Selective involvement of the quadriceps muscle in congenital muscular dystrophies: an ultrasonographic study.

Abstract:

:Muscle ultrasound scanning is a non-invasive and painless technique for evaluating muscle disorders in childhood. We have performed ultrasound scans of the quadriceps muscle in 26 children with various forms of congenital muscular dystrophies. There were 8 patients clearly showing selective involvement within the components of the quadriceps. In all cases showing selective involvement, the rectus femoris was spared and the vastus muscles were the affected group. Our findings support the concept of heterogeneity, often encountered in congenital muscular dystrophies.

journal_name

Brain Dev

journal_title

Brain & development

authors

Topaloğlu H,Gücüyener K,Yalaz K,Renda Y,Topçu M,Aysun S,Ozdirim E,Anlar B

doi

10.1016/s0387-7604(12)80091-x

keywords:

subject

Has Abstract

pub_date

1992-03-01 00:00:00

pages

84-7

issue

2

eissn

0387-7604

issn

1872-7131

pii

S0387-7604(12)80091-X

journal_volume

14

pub_type

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