Familial recurrent Bell's palsy with ocular motor palsies.

Abstract:

:We studied a family in which the father and 7 of 10 children had episodes of Bell's palsy. Five of the eight affected family members also had ocular motor palsies. Facial nerve and blink reflex studies in four affected siblings demonstrated asymmetrically reduced amplitude of evoked responses without delayed conduction. EMG revealed signs of chronic denervation and reinnervation in all four patients; two had synkinesis. Three siblings had diabetes mellitus, but with no clinically evident polyneuropathy.

journal_name

Neurology

journal_title

Neurology

authors

Aldrich MS,Beck RW,Albers JW

doi

10.1212/wnl.37.8.1369

subject

Has Abstract

pub_date

1987-08-01 00:00:00

pages

1369-71

issue

8

eissn

0028-3878

issn

1526-632X

journal_volume

37

pub_type

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