Cardiovascular Manifestations of Erdheim-Chester's Disease: A Case Series.

Abstract:

:Erdheim-Chester Disease is a rare entity, classified as an inflammatory myeloid neoplasm, with an unknown incidence, occurring preferentially in men after 50 years of age. Classically, it has a multisystemic presentation, with the skeletal system being the most frequently affected (90% of the patients), followed by genitourinary involvement in 60% of cases and central nervous system in the pituitary and diabetes insipidus in 25% of the cases. Cardiovascular manifestations are present in more than half of the patients, with aortic infiltration and atrial pseudotumor being the most common forms.

journal_name

Arq Bras Cardiol

authors

Costa IBSDS,Abdo ANR,Bittar CS,Fonseca SMR,Moraes ASHT,Kalil Filho R,Pereira J,Hajjar LA

doi

10.5935/abc.20180218

subject

Has Abstract

pub_date

2018-12-01 00:00:00

pages

852-855

issue

6

eissn

0066-782X

issn

1678-4170

pii

S0066-782X2018001800852

journal_volume

111

pub_type

杂志文章
  • The influence of health insurance plans on the long term outcome of patients with acute myocardial infarction.

    abstract:BACKGROUND:Little is known, especially in our country, about the influence of health insurance plans on the long term outcome of patients after acute myocardial infarction (AMI). OBJECTIVE:To assess the outcome of patients with AMI who are covered by the National Health System (SUS) or other health insurance plans. M...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2008001800004

    authors: Nicolau JC,Baracioli LM,Serrano CV Jr,Giraldez RR,Kalil Filho R,Lima FG,Franken M,Ganem F,Lage RL,Truffa R

    更新日期:2008-12-01 00:00:00

  • [Submammary incision for median sternotomy].

    abstract:PURPOSE:To evaluate the indications, complications, cosmetic and functional results with submammary skin incision for a median sternotomy in females. METHODS:Two hundred and eighty female patients have undergone submammary skin incision for a median sternotomy between 1981 to 1991 ages ranged from 2 months to 42 years...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Baucia JA,Sobrinho AF,Barbero-Marcial M

    更新日期:1993-05-01 00:00:00

  • Tissue doppler echocardiography in the diagnosis of heart transplantation rejection.

    abstract:BACKGROUND:Endomyocardial biopsy (EMB) is the gold standard method for the diagnosis of cellular rejection (CR) after heart transplantation (HT). OBJECTIVE:To test the hypothesis that tissue Doppler imaging (TDI) could detect CR > 3A and add diagnostic information compared to conventional Doppler. METHODS:Fifty-four ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2011005000060

    authors: Resende MV,Vieira ML,Bacal F,Andrade JL,Stolf NA,Bocchi EA

    更新日期:2011-07-01 00:00:00

  • [Inadequate blood pressure control in patients with type 2 diabetes mellitus].

    abstract:BACKGROUND:There is evidence indicating that blood pressure control is more effective in reducing macrovascular complications of diabetes mellitus (DM) than glycemic control. However, the reduction in BP to levels recommended by international guidelines is difficult in clinical practice. OBJECTIVE:To assess the percen...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2010005000034

    authors: Pinto LC,Ricardo ED,Leitão CB,Kramer CK,Zanatta CM,Gross JL,Canani LH

    更新日期:2010-05-01 00:00:00

  • [Diagnosis using nuclear medicine of anterior descending artery stenosis in patients with left bundle branch block].

    abstract:PURPOSE:To evaluate septal perfusion and contractility in patients with left bundle branch block (LBBB). METHODS:Twenty patients were submitted to myocardial scintigraphy with Tecnecium-99m isontrile after exercise and dipyridamole infusion. The septal contractility was observed during the radionuclide ventriculograph...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 临床试验,杂志文章

    doi:

    authors: Smanio PE,Martins LR,Tazima S,Meneghelo R,Thom A,Sousa JE

    更新日期:1995-11-01 00:00:00

  • Long-term follow-up of patients with indication for a implantable defibrillator for primary prevention of death.

    abstract:BACKGROUND:Recent MADIT II and SCD-HeFT trials have led to an expansion of indications for use of prophylactic Implantable Cardioverter Defibrillator (ICD) in patients with severe left-ventricular impairment. This therapy has not been fully adopted in our health care system, mainly due to its high cost. OBJECTIVE:To a...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2008000500006

    authors: Hadid C,Avellana P,Di Toro D,Gomez CF,Visser M,Prieto N

    更新日期:2008-05-01 00:00:00

  • Acute Coronary Syndrome Treatment Costs from the Perspective of the Supplementary Health System.

    abstract:BACKGROUND:Acute coronary syndrome (ACS) is defined as a "group of clinical symptoms compatible with acute myocardial ischemia", representing the leading cause of death worldwide, with a high clinical and financial impact. In this sense, the development of economic studies assessing the costs related to the treatment o...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20150129

    authors: Teich V,Piha T,Fahham L,Squiassi HB,Paloni Ede M,Miranda P,Araújo DV

    更新日期:2015-10-01 00:00:00

  • Right sinus of Valsalva aneurysm causing extrinsic coronary compression.

    abstract::Sinus of Valsalva aneurysm is a rare cardiac disorder. It is more frequently a congenital, but it may also be an acquired condition. Takayasu's disease is an extremely rare cause of this disorder. Most cases of unruptured sinus of Valsalva aneurysm are asymptomatic. Compression of the left coronary artery is an unusua...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2009000600017

    authors: Dias RR,Camurça FD,Leite Filho OA,Stolf NA

    更新日期:2009-06-01 00:00:00

  • Variability among cardiologists in the management of patients under secondary prevention of ischemic heart disease.

    abstract:OBJECTIVE:To compare the management of patients with ischemic heart disease being followed up in a general cardiology outpatient clinic with that of patients being followed up in an outpatient clinic specific for ischemic heart disease, emphasizing the lipid profile and the pharmacological treatment prescribed. METHOD...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2004001500005

    authors: Stein R,Alboim C,Campos C,Mello RB,Rosito GA,Polanczyk CA

    更新日期:2004-09-01 00:00:00

  • Aneurysm of the right atrial appendage.

    abstract::Atrial aneurysms involving the free wall or atrial appendage are rare entities in cardiology practice and may be associated with atrial arrhythmias or embolic phenomena. We review the literature and report a case of aneurysm of the right atrial appendage in a young adult, whose diagnosis was established with echocardi...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2002000200013

    authors: Barberato SH,Barberato MF,Avila BM,Perretto S,Blume Ld Ldo R,Chamma Neto M

    更新日期:2002-02-01 00:00:00

  • Influence of cardiopulmonary bypass on the plasma concentrations of atenolol.

    abstract:BACKGROUND:Betablockers are used in the treatment of angina pectoris and others ischemic coronary diseases, reducing mortality and cardiovascular events. Atenolol is a hydrophilic betablocker which is characterized by gastrointestinal absorption, small extent of distribution and renal function-dependent elimination. O...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2007000600003

    authors: Leite Fda S,dos Santos LM,Bonafé WW,Chignalia AZ,Carmona MJ,Suyama MJ,Malbouisson LM,Auler JO Jr,Santos SR

    更新日期:2007-06-01 00:00:00

  • [Detection of myocardial ischemia during dobutamine stress echocardiography. Correlation with coronary cineangiography].

    abstract:PURPOSE:To detect myocardial ischemia during dobutamine stress echocardiography (DSE). METHODS:Two hundred and seventy one patients were studied; 63 (23%) underwent coronary angiography within a month of DSE. Angiograms were analyzed independently by 3 angiographers, and coronary lesions larger than 50% of luminal occ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Mathias Júnior W,Doya EH,Ribeiro EE,Silva LA,Gasques A,Salvadori RA,Duprat Filho R

    更新日期:1993-04-01 00:00:00

  • Congenital Heart Disease as a Warning Sign for the Diagnosis of the 22q11.2 Deletion.

    abstract::Background: To alert for the diagnosis of the 22q11.2 deletion syndrome (22q11.2DS) in patients with congenital heart disease (CHD). Objective: To describe the main CHDs, as well as phenotypic, metabolic and immunological findings in a series of 60 patients diagnosed with 22q11.2DS. Methods: The study included 60 pati...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20140145

    authors: Grassi MS,Jacob CM,Kulikowski LD,Pastorino AC,Dutra RL,Miura N,Jatene MB,Pegler SP,Kim CA,Carneiro-Sampaio M

    更新日期:2014-11-01 00:00:00

  • Cardiovascular risks in adolescents with different degrees of obesity.

    abstract:BACKGROUND:There have been few studies on cardiovascular risk factors in adolescents with different degrees of obesity. OBJECTIVE:To evaluate metabolic effects associated with different degrees of obesity in adolescents and their impact on cardiovascular risks. METHODS:Cross-sectional study of 80 obese adolescents, d...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2010005000166

    authors: Lavrador MS,Abbes PT,Escrivão MA,Taddei JA

    更新日期:2011-03-01 00:00:00

  • Is systemic lupus erithematosus a new risk factor for atherosclerosis?

    abstract:OBJECTIVE:To evaluate the prevalence of cardiovascular events (CVE) secondary to atherosclerosis in lupus patients and correlate them to the traditional risk factors, disease duration and drug therapy used. METHODS:A retrospective study was carried out based on data obtained from patients charts. Patients included wer...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2006001600012

    authors: Freire BF,da Silva RC,Fabro AT,dos Santos DC

    更新日期:2006-09-01 00:00:00

  • [Percutaneous transluminal coronary angioplasty after orthotopic heart transplantation].

    abstract::We report the case of 22 year-old male who developed coronary artery disease two years after orthotopic cardiac transplantation, manifested as congestive heart failure NYHA functional class III. The left ventricular radioisotopic evaluation at rest revealed worsening of left ventricular ejection fraction from 50% to 3...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Bocchi EA,Vilas-Boas F,Pedrosa AA,Bacal F,Fiorelli A,Ariê S,Stolf N,Bellotti G,Jatene A,Pileggi F

    更新日期:1994-03-01 00:00:00

  • [Rupture of the left sinus of Valsalva forming a subepicardial pseudoaneurysm].

    abstract::A healthy 44 year-old male patient presented a calcified mass in the middle mediastinum on a chest film. During diagnostic investigation cineangiograms showed a rupture of the left sinus of Valsalva forming a large pseudoaneurysm that produced important distortion of the left coronary artery and it's main branches. Th...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Barbosa V,Kopel L,Oliveira SA,Barretto AC,Mady C,Bellotti G,Pileggi F

    更新日期:1990-10-01 00:00:00

  • Rare Complication of non-Treated Abdominal Aortic Aneurysm: Extensive Thrombus in Right Cardiac Chambers.

    abstract::A 78-year-old patient presented with shortness of breath after falling down. Transthoracic echocardiogram showed an extensive thrombus in the right atrium (RA), extensive thrombosis of the inferior vena cava (IVC), and abdominal aortic aneurysm (AAA). A magnetic resonance confirmed the thrombosis of the RA extending t...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20160143

    authors: Hotta VT,Bluemke DA,Staszko KF,Pereira AN,Rochitte CE

    更新日期:2016-10-01 00:00:00

  • Cardiac magnetic resonance and its anatomical planes: how do I do it?

    abstract::Due to the increasing use of the cardiac magnetic resonance (CMR) method and the frequent implementation of such method in new services, we describe herein, in a step-by-step format, the acquisition techniques that are necessary for a complete cardiac approach, of the main anatomical planes of the heart used by CMR. ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,评审

    doi:10.1590/s0066-782x2010001600014

    authors: Nacif MS,Oliveira Junior AC,Carvalho AC,Rochitte CE

    更新日期:2010-12-01 00:00:00

  • Cross-sectional study of treatment strategies on atrial fibrillation.

    abstract:BACKGROUND:Despite the high prevalence and clinical importance of atrial fibrillation (AF), there is no Brazilian study describing the clinical profile of patients with AF and the most used treatment strategy (rhythm control vs. rate control). OBJECTIVE:Assess the most common treatment on AF in an outpatient specializ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2012005000020

    authors: Oliveira LH,Mallmann FB,Botelho FN,Paul LC,Gianotto M,Abt Rde B,Silva NJ,Luize CM,Nogueira FL,Carvalho RS,Paola AA,Cirenza C

    更新日期:2012-03-01 00:00:00

  • Coronary artery bypass using only computed tomography as pre-operative angiogram.

    abstract::Coronary artery bypass graft (CABG) is a well established procedure with current precise indications. The advent and spread of this technique was possible after the introduction of the coronary angiogram. Although many evaluation methods have been developed in the past years, to date, none have been able to replace th...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2009000900019

    authors: Gaia DF,Palma JH,Branco JN,Teles CA,Catani R,Buffolo E

    更新日期:2009-09-01 00:00:00

  • Evaluation of the medical care of patients with hypertension in an emergency department and in ambulatory hypertension unit.

    abstract:OBJECTIVE:To evaluate the characteristics of the patients receiving medical care in the Ambulatory of Hypertension of the Emergency Department, Division of Cardiology, and in the Emergency Unit of the Clinical Hospital of the Ribeirão Preto Medical School. METHODS:Using a protocol, we compared the care of the same hyp...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,多中心研究

    doi:10.1590/s0066-782x2002000200003

    authors: Nobre F,Chauchar F,Viana JM,Pereira GJ,Lima NK

    更新日期:2002-02-01 00:00:00

  • Acute myocardial infarction: clinical and epidemiological profile and factors associated with in-hospital death in the municipality of Rio de Janeiro.

    abstract:OBJECTIVE:To study the factors associated with the risk of in-hospital death in acute myocardial infarction in the Brazilian public health system in Rio de Janeiro, Brazil. METHODS:Sectional study of a sample with 391 randomly drawn medical records of the hospitalizations due to acute myocardial infarction recorded in...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2003000600003

    authors: Escosteguy CC,Portela MC,Medronho Rde A,de Vasconcellos MT

    更新日期:2003-06-01 00:00:00

  • Transthoracic impedance compared to magnetic resonance imaging in the assessment of cardiac output.

    abstract:BACKGROUND:Cardiac magnetic resonance imaging is considered the gold-standard method for the calculation of cardiac volumes. Transthoracic impedance cardiography assesses the cardiac output. No studies validating this measurement, in comparison to that obtained by magnetic resonance imaging, are available. OBJECTIVE:T...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2012005000104

    authors: Villacorta Junior H,Villacorta AS,Amador F,Hadlich M,Albuquerque DC,Azevedo CF

    更新日期:2012-12-01 00:00:00

  • [Correlation between evolution of the cognitive function and mortality after hospital discharge in elderly patients with advanced heart failure].

    abstract:OBJECTIVE:To assess the relation between the evolution of cognitive performance and the prognosis of elderly patients after compensation of advanced heart failure. METHODS:Thirty-one patients older than 64 (68 +/- 7) years and admitted with New York Heart Association class IV heart failure and ejection fraction = 0.45...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2004000300005

    authors: Ochiai ME,Franco LL,Gebara OC,Nussbacher A,Serro-Azul JB,Pierri H,Rays J,Barretto AC,Wajngarten M

    更新日期:2004-03-01 00:00:00

  • Successful reversal of pulmonary hypertension in Eisenmenger complex.

    abstract::We present a case of a 19-year old female with systemic pulmonary artery (PA) pressure due to a congenital ventricular septal defect (VSD) and atrial septal defect (ASD). She was pink at rest and cyanotic on exercise. Lung biopsy revealed grade IV pulmonary vascular changes. As a preliminary step PA was banded to incr...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Batista RJ,Santos JL,Takeshita N,Eocchino L,Lima PN,Goehr M,Cunha MA,Kawaguchi AT,Salerno TA

    更新日期:1997-04-01 00:00:00

  • [Use of implantable pacemaker in the treatment of paroxysmal supraventricular tachycardia refractory to pharmacologic therapy].

    abstract:PURPOSE:To evaluate the results with the use of an automatic antitachycardia pacemaker in patients with refractory paroxysmal supraventricular tachycardia. PATIENTS AND METHODS:Nine patients aged 32 to 63 years with symptoms from 2 to more than 40 years and prophylactic treatment with several antiarrhythmic drugs that...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:

    authors: Sant'Anna JR,Medeiros C,Halperin C,Lucchese F,Kalil R,Prates P,Nonohay N,Nesralla I

    更新日期:1991-04-01 00:00:00

  • Treatment of a cohort of patients with acute myocardial infarction and ST-segment elevation.

    abstract:BACKGROUND:Although thrombolysis and primary CTA are well-established procedures, they are not administered in a large proportion of the patients with STEMI who arrive to the emergency rooms. OBJECTIVE:Describe initial and final the results in a cohort of STEMI patients METHODS:The study included, from hospital admis...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2009000600009

    authors: Soares Jda S,Souza NR,Nogueira Filho J,Cunha CC,Ribeiro GS,Peixoto RS,Soares CE,Soares LC,Reis AF,Faria CA

    更新日期:2009-06-01 00:00:00

  • Anthropometric indicators as predictors of high blood pressure in adolescents.

    abstract:BACKGROUND:Hypertension is related to increased body fat, which can be evaluated by anthropometric indicators. OBJECTIVE:To determine the predictive power of anthropometric indicators and establish their cutoff points as discriminators of high blood pressure. METHODS:Cross-sectional study with a sample of 660 adolesc...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.1590/s0066-782x2010005000153

    authors: Beck CC,Lopes Ada S,Pitanga FJ

    更新日期:2011-02-01 00:00:00

  • Women with Polycystic Ovarian Syndrome Exhibit Reduced Baroreflex Sensitivity That May Be Associated with Increased Body Fat.

    abstract:BACKGROUND:Polycystic ovarian syndrome (PCOS) women have a high prevalence of obesity and alterations in cardiovascular autonomic control, mainly modifications in heart rate variability (HRV) autonomic modulation. However, there are few studies about other autonomic control parameters, such as blood pressure variabilit...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章

    doi:10.5935/abc.20190031

    authors: Philbois SV,Gastaldi AC,Facioli TP,Felix ACS,Reis RMD,Fares TH,Souza HCD

    更新日期:2019-04-01 00:00:00