Cardiac involvement in total generalized lipodystrophy (Berardinelli- Seip syndrome).

Abstract:

:Total generalized lipodystrophy (Berardinelli - Seip Syndrome) is a rare hereditary disease characterized by insulin-resistant diabetes mellitus and a small quantity of adipose tissue and is of unknown origin. Common cardiovascular alterations related to this syndrome are cardiac hypertrophy and arterial hypertension. This article reports a case of Berardinelli - Seip syndrome and reviews the literature with special emphasis on the cardiovascular manifestations of this syndrome.

journal_name

Arq Bras Cardiol

authors

Viégas RF,Diniz RV,Viégas TM,Lira EB,Almeida DR

doi

10.1590/s0066-782x2000000900006

subject

Has Abstract

pub_date

2000-09-01 00:00:00

pages

243-8

issue

3

eissn

0066-782X

issn

1678-4170

pii

S0066-782X2000000900006

journal_volume

75

pub_type

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