Pediatric lung transplantation and end of life care in cystic fibrosis: Barriers and successful strategies.

Abstract:

:Pediatric lung transplantation has advanced over the years, providing a potential life-prolonging therapy to patients with cystic fibrosis. Despite this, many challenges in lung transplantation remain and result in worse outcomes than other solid organ transplants. As CF lung disease progresses, children and their caregivers are often simultaneously preparing for lung transplantation and end of life. In this article, we will discuss the current barriers to success in pediatric CF lung transplantation as well as approaches to end of life care in this population.

journal_name

Pediatr Pulmonol

journal_title

Pediatric pulmonology

authors

Dellon E,Goldfarb SB,Hayes D Jr,Sawicki GS,Wolfe J,Boyer D

doi

10.1002/ppul.23748

subject

Has Abstract

pub_date

2017-11-01 00:00:00

pages

S61-S68

issue

S48

eissn

8755-6863

issn

1099-0496

journal_volume

52

pub_type

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