Abstract:
:The fatty acid pattern of serum lecithin was studied in 31 children with hereditary motor and sensory neuropathies (HMSN) of types specified in the classification of Dyck et al. (1975). In 30 children no relevant changes were revealed. The remaining patient had changes which were reversible and were considered to be independent of the polyneuropathy. It is concluded that primary defects of fatty acid metabolism do not characterize the well-defined types I, II and III of HMSN.
journal_name
Neuropediatricsjournal_title
Neuropediatricsauthors
Alling C,Svennerholm L,Hagberg B,Westerberg Bdoi
10.1055/s-2008-1059635subject
Has Abstractpub_date
1981-02-01 00:00:00pages
18-21issue
1eissn
0174-304Xissn
1439-1899journal_volume
12pub_type
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