：2012-12-01 00:00:00
abstract：:Remodelling is the adaptive or maladaptive response to cardiac overload or injury resulting in changes of size and function of the heart. The final pathway of maladaptive or adverse cardiac remodelling is the evolution of heart failure or sudden cardiac death. In coronary artery disease, ischemic injury leads to chang...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-012-3660-7
更新日期：2012-09-01 00:00:00
abstract：:Despite great advances in the pathophysiology and etiology of myocarditis, the clinical diagnosis of myocarditis in daily clinical practise remains challenging. Often the diagnosis was not clear because of the heterogeneity of clinical symptoms and the lack of guidelines for adequate diagnostic requirements and consec...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-013-3988-7
更新日期：2013-12-01 00:00:00
abstract：BACKGROUND:The current study aimed to evaluate the influence of regular annual influenza vaccinations on cardiovascular (CV) death and heart failure-related hospitalizations (HFrH) in stable outpatients with heart failure with reduced ejection fraction. METHODS:The Turkish research team-HF (TREAT-HF) is a network unde...
journal_title：Herz
pub_type： 临床试验,杂志文章
doi：10.1007/s00059-016-4460-2
更新日期：2017-05-01 00:00:00
abstract：:In patients with chronic coronary artery disease different therapeutic strategies, such as optimal medical therapy, revascularization by percutaneous coronary intervention or coronary artery bypass grafting have been shown to improve the prognosis and symptoms and yield proven superiority over other treatment strategi...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-013-3803-5
更新日期：2013-06-01 00:00:00
abstract：:This review summarizes some information on the management of diabetic patients at risk for or with already established coronary artery disease. Improved knowledge among diabetologists regarding treatment and prevention of cardiovascular complications and among cardiologists regarding diabetology is a prerequisite for ...
journal_title：Herz
pub_type： 杂志文章,评审
doi：10.1007/s00059-008-3105-5
更新日期：2008-04-01 00:00:00
abstract：:While there is generell agreement that patients with aortic stenosis (AS) who have already developed symptoms, such as exertional dyspnea, angina or dizziness and syncope, require urgent surgery because of their otherwise very poor outcome, the management of asymptomatic severe AS remains controversial. Although preve...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-006-2871-1
更新日期：2006-10-01 00:00:00
abstract：:The natural history of hypertrophic obstructive cardiomyopathy is characterized, in particular, in younger patients by sudden cardiac death, in the majority of patients by progressive congestive heart failure [14, 26, 27, 33-36]. With the aid of beta-adrenergic receptor blockers, calcium channel blockers and antiarrhy...
journal_title：Herz
pub_type： 杂志文章
doi：
更新日期：1985-04-01 00:00:00
abstract：BACKGROUND:The German national guidelines on chronic heart failure provide treatment recommendations to physicians and reflect the current level of evidence; however, it is questionable to what extent these recommendations are applied in the routine practice and what the effect of guideline adherence on mortality is. ...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-016-4401-0
更新日期：2016-11-01 00:00:00
abstract：:Diastolic function in coronary artery disease is modified to a variable extent. There are distinct abnormalities produced during acute ischemia, and following myocardial infarction. The pathophysiology of diastolic abnormalities in these two syndromes is reviewed. During acute ischemia filling pressures of the left ve...
journal_title：Herz
pub_type： 杂志文章,评审
doi：
更新日期：1991-02-01 00:00:00
abstract：CASE REPORT:A 41-year-old male saw his general practitioner because of progressive atypical angina symptoms and palpitations for the last 7 years. Chest X-ray showed a mediastinal mass. Further investigation by computed tomography (CT), magnetic resonance imaging (MRI) and cardiac catheterization revealed two bronchoge...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-002-2366-7
更新日期：2002-12-01 00:00:00
abstract：:The post-cardiac transplantation patient is frequently debilitated as a result of "end-stage" heart disease and typically demonstrates muscle wasting, with a reduced work capacity, maximum heart rate and peak oxygen uptake. At submaximal effort perceived exertion and ventilation are higher, and the absolute ventilator...
journal_title：Herz
pub_type： 杂志文章,评审
doi：
更新日期：1991-08-01 00:00:00
abstract：BACKGROUND:Upon coincubation with platelet aggregates, CD34(+) progenitor cells have the potential to differentiate into foam cells. There is evidence that progenitor cells from diabetic and nondiabetic patients have different properties, which may affect the patients' prognosis. In this study we investigated an in vit...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-013-4012-y
更新日期：2015-05-01 00:00:00
abstract：OBJECTIVES:Little is known about cardiac involvement in m.3243A>G variant carriers. Thus, this study aimed to assess type and frequency of cardiac disease in symptomatic and asymptomatic m.3243A>G carriers. METHODS:Systematic literature review. RESULTS:The m.3243A>G variant may manifest phenotypically as mitochondria...
journal_title：Herz
pub_type： 杂志文章,评审
doi：10.1007/s00059-018-4739-6
更新日期：2020-06-01 00:00:00
abstract：:Since the first comprehensive computerized videometric systems for quantitative assessment of the dynamic morphology and function of the heart have been developed, angiocardiographic image generation and computer aided evaluation have improved considerably. As a second method for morphological imaging echocardiography...
journal_title：Herz
pub_type： 杂志文章
doi：
更新日期：1985-08-01 00:00:00
abstract：BACKGROUND:There is an increasing prevalence of older adults (> 65 years) with hypertension and the need for antihypertensive medication. It is well established that elderly hypertensive patients benefit from drug treatment with regards to cardiovascular morbidity and mortality. Due to the comorbidity and reduced quali...
journal_title：Herz
pub_type： 临床试验,杂志文章
doi：10.1007/pl00002050
更新日期：2001-11-01 00:00:00
abstract：:The tricuspid valve and the right ventricle are hemodynamically closely related. Pathological changes of the valve or of the ventricle itself and also various diseases beyond that can result in a downward spiral of mutual interference, which is of prognostic importance for the patient. The development of a functional ...
journal_title：Herz
pub_type： 杂志文章,评审
doi：10.1007/s00059-017-4614-x
更新日期：2017-11-01 00:00:00
abstract：IMPORTANCE:Anxiety and depression are frequent problems in patients with heart diseases. Prevalences vary between 15 and 50%, depending on diagnostic criteria as well as on sociodemographic and medical patient characteristics. During the last 10-15 years, a large number of studies have shown that anxiety and depression...
journal_title：Herz
pub_type： 杂志文章,评审
doi：10.1007/s00059-001-2300-4
更新日期：2001-08-01 00:00:00
abstract：:Heart failure is one of the leading diseases in internal medicine worldwide. Because of the increase in population aging, the incidence and prevalence of heart insufficiency is rising annually and is now the most frequent individual diagnosis among hospitalized patients in Germany. The mortality rate has recently been...
journal_title：Herz
pub_type： 杂志文章,评审
doi：10.1007/s00059-018-4715-1
更新日期：2020-04-01 00:00:00
abstract：:In April 1996 the Munich Rehabilitation Center was founded by the Social Security Agency as a "satellite center" of the "Klinik Höhenried for Cardiovascular Diseases", which is located 50 km south of Munich near the lake Starnberg and performs in-patient rehabilitation since 1967. The Munich Rehabilitation Center is e...
journal_title：Herz
pub_type： 杂志文章
doi：
更新日期：1999-04-01 00:00:00
abstract：:Transcatheter aortic valve implantation (TAVI) using a balloon-expandable valve has been developed by the authors' group 7 years ago to offer a therapeutic solution to nonoperable or surgical high-risk patients with degenerative aortic stenosis. The technique and the devices used have rapidly evolved thereafter and TA...
journal_title：Herz
pub_type： 杂志文章,评审
doi：10.1007/s00059-009-3264-z
更新日期：2009-08-01 00:00:00
abstract：:Morphologic observations following balloon angioplasty are summarized from adult patients undergoing coronary or saphenous vein bypass graft angioplasty and from infants undergoing aortic valve stenosis angioplasty. Possible mechanisms of dilation injury and complications of angioplasty balloon bursting are reviewed. ...
journal_title：Herz
pub_type： 杂志文章
doi：
更新日期：1985-10-01 00:00:00
abstract：UNLABELLED:Due to the increasing number of elderly as well as chronically-ill patients, venous thrombosis assumes an increasing role as a typical complication of many courses of disease. Postoperatively, in patients without anticoagulation, fibrinogen tests show venous thrombosis in the lower extremities in up to 50% b...
journal_title：Herz
pub_type： 杂志文章,评审
doi：
更新日期：1989-12-01 00:00:00
abstract：BACKGROUND:Galectin-3 has been reported as a mediator of heart failure (HF) development and progression. Most studies, however, have been conducted on patients with chronic HF rather than acute HF (AHF). The aim of this study was to confirm galectin-3 as a prognostic marker in subjects with AHF and to investigate its p...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-017-4538-5
更新日期：2018-03-01 00:00:00
abstract：:In order to understand the mechanics of left ventricular (LV) diastolic filling it has become important to understand the role of the pericardium. This is because it has been demonstrated that the LV pressure-volume relationship can be shifted by previously unrecognized changes in pericardial "pressure" and, therefore...
journal_title：Herz
pub_type： 杂志文章,评审
doi：
更新日期：1990-12-01 00:00:00
abstract：OBJECTIVE:Cardiovascular magnetic resonance imaging (CMR) has been established as a modality to detect myocardial viability. The aim of this study was to evaluate myocardial viability by observing transmural extent of infraction and microvascular perfusion level. METHODS:We performed CMR in 30 myocardial infarction (M...
journal_title：Herz
pub_type： 杂志文章
doi：10.1007/s00059-018-4741-z
更新日期：2019-12-01 00:00:00
abstract：:In the clinical management of patients with valvular heart disease, transthoracic echocardiography (TTE) combined with Doppler has become the central diagnostic tool during the past decades. The development of transesophageal echocardiography (TEE) has led to an improved image quality especially of structures distant ...
journal_title：Herz
pub_type： 杂志文章,评审
doi：
更新日期：1993-12-01 00:00:00
abstract：BACKGROUND AND AIM OF THE STUDY:The predisposition to atrial fibrillation (AF) in mitral stenosis (MS) has been demonstrated with several electrocardiographic (increased P-wave dispersion) and echocardiographic parameters (atrial electromechanical delay). Despite the improvement in P-wave dispersion after percutaneous ...
journal_title：Herz
pub_type： 临床试验,杂志文章
doi：10.1007/s00059-012-3672-3
更新日期：2013-03-01 00:00:00
