Megacystis-microcolon-intestinal hypoperistalsis syndrome: survival of a male infant.

Abstract:

:The combination of megacystis with microcolon and severe intestinal hypoperistalsis constitutes a rarely encountered syndrome in neonates. Of 16 previously reported cases, 14 have occurred in females and all but one have been fatal. Various forms of intestinal diversions have been unsuccessful. Aganglionosis has been excluded in every case. A method of management involving prolonged total parenteral nutrition, followed by graduated jejunostomy and gastrostomy feedings, has resulted in the survival of a male infant with this syndrome. No previous male survivors have been reported.

journal_name

J Pediatr Surg

authors

Gillis DA,Grantmyre EB

doi

10.1016/s0022-3468(85)80122-6

subject

Has Abstract

pub_date

1985-06-01 00:00:00

pages

279-81

issue

3

eissn

0022-3468

issn

1531-5037

pii

S0022346885000513

journal_volume

20

pub_type

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