Cardiovascular Manifestations of Erdheim-Chester's Disease: A Case Series.


:Erdheim-Chester Disease is a rare entity, classified as an inflammatory myeloid neoplasm, with an unknown incidence, occurring preferentially in men after 50 years of age. Classically, it has a multisystemic presentation, with the skeletal system being the most frequently affected (90% of the patients), followed by genitourinary involvement in 60% of cases and central nervous system in the pituitary and diabetes insipidus in 25% of the cases. Cardiovascular manifestations are present in more than half of the patients, with aortic infiltration and atrial pseudotumor being the most common forms.


Arq Bras Cardiol


Costa IBSDS,Abdo ANR,Bittar CS,Fonseca SMR,Moraes ASHT,Kalil Filho R,Pereira J,Hajjar LA




Has Abstract


2018-12-01 00:00:00














  • Acute myocardial infarction: clinical and epidemiological profile and factors associated with in-hospital death in the municipality of Rio de Janeiro.

    abstract:OBJECTIVE:To study the factors associated with the risk of in-hospital death in acute myocardial infarction in the Brazilian public health system in Rio de Janeiro, Brazil. METHODS:Sectional study of a sample with 391 randomly drawn medical records of the hospitalizations due to acute myocardial infarction recorded in...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Escosteguy CC,Portela MC,Medronho Rde A,de Vasconcellos MT

    更新日期:2003-06-01 00:00:00

  • Blood pressure measurement during aerobic exercise: subsidies for cardiac rehabilitation.

    abstract:BACKGROUND:Institutional documents recommend that hemodynamic variables--heart rate (HR) and systolic (SAP) and diastolic arterial pressure (DAP)--be routinely controlled at the aerobic part of supervised exercise sessions for coronary disease patients. OBJECTIVE:a) to determine the pattern and reproducibility of the ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Furtado EC,Ramos Pdos S,Araújo CG

    更新日期:2009-07-01 00:00:00

  • [Different therapies in the treatment of obesity in hypertensive patients].

    abstract:PURPOSE:To evaluate the efficacy and tolerability of different therapies associated with diet in the treatment of hypertensive obese patients. METHODS:In a clinical study we randomly evaluated 39 hypertensive obese patients (body mass index (BMI) > or = 30 kg/m2). After 45 days of diet the patients were again randomly...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 临床试验,杂志文章,随机对照试验


    authors: Monego ET,Peixoto Mdo R,Jardim PC,Sousa AL,Braga VL,Moura MF

    更新日期:1996-06-01 00:00:00

  • Role of echocardiography in the ventricular assessment of the transplanted heart versus heart rejection.

    abstract:BACKGROUND:Heart transplantation is an alternative for individuals with end-stage heart disease. However, episodes of heart rejection (HR) are frequent and increase morbidity and mortality, requiring the use of an accurate non-invasive exam for their diagnosis, since endomyocardial biopsy (EMB) is not a complication-fr...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Miguel GA,Rojas SS,Vieira RW,Silva JP,Abensur H

    更新日期:2012-11-01 00:00:00

  • Atorvastatin Reduces Accumulation of Vascular Smooth Muscle Cells to Inhibit Intimal Hyperplasia via p38 MAPK Pathway Inhibition in a Rat Model of Vein Graft.

    abstract:BACKGROUND:The rate of saphenous vein graft failure one year after coronary artery bypass grafting ranges from 10% to 25%. The aim of this study was to explore whether atorvastatin can reduce accumulation of vascular smooth muscle cells to inhibit intimal hyperplasia via p38 MAPK pathway inhibition. METHODS:Forty-five...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Chu T,Huang M,Zhao Z,Ling F,Cao J,Ge J

    更新日期:2020-10-01 00:00:00

  • Abdominal circumference as a predictor of 30-day outcome in acute coronary syndrome.

    abstract:BACKGROUND:Abdominal circumference (WC) is the measure that correlates most closely with the risk factors and death from cardiovascular disease. However, the impact of obesity on the prognosis of patients with cardiovascular disease remains controversial and requires further clarification. OBJECTIVE:To evaluate WA as ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Lopes de Souza PA,Trussardi Fayh AP,Lúcia Portal V

    更新日期:2011-05-01 00:00:00

  • Temporal variation in the prognosis and treatment of advanced heart failure - before and after 2000.

    abstract:BACKGROUND:The treatment of heart failure has evolved in recent decades suggesting that survival is increasing. OBJECTIVE:To verify whether there has been improvement in the survival of patients with advanced heart failure. METHODS:We retrospectively compared the treatment and follow-up data from two cohorts of patie...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Carlo CH,Cardoso JN,Ochia ME,Oliveira MT Jr,Ramires JA,Pereira-Barretto AC

    更新日期:2014-05-01 00:00:00

  • Effects of lisinopril on experimental ischemia in rats. Influence of infarct size.

    abstract::OBJECTIVE - Angiotensin-converting enzyme inhibitors (ACEIs) have gained importance in preventing or attenuating the process of ventricular remodeling after myocardial infarction. The significance of infarct size in regard to the response to ACEIs, however, is controversial. This study aimed to analyze the effects of ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Zornoff LA,Matsubara BB,Matsubara LS,Paiva SA,Tornero MT,Spadaro J

    更新日期:1999-10-01 00:00:00

  • Revision of the Sokolow-Lyon-Rappaport and cornell voltage criteria for left ventricular hypertrophy.

    abstract:BACKGROUND:Electrocardiographically-detected left ventricular hypertrophy (LVH) is a strong predictor of cardiovascular morbidity and mortality. OBJECTIVE:To assess the performance of the Sokolow-Lyon-Rappaport (SLR) and Cornell voltage criteria in a population sample regarding the diagnosis of LVH on echocardiogram (...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Rodrigues SL,D'Angelo L,Pereira AC,Krieger JE,Mill JG

    更新日期:2008-01-01 00:00:00

  • Mild stunting is associated with higher blood pressure in overweight adolescents.

    abstract:BACKGROUND:Studies have shown that pre/postnatal undernutrition leads to higher risk of non communicable diseases such as diabetes, hypertension and obesity in adulthood. OBJECTIVE:To determine whether overweight adolescents with mild stunting [height-for-age Z scores (HAZ) in the range <-1 to ≥ -2] have higher blood ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Clemente AP,Santos CD,Silva AA,Martins VJ,Marchesano AC,Fernandes MB,Albuquerque MP,Sawaya AL

    更新日期:2012-01-01 00:00:00

  • Hyperkalemia during spironolactone use in patients with decompensated heart failure.

    abstract:BACKGROUND:The incidence of hyperkalemia related to spironolactone use is low in stable heart failure; however, it has not been studied during decompensation. OBJECTIVE:To evaluate the influence of spironolactone on serum potassium in decompensated heart failure (HF). METHODS:In a cohort study, patients that had been...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Lima MV,Ochiai ME,Cardoso JN,Morgado PC,Munhoz RT,Barretto AC

    更新日期:2008-09-01 00:00:00

  • [Echocardiographic monitoring of balloon atrial septostomy].

    abstract:OBJECTIVE:To assess balloon atrial septostomy monitored with echocardiography. METHODS:From August 1997 to January 2004, 31 infants with congenital heart diseases indicated for balloon atrial septostomy underwent the procedure with exclusive echocardiographic monitoring. Success was defined as the obtainment of an atr...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Marchi CH,Godoy MF,Santos MA,Moscardini AC,Hassen Sobrinho S,Croti UA

    更新日期:2005-03-01 00:00:00

  • Influence of cardiopulmonary bypass on the plasma concentrations of atenolol.

    abstract:BACKGROUND:Betablockers are used in the treatment of angina pectoris and others ischemic coronary diseases, reducing mortality and cardiovascular events. Atenolol is a hydrophilic betablocker which is characterized by gastrointestinal absorption, small extent of distribution and renal function-dependent elimination. O...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Leite Fda S,dos Santos LM,Bonafé WW,Chignalia AZ,Carmona MJ,Suyama MJ,Malbouisson LM,Auler JO Jr,Santos SR

    更新日期:2007-06-01 00:00:00

  • Women with Polycystic Ovarian Syndrome Exhibit Reduced Baroreflex Sensitivity That May Be Associated with Increased Body Fat.

    abstract:BACKGROUND:Polycystic ovarian syndrome (PCOS) women have a high prevalence of obesity and alterations in cardiovascular autonomic control, mainly modifications in heart rate variability (HRV) autonomic modulation. However, there are few studies about other autonomic control parameters, such as blood pressure variabilit...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Philbois SV,Gastaldi AC,Facioli TP,Felix ACS,Reis RMD,Fares TH,Souza HCD

    更新日期:2019-04-01 00:00:00

  • Prognostic Value of NT-proBNP versus Killip Classification in Patients with Acute Coronary Syndromes.

    abstract:BACKGROUND:Plasma levels of brain natriuretic peptides have better diagnostic accuracy compared to clinical-radiologic judgment for acute heart failure. In acute coronary syndromes (ACS), the prognostic value of acute heart failure is incorporated into predictive models through Killip classification. It is not establis...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Souza TMB,Cerqueira AMS Jr,Suerdieck JG,Sá NC,Sodré GS,Correia VCA,Lacerda YF,Fonseca LL,Noya-Rabelo MM,Correia LCL

    更新日期:2020-04-01 00:00:00

  • Influence of angiotensin II receptor subtypes of the paraventricular nucleus on the physiological responses induced by angiotensin II injection into the medial septal area.

    abstract:OBJECTIVE:We determined the effects of losartan and PD 123319 (antagonists of the AT1 and AT2 angiotensin receptors, respectively), and [Sar1, Ala8] ANG II (a relatively peptide antagonist of angiotensin receptors) injected into the paraventricular nucleus (PVN) on water and 3% NaCl intake, and the diuretic, natriureti...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Saad WA,Camargo LA

    更新日期:2003-04-01 00:00:00

  • Coronary artery disease in patients with rheumatic and non-rheumatic valvular heart disease treated at a public hospital in Rio de Janeiro.

    abstract:OBJECTIVE:to estimate the prevalence of coronary artery disease (CAD) in valvular heart disease of rheumatic (RVHD) and non-rheumatic (NVHD) etiology, assessing possible predictive factors for the presence of CAD. METHODS:This is a cross-sectional study of a series of cases obtained from a pre-defined population, wher...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Kruczan DD,Silva NA,Pereira Bde B,Romão VA,Correa Filho WB,Morales FE

    更新日期:2008-03-01 00:00:00

  • Methodological Gaps in Left Atrial Function Assessment by 2D Speckle Tracking Echocardiography.

    abstract::The assessment of left atrial (LA) function is used in various cardiovascular diseases. LA plays a complementary role in cardiac performance by modulating left ventricular (LV) function. Transthoracic two-dimensional (2D) phasic volumes and Doppler echocardiography can measure LA function non‑invasively. However, eval...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,评审


    authors: Rimbaş RC,Dulgheru RE,Vinereanu D

    更新日期:2015-12-01 00:00:00

  • Subclinical ventricular dysfunction detected by speckle tracking two years after use of anthracycline.

    abstract:BACKGROUND:Heart failure is a severe complication associated with doxorubicin (DOX) use. Strain, assessed by two-dimensional speckle tracking (2D-STE), has been shown to be useful in identifying subclinical ventricular dysfunction. OBJECTIVES:a) To investigate the role of strain in the identification of subclinical ve...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: de Almeida AL,Silva VA,de Souza Filho AT,Rios VG,Lopes JR,de Afonseca SO,Cunha Dde C,Mendes MO,Miranda DL,dos Santos Júnior EG

    更新日期:2015-04-01 00:00:00

  • Evaluation of cardiopulmonary fitness in individuals with hemiparesis after cerebrovascular accident.

    abstract:BACKGROUND:Due to the hemiparesis, the assessment of cardiorespiratory fitness on individuals after cerebrovascular accident (CVA), using exercise tests with conventional protocols, has become a challenge. OBJECTIVE:Perform cardiopulmonary test (CPT) in hemiparetic patients to a pre-participation evaluation aimed at a...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Ovando AC,Michaelsen SM,Carvalho Td,Herber V

    更新日期:2011-02-01 00:00:00

  • Determinants of Aortic Prosthesis Mismatch in a Brazilian Public Health System Hospital: Big Patients or Small Prosthesis?

    abstract:BACKGROUND:Prosthesis-patient mismatch (PPM) is associated with worse outcomes. OBJECTIVE:Determine the frequency and evaluate preoperatory variables independently associated with severe PPM in a tertiary hospital focused on Public Health Care. METHODS:A total of 316 patients submitted to aortic valve replacement, wh...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Otto ME,Atik FA,Moreira MDN,Ribeiro LCM,Mello BCR,Lima JGE,Ribeiro MS,Domingues ACPM,Calzada RP,Jreige A Jr,Schloicka LL,Pibarot P

    更新日期:2020-01-01 00:00:00

  • Emerging role of the GH/IGF-I on cardiometabolic control.

    abstract::Growth hormone (GH), the main regulator for post-natal growth, has important metabolic actions on different tissues, similar or opposite to insulin like growth factor I (IGF-I), mainly produced by the liver after the binding of GH to its receptor. Experiments with animal models indicate an important role of GH on insu...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章,评审


    authors: Oliveira CR,Meneguz-Moreno RA,Aguiar-Oliveira MH,Barreto-Filho JA

    更新日期:2011-11-01 00:00:00

  • Predictive value of myeloperoxidase to identify high risk patients admitted to the hospital with acute chest pain.

    abstract:BACKGROUND:Myeloperoxidase (MPO) is a highly expressed enzyme due to leukocyte activation, with multiple atherogenic actions, including LDL cholesterol oxidation, and is related to the instability of atherosclerotic plaque. It is a predictor of adverse events in healthy individuals, patients with heart disease or those...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Esporcatte R,Rey HC,Rangel FO,Rocha RM,Mendonça Filho HT,Dohmann HF,Albanesi Filho FM

    更新日期:2007-12-01 00:00:00

  • Gene expression related to oxidative stress in the heart of mice after intestinal ischemia.

    abstract:BACKGROUND:Intestinal ischemia-reperfusion is a frequent clinical event associated to injury in distant organs, especially the heart. OBJECTIVE:To investigate the gene expression of oxidative stress and antioxidant defense in the heart of inbred mice subjected to intestinal ischemia and reperfusion (IR). METHODS:Twel...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Somaio Neto F,Ikejiri AT,Bertoletto PR,Chaves JC,Teruya R,Fagundes DJ,Taha MO

    更新日期:2014-02-01 00:00:00

  • [Study of the prevalence and multiplicity of cardiovascular risk factors in hypertensive individuals from the city of Brusque, SC, Brazil].

    abstract:OBJECTIVE:To investigate the prevalence and multiplicity of additional risk factors (RF) in a population sample of hypertensive smokers, diagnosed and enrolled at the Hiperdia Program of the Ministry of Health, in the city of Brusque, SC, Brazil. METHODS:Determination of the anthropometrical parameters and laboratory ...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Rosini N,Machado MJ,Xavier HT

    更新日期:2006-03-01 00:00:00

  • Lower Prevalence and Severity of Coronary Atherosclerosis in Chronic Chagas' Disease by Coronary Computed Tomography Angiography.

    abstract:BACKGROUND:In Chagas' disease endemic regions, there has been for many years a recurrent empirical observation that coronary artery disease (CAD) is uncommon in patients with Chagas' disease. Previous pathological and invasive coronary angiography studies led to controversial results. OBJECTIVE:We sought to investigat...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Cardoso S,Azevedo Filho CF,Fernandes F,Ianni B,Torreão JA,Marques MD,Ávila LFR,Santos Filho R,Mady C,Kalil-Filho R,Ramires JAF,Bittencourt MS,Rochitte CE

    更新日期:2020-12-01 00:00:00

  • Association between immunological diseases and their similar clinical manifestations.

    abstract::We report on a 30-year-old female patient, with biological mitral valve prosthesis due to symptomatic mitral stenosis and a history of acute myocardial infarction and generalized tonic-clonic seizure episodes, visual hallucinations, cerebral thromboembolic events and, at present, chorea and acute carditis. The patient...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Soeiro Ade M,Almeida MC,Accorsi TA,Spina GS,Serrano CV Jr,Tarasoutchi F

    更新日期:2012-02-01 00:00:00

  • [The usefulness of digital angiography in performing coronary angioplasty. An analysis of 100 cases].

    abstract:PURPOSE:To analyse the actual contribution of digital angiography in the angioplasty setting and to assess its utility to optimize angioplasty results. METHODS:One hundred patients with single vessel coronary artery disease, without previous angioplasty or coronary artery bypass graft surgery, who underwent angioplast...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Pinto IM,Sousa AG,Feres F,Tanajura LF,Mattos LA,Cano MN,Maldonado G,Fontes VF,Sousa JE

    更新日期:1992-10-01 00:00:00

  • Rare Complication of non-Treated Abdominal Aortic Aneurysm: Extensive Thrombus in Right Cardiac Chambers.

    abstract::A 78-year-old patient presented with shortness of breath after falling down. Transthoracic echocardiogram showed an extensive thrombus in the right atrium (RA), extensive thrombosis of the inferior vena cava (IVC), and abdominal aortic aneurysm (AAA). A magnetic resonance confirmed the thrombosis of the RA extending t...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Hotta VT,Bluemke DA,Staszko KF,Pereira AN,Rochitte CE

    更新日期:2016-10-01 00:00:00

  • Influence of the elevation of the left ventricular diastolic pressure on the values of the first temporal derivative of the ventricular pressure (dP/dt).

    abstract:PURPOSE:To assess the effects of the elevation of the left-ventricular end-diastolic pressure (LVEDP) on the value of the 1st temporal derivative of the ventricular pressure (dP/dt). METHODS:Nineteen anesthetized dogs were studied. The dogs were mechanically ventilated and underwent thoracotomy with parasympathetic ne...

    journal_title:Arquivos brasileiros de cardiologia

    pub_type: 杂志文章


    authors: Okoshi K,Fioretto JR,Bonatto RC,Tornero MT,Tucci PJ

    更新日期:1999-07-01 00:00:00