Syndrome of periodic fever, aphthous stomatitis, pharyngitis, and adenitis (PFAPA) in siblings.

Abstract:

:PFAPA syndrome is characterized by episodes of periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis. PFAPA syndrome usually begins in children under 5 years old and normally has self-resolution. The etiology of PFAPA syndrome remains unknown. In this paper, we report the cases of two different families with siblings with PFAPA syndrome: two sisters and two brothers. To our knowledge, this is the first report of siblings with PFAPA syndrome.

journal_name

Clin Rheumatol

journal_title

Clinical rheumatology

authors

Valenzuela PM,Majerson D,Tapia JL,Talesnik E

doi

10.1007/s10067-009-1222-z

subject

Has Abstract

pub_date

2009-10-01 00:00:00

pages

1235-7

issue

10

eissn

0770-3198

issn

1434-9949

journal_volume

28

pub_type

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