Single mandibular incisor in a patient with del (18p) anomaly.

Abstract:

:A single mandibular incisor and an unusually narrow mandible and tongue were noted in an 8-year-old moderately retarded boy with 18p- (45, XY, der dic (18) (18qter-p11.2::22p 11.2-qter). While a single maxillary incisor, considered a minor feature of holoprosencephaly, was reported in three cases of 18p-, reduction of mandibular incisors has been a very rare finding and has never been noted in similar cases.

journal_name

Clin Genet

journal_title

Clinical genetics

authors

Pfeiffer RA,Hertrich K,Cohen M

doi

10.1111/j.1399-0004.1994.tb04411.x

subject

Has Abstract

pub_date

1994-12-01 00:00:00

pages

430-2

issue

6

eissn

0009-9163

issn

1399-0004

journal_volume

46

pub_type

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