Abstract:
:Erdheim-Chester disease (ECD) is a disseminated non-Langerhans' cell histiocytosis with multisystem involvement, including characteristic sclerotic musculoskeletal lesions. We present the case of a 27-year-old woman with a fulminant course and atypical involvement by ECD manifesting as extensive cerebrovascular disease and lytic musculoskeletal lesions. This case represents an unusual and aggressive presentation of ECD owing to the patient's young age, the severity of the cerebrovascular involvement and the lytic osseous lesions.
journal_name
Clin Rheumatoljournal_title
Clinical rheumatologyauthors
Lyders EM,Kaushik S,Perez-Berenguer J,Henry DAdoi
10.1007/s10067-003-0784-4subject
Has Abstractpub_date
2003-12-01 00:00:00pages
464-6issue
6eissn
0770-3198issn
1434-9949journal_volume
22pub_type
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