Abstract:
:Proteus syndrome is an extremely rare mosaic condition characterized by progressive overgrowth of tissues due to a somatic activating mutation of the AKT1 gene. Distinct cutaneous features, including cerebriform connective tissue nevi, epidermal nevi, vascular malformations, and adipose abnormalities, can alert the dermatologist to the underlying condition before the onset of asymmetric skeletal overgrowth. We present a series of photographs documenting the skin and musculoskeletal changes in a patient with Proteus syndrome over the first 2 years of life to emphasize the key signs that a dermatologist can recognize to facilitate an earlier diagnosis in these patients.
journal_name
Pediatr Dermatoljournal_title
Pediatric dermatologyauthors
Rodenbeck DL,Greyling LA,Anderson JH,Davis LSdoi
10.1111/pde.12900subject
Has Abstractpub_date
2016-09-01 00:00:00pages
e306-10issue
5eissn
0736-8046issn
1525-1470journal_volume
33pub_type
杂志文章abstract::A 3 year-old boy presented to our clinic with a 3-day history of itchy rash involving the face and limbs and recent contact with a caterpillar. A diagnosis of caterpillar dermatitis was suspected. This condition has rarely been reported and may be underestimated in the pediatric population who may suffer more systemic...
journal_title:Pediatric dermatology
pub_type: 杂志文章
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更新日期:2020-05-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
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abstract:OBJECTIVES:To compare prevalence and severity of diaper dermatitis (DD) in infants and toddlers (babies) across three countries (China, USA, and Germany), including diapered skin measures and caregiver practices. METHODS:A cross-sectional study of 1791 babies (~600 from each country) was recruited at each clinical sit...
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journal_title:Pediatric dermatology
pub_type: 杂志文章
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更新日期:2020-11-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
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journal_title:Pediatric dermatology
pub_type: 杂志文章
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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pub_type: 杂志文章,评审
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.12296
更新日期:2014-09-01 00:00:00
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journal_title:Pediatric dermatology
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doi:10.1111/j.1525-1470.2006.00291.x
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/j.1525-1470.1996.tb00708.x
更新日期:1996-09-01 00:00:00
abstract:BACKGROUND/OBJECTIVES:Port-wine stains, also known as capillary malformations, are due to dermal vascular ectasia and dilation and are most commonly congenital; however, acquired port-wine stains (APWS) developing later in life have been noted in the literature, most commonly in the context of trauma. METHODS/RESULTS:...
journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.14019
更新日期:2020-01-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/j.1525-1470.1989.tb00919.x
更新日期:1989-12-01 00:00:00
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
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journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
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journal_title:Pediatric dermatology
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更新日期:2011-07-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/j.0736-8046.2004.21114.x
更新日期:2004-01-01 00:00:00
abstract::Fibro-osseous pseudotumor of the digits is a benign neoplasm that originates in the soft tissue adjacent to the short bones of the hands and feet. We present a case in a 13-year-old girl that was initially misdiagnosed as pyogenic granuloma. Familiarity with this entity and imaging and histologic studies are necessary...
journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.13087
更新日期:2017-05-01 00:00:00
abstract::Subcutaneous panniculitis-like T-cell lymphoma (SPTCL) is a type of skin lymphoma. Pleomorphic T-cells infiltrate the subcutaneous tissue and mimic lobular panniculitis. We report a case occurring in a 12-year-old Chinese boy who presented with multiple indolent erythematous subcutaneous nodules on both extremities wi...
journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
doi:10.1111/pde.12452
更新日期:2015-07-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.13190
更新日期:2017-07-01 00:00:00
abstract::In addition to the evaluation of melanocytic growths (Part I), dermoscopy is helpful in the identification and management of vascular tumors, skin infections, and inflammatory conditions. In this practical review, we present the classic dermoscopic findings of the following: vascular tumors, infectious conditions (mol...
journal_title:Pediatric dermatology
pub_type: 杂志文章,评审
doi:10.1111/pde.14284
更新日期:2020-09-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.12664
更新日期:2015-11-01 00:00:00
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journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/j.1525-1470.1994.tb00596.x
更新日期:1994-09-01 00:00:00
abstract:BACKGROUND/OBJECTIVES:Loose anagen syndrome (LAS) is a disorder of abnormal anchorage of the hair to the scalp. Its symptoms include an inability to grow hair long and hair that is easily pulled out. METHODS:We conducted a retrospective chart review of patients with LAS over the last 10 years at the Children's Hospita...
journal_title:Pediatric dermatology
pub_type: 杂志文章
doi:10.1111/pde.12912
更新日期:2016-09-01 00:00:00