Pathophysiology of Neuromuscular Respiratory Diseases.

Abstract:

:Gas exchange between the atmosphere and the human body depends on the lungs and the function of the respiratory pump. The respiratory pump consists of the respiratory control center located in the brain, bony rib cage, diaphragm, and intercostal, accessory, and abdominal muscles. A variety of muscles serve to fine-tune adjustments of ventilation to metabolic demands. Appropriate evaluation and interventions can prevent respiratory complications and prolong life in individuals with neuromuscular diseases. This article discusses normal function of the respiratory pump, general pathophysiologic issues, and abnormalities in more common neuromuscular diseases.

journal_name

Clin Chest Med

authors

Benditt JO

doi

10.1016/j.ccm.2018.01.011

subject

Has Abstract

pub_date

2018-06-01 00:00:00

pages

297-308

issue

2

eissn

0272-5231

issn

1557-8216

pii

S0272-5231(18)30011-X

journal_volume

39

pub_type

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