[Ophthalmologic and roentgenologic findings in a rare case of mucopolysaccharidosis 4 B].

Abstract:

:A rare case of mucopolysaccharidosis, i.e., Morquio's disease with spondyloepiphyseal dysplasia, corneal clouding, normal intelligence, and deficiency of beta-galactosidase activity is described.

journal_name

Klin Monbl Augenheilkd

authors

Faschinger C,Schmidberger H

doi

10.1055/s-2008-1054350

subject

Has Abstract

pub_date

1985-11-01 00:00:00

pages

408-10

issue

5

eissn

0023-2165

issn

1439-3999

journal_volume

187

pub_type

杂志文章
  • [A long-term study of morphological and functional developments after central serous chorioretinitis].

    abstract::Of 163 patients suffering from central serous chorioretinopathy, 40 who had been treated by light coagulation and 40 who had been treated conservatively were selected at random. They were examined at intervals averaging 5.7 and 4.6 years respectively after the initial treatment. Central visual acuity, central visual f...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1054851

    authors: Fuhrmeister H

    更新日期:1983-06-01 00:00:00

  • [Circulating immune complexes in uveitis].

    abstract::The serum of 63 patients suffering from various clinical types of endogenous uveitis with unknown etiology was investigated for the presence of circulating immune complexes (CIC). None of the patients was suffering from a systemic disease usually associated with CIC. Significantly elevated CIC levels were detected in ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1054906

    authors: Radda TM,Menzel EJ,Gnad HD

    更新日期:1983-09-01 00:00:00

  • [Chemical and thermal eye burns in the residential area of RWTH Aachen. Analysis of accidents in 1 year using a new automated documentation of findings].

    abstract:BACKGROUND:Until now there were no statistical data on the incidence and the prevalence of eye burns. Therefore we studied all patients coming to our hospital from the area of Aachen with eye burns during the time from September 1990 until August 1991. PATIENTS AND METHODS:All patients underwent a standardized examina...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1045646

    authors: Kuckelkorn R,Luft I,Kottek AA,Schrage NF,Makropoulos W,Reim M

    更新日期:1993-07-01 00:00:00

  • [Acute reversible night blindness caused by vitamin A deficiency in pancreatic carcinoma].

    abstract:BACKGROUND:Vitamin A deficiency is a leading cause of blindness in childhood in the developing countries. In developed countries xerophthalmia occurs mainly as secondary hypovitaminosis due to malabsorption in chronic alcoholism or intestinal disorders. PATIENT AND METHODS:A 24-year-old female patient complained of ni...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1034956

    authors: Schönherr U

    更新日期:1998-08-01 00:00:00

  • [Use of a new anomaloscope test in diagnosis of glaucoma].

    abstract:BACKGROUND:The Color Vision Meter 712 (CVM) is a new automatic computerized anomaloscope relying on both the Rayleigh and the Moreland equation. In the present study the diagnostic value of Color Vision Meter was examined in glaucoma for the first time and was compared with the Farnsworth 100 hue test. PATIENTS AND ME...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1035512

    authors: Nguyen NX,Korth M,Wisse M,Jünemann A

    更新日期:1994-03-01 00:00:00

  • [Efficiency and Therapy Safety of Fractionated Cyclophotocoagulation with up to Ten Laser Spots for Advanced Primary Open-Angle and Pseudoexfoliation Glaucoma].

    abstract:BACKGROUND:Various procedures are available for the treatment of advanced glaucoma. We examined the efficacy and safety of fractionated cyclophotocoagulation (CPC) with up to ten laser spots for advanced primary open-angle glaucoma (POAG) and pseudoexfoliation (PEX) glaucoma treated with maximal topical therapy or eye-...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/a-1057-9699

    authors: Grohmann C,Farrokhi S,Klemm M

    更新日期:2020-02-03 00:00:00

  • [Cryptophthalmos solum corneae].

    abstract::The authors report on an 11-month-old child in whom subcutaneous fatty tissue covered with normal skin was found instead of a cornea. Since the lid and conjunctiva were intact this developmental anomaly may be designated cryptophthalmos solum corneae. ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1046162

    authors: Alberth B,el Zein G

    更新日期:1990-04-01 00:00:00

  • [Changes in corneal topography after using tear substitutes].

    abstract:BACKGROUND:Computer-controlled video keratoscopy is being employed ever more frequently and for various indications. PATIENTS:We have studied the effects of high-viscosity and low-viscosity tear substitutes on the corneal topography, one and five minutes after application to 14 normal eyes of 7 subjects, and compared ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1035260

    authors: Emde CW,Brewitt H,Winter R

    更新日期:1996-06-01 00:00:00

  • [The clinical course of an embolism of a branch of the retinal artery (author's transl)].

    abstract::The way in which a varying amount of blood runs past an almost obliterating yellowish-grey, homogenous "embolus" in a branch of the artery is shown. Finally although the "embolus" remained, there was an almost normal blood flow in amount. Retinal arteries running downwards showed changing vascular spasms, sometimes a...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Pau H

    更新日期:1978-09-01 00:00:00

  • [Treatment of retinal detachment with macular hole: scleral buckling with an absorbable fibrin sponge (author's transl)].

    abstract::In 21 patients with macular hole and retinal detachment a macular buckling procedure was performed including diathermic or cryogenic coagulation. An absorbable fibrin sponge (Fibrospum) was used as a new buckling material, which needs not to be sutured to the sclera at the posterior pole. In comparison to other proced...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Wollensak J,Engels T

    更新日期:1977-08-01 00:00:00

  • [Controlled hypotension by sodium-nitroprusside in general anaesthesia for difficult intraocular surgery (preliminary report) (author's transl)].

    abstract::General anaesthesia was performed in 75 patients with difficult intraocular procedures in which the standard relaxation and hyperventilation was supplemented by controlled short-term hypotension by sodium-nitroprusside. This resulted in a significant decrease of the "vis a tergo"--e.g. the threatening prolaps of intra...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Naumann GO,Eisert S,Gieler J,Baur KF

    更新日期:1977-06-01 00:00:00

  • [Treatment of central retinal venous and arterial occlusion by isovolemic hemodilution (author's transl)].

    abstract::(1) Ten patients (mean age 71) with fully developed central retinal venous occlusion were treated by isovolemic hemodilution over a period of four to six weeks. Hematocrit was lowered in steps to about 30% to improve retinal microcirculation. For two to four days, 500 ml whole blood were exchanged daily for about 250 ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1057628

    authors: Wiederholt M,Leonhardt H,Schmid-Schönbein H,Hager H

    更新日期:1980-01-01 00:00:00

  • [The usefulness of echography in retinal surgery (author's transl)].

    abstract::Upon utilization of echography one certainly will not be able to detect retinal defects; however, other parameters of retinal detachment which by means of solely optical examination techniques may remain undiagnosed can be evaluated successfully. This concerns not only the diagnosis of retinal detachment alone but als...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Freyler H

    更新日期:1979-03-01 00:00:00

  • [Structures of the European union--possibilities for influence by medical societies].

    abstract::In the EU more than 70 % of national law has already been replaced by EU law. Medical doctors are mostly not informed, how these EU-laws will pass. Many directives, regulations and decisions are important for medical doctors. A characterization of the EU- institutions is represented. ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2005-858749

    authors: Grewe R

    更新日期:2005-11-01 00:00:00

  • [Therapy of herpetic diseases of the anterior eye segment].

    abstract::Clinico-virologic investigations and the availability of the new antiviral drug Acyclovir have changed our therapeutic approach to deep herpetic diseases. Treatment of the symptoms alone with steroids should now be avoided. Basic treatment should consist of optimal dosages of Acyclovir. However, additional steroid the...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1050949

    authors: Sundmacher R

    更新日期:1985-06-01 00:00:00

  • [Juvenile cataract associated with microcornea and glucosuria: a new syndrome].

    abstract:BACKGROUND:Predisposition is responsible for approximately 50% of age-related cataracts. Investigation of inherited forms of cataract provides the opportunity to identify the genes that may play a role in age-related cataract as well. PATIENTS AND METHODS:We describe the phenotype of a Swiss family with juvenile catar...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2007-962943

    authors: Vandekerckhove K,Lange AP,Herzog D,Schipper I

    更新日期:2007-04-01 00:00:00

  • [The effects of the xenon arc lamp upon the iris of the pigmented rabbit eye (author's transl)].

    abstract::The ultrastructural alterations of 10 pigmented rabbit irides 15 minutes to 257 days after irradiation with a xenon arc lamp were analysed. Pulse duration was varied while irradiation power was kept constant at 3.24 W. 0.32 J (= 100 ms pulse duration) were delivered to the left eye and 3.2 J (= 1 second pulse duration...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Bernhard K,van der Zypen E,Fankhauser F

    更新日期:1979-06-01 00:00:00

  • [Gene replacement therapy in achromatopsia type 2].

    abstract::Achromatopsia is an autosomal recessive inherited retinal disease caused by a complete loss of cone photoreceptor function. About 80 % of achromatopsia patients show mutations in the alpha or beta subunit (A3 and B3) of the cGMP controlled cation channel CNG (cyclic nucleotide-gated channel) of cone photoreceptors. Ho...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章,评审

    doi:10.1055/s-0034-1368180

    authors: Mühlfriedel R,Tanimoto N,Seeliger MW

    更新日期:2014-03-01 00:00:00

  • Assessment and classification of choroidal vasculitis in posterior uveitis using indocyanine green angiography.

    abstract:BACKGROUND:By allowing one to detect fluorescence beyond the retinal pigment epithelium, indocyanine green angiography (ICGA) has made it possible to analyse the choroidal vessels. Our aim was to characterize choroidal vasculitis in posterior uveitis using ICGA. METHODS:Charts of active posterior uveitis patients with...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2002-30661

    authors: Bouchenaki N,Cimino L,Auer C,Tao Tran V,Herbort CP

    更新日期:2002-04-01 00:00:00

  • [Hema socket expander in primary conservative treatment of congenital anophthalmos].

    abstract::In anophthalmos the forces which stimulate development and growth of the bony orbit are absent. As a result these cases have not only a tiny socket but also an underdeveloped bony orbit, which cannot retain an artificial eye. The small conjunctival sac and bony orbit can be mechanically enlarged by means of Hema socke...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1050502

    authors: Steinkogler FJ,Polzhofer K

    更新日期:1987-09-01 00:00:00

  • [Polyglycolic acid suture in strabismus surgery (author's transl)].

    abstract::We report on 60 patients who underwent altogether 100 operations on their eye muscles, either recession or resection of a lateral rectus muscle, or both operations together. All muscles were sutured with 5-0 Dexon, and the conjunctivae with 7-0 Dexon. The postoperative reaction was studied. This suture material produc...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1057640

    authors: Demmler N

    更新日期:1980-01-01 00:00:00

  • [Clinical and fluorescein angiography findings in patients with retinal vein occlusion. A unicenter study of 211 patients].

    abstract::Between january 1986 and december 1989 we prospectively studied 211 patients with branch retinal vein occlusion (BRVO). Documented by fundus photography and fluorescein angiography clinical and angiographic findings were analysed. The age ranged from 28 to 83 with a mean of 63 years. 104 (48.8%) patients were male, 10...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1045901

    authors: Lang GE,Freissler K

    更新日期:1992-10-01 00:00:00

  • [Switching the Treatment Regime from PRN (pro re nata, as needed) to T&E (Treat and Extend) for Intravitreal Therapy with Anti-VEGF Agents in Private Practice or Small Institutions].

    abstract::In everyday practice, intravitreal therapy in an "as needed" regimen (pro re nata, PRN) is less predictable and requires more visits (monitoring and injections taken together) with poorer functional results than with the treat and extend (T&E) regimen. Current literature supports the benefit of a switch. However, prac...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章,评审

    doi:10.1055/s-0042-118184

    authors: Imesch P,Sarra GM

    更新日期:2018-01-01 00:00:00

  • [Basic in vitro studies on VEGF inhibition with aflibercept: similarities and differences to other VEGF-binding therapeutic proteins].

    abstract::Patients suffering from various retinal diseases benefit from therapies directed against the vascular endothelial growth factor (VEGF). Aflibercept (Eylea) is another VEGF-binding protein available for intravitreal injection, in addition to the antibody bevacizumab (Avastin) and the F(ab) fragment ranibizumab (Lucenti...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章,评审

    doi:10.1055/s-0034-1383142

    authors: Lang GE,Lang GK,Deissler HL

    更新日期:2015-03-01 00:00:00

  • [Combined phacoemulsification with trabecular aspiration with differing outcomes in pseudoexfoliative glaucoma - a retrospective study].

    abstract:INTRODUCTION:The aim of this study was to differentiate the pressure-reducing results following trabecular aspiration combined with small incision cataract surgery in eyes with pseudoexfoliation depending on preoperative pressure and medication score. PATIENTS AND METHODS:A retrospective analysis was made of 104 exfol...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-0031-1282014

    authors: Dinslage S,Rosentreter A,Schild AM,Jordan JF,Widder R,Dietlein TS

    更新日期:2012-06-01 00:00:00

  • [Correspondence alterations due to tenomyotomy (author's transl)].

    abstract::This report covers 310 patients with concomitant convergent strabismus and anomalous retinal correspondence. In 36 cases tenomyotomy alone was responsible for normalization of correspondence. This is best achieved in cases of bilateral converging strabismus without vertical divergence. ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Schellenbeck R,Schmidt I

    更新日期:1979-08-01 00:00:00

  • [NF2: ocular, neural and genetic manifestations].

    abstract::Neurofibromatosis 2 is an autosomal-dominant disease, which is characterized by vestibular schwannomas, cataract, retinal hamartomas as well as tumors of the peripheral and central nerve system, demonstrating a variety of expression. The ophthalmologist plays an important role in making the diagnosis, as several ocula...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章,评审

    doi:10.1055/s-2005-857956

    authors: Feucht M,Mautner VF,Richard G

    更新日期:2005-04-01 00:00:00

  • [Lamellar keratoplasty, ipsilateral rotation-autokeratoplasty and contralateral autokeratoplasty (author's transl)].

    abstract::During the years 1967--1977, there were performed about 500 mostly perforating keratoplasties. Among these there were special groups: 50 lamellar keratoplasties (43 central, 7 marginal), 5 perforating ipsilateral rotation-autokeratoplasties 2 perforating contralateral autokeratoplasties. The results encourage to use t...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:

    authors: Doden W,Schmitt H,Welt R

    更新日期:1978-10-01 00:00:00

  • [Reasonableness of surgical interventions and compliance responsibilities in various insurance fields and under the social compensation law].

    abstract::According to the German Social Legal Code I (I. Sozialgesetzbuch, SGB I) the recipient of social benefits is under obligation to submit to medical treatment if such treatment would result in an improvement of his/her condition or in the prevention of further deterioration (section 63 SGB I). In certain situations, lac...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章

    doi:10.1055/s-2008-1050624

    authors: Thomann H

    更新日期:1986-03-01 00:00:00

  • [Autoimmune diseases of the peripheral cornea. Immunopathology, clinical aspects and therapy].

    abstract::Noninfectious ulceration of the peripheral cornea remains a major diagnostic and therapeutic challenge. The pathogenesis in most of these disorders is unclear, however, on the basis of systemic connective tissue diseases, autoimmune mechanisms are most likely involved. The peripheral cornea has distinct morphological ...

    journal_title:Klinische Monatsblatter fur Augenheilkunde

    pub_type: 杂志文章,评审

    doi:10.1055/s-2008-1035173

    authors: Pleyer U,Bergmann L,Krause A,Hartmann C

    更新日期:1996-02-01 00:00:00