Hereditary Hemorrhagic Telangiectasia: A Primer for Critical Care Nurses.

Abstract:

:Hereditary hemorrhagic telangiectasia is a rare, autosomal dominant genetic disease that causes abnormal growth of blood vessels and, subsequently, life-threatening arteriovenous malformations in vital organs. Epistaxis may be one of the initial clues that a patient has more serious, generalized arteriovenous malformations. Recommended treatment involves careful evaluation to determine the severity and risk of spontaneous rupture of the malformations and the management of various signs and symptoms. The disease remains undiagnosed in many patients, and health care providers may miss the diagnosis until catastrophic events happen in multiple family members. Prompt recognition of hereditary hemorrhagic telangiectasia and early intervention can halt the dangerous course of the disease. Critical care nurses can assist with early diagnosis within families with this genetic disease, thus preventing early death and disability.

journal_name

Crit Care Nurse

journal_title

Critical care nurse

authors

Sacco KM,Barkley TW Jr

doi

10.4037/ccn2016270

subject

Has Abstract

pub_date

2016-06-01 00:00:00

pages

36-48

issue

3

eissn

0279-5442

issn

1940-8250

pii

36/3/36

journal_volume

36

pub_type

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