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Surface electromyogram and muscle ultrasonography for detection of muscle fasciculations in pediatric peripheral neuropathy.

Abstract：

:A 12-year-old girl presented with talipes equinus of both legs, attenuation of upper and lower limb tendon reflexes, thermal hyperalgesia, and reduction of vibratory sensation. On clinical examination, muscle twitches of fingers of both hands, as well as the abductor halluces and the dorsal interossei muscles of the right foot were observed. Nerve conduction velocity was significantly declined in the upper and lower extremities. Needle electromyography (EMG) was not performed; however, ultrasonography revealed repetitive, semi-regular muscle twitches lasting 0.2-0.4s, concomitant with muscle discharges on surface EMG in the right foot muscles. These findings were compatible with contraction fasciculation in muscles under chronic reinnervation. Nerve and muscle biopsies were suggestive of chronic motor, sensory, and autonomic neuropathy. This is the first case of pediatric peripheral neuropathy where muscle fasciculation was noninvasively identified by simultaneous surface EMG and ultrasonography.

journal_name

Brain Dev

journal_title

Brain & development

authors

Oguri M,Saito Y,Okazaki T,Matsumura W,Ohno K,Togawa M,Fukuda C,Saito Y,Nishino I,Maegaki Y

doi

10.1016/j.braindev.2017.02.006

subject

Has Abstract

pub_date

2017-08-01 00:00:00

pages

617-620

issue

7

eissn

0387-7604

issn

1872-7131

pii

S0387-7604(17)30033-5

journal_volume

39

pub_type

杂志文章

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