Rapp-Hodgkin syndrome with pili canaliculi.

abstract：:An 8-year-old girl had Crohn's disease of the vulva 16 months before the onset of intestinal symptoms. At the time of diagnosis she had no evidence of systemic disease. Cutaneous and intestinal lesions responded rapidly to corticosteroids and metronidazole. Crohn's disease must be considered in the differential diagno...

journal_title：Pediatric dermatology

authors： Lally MR,Orenstein SR,Cohen BA

更新日期：1988-05-01 00:00:00

abstract：:Hypertrichosis cubiti, also named hairy elbows syndrome (HES), is an uncommon variety of congenital, circumscribed hypertrichosis in which a remarkable amount of long vellus hair is localized on the extensor surfaces of the upper extremities. Usually, this condition appears in infancy, increases during early childhood...

journal_title：Pediatric dermatology

authors： Escalonilla P,Aguilar A,Gallego M,Piqué E,Fariña MC,Requena L

更新日期：1996-07-01 00:00:00

abstract：:Mutations in the p63 gene have been identified in five human disorders characterized by varying degrees of limb anomalies, ectodermal dysplasia, and facial clefts. We report a new point mutation in the p63 gene in a family in which the mother was initially diagnosed with Rapp-Hodgkin syndrome and her two offspring man...

journal_title：Pediatric dermatology

authors： Steele JA,Hansen H,Arn P,Kwong PC

更新日期：2005-09-01 00:00:00

abstract：BACKGROUND:Bullous impetigo (BI) is a common skin infection of early childhood, resulting from desmoglein-1 cleavage by Staphylococcus aureus exfoliative toxins. Due to compromised barrier function and immune dysregulation, children with atopic dermatitis (AD) are at increased risk of cutaneous infections, yet no liter...

journal_title：Pediatric dermatology

authors： Mannschreck D,Feig J,Selph J,Cohen B

更新日期：2020-01-01 00:00:00

abstract：:Diaper dermatitis, an acute inflammation of the skin in the diaper area, is the most common dermatologic disorder of infancy. This placebo-controlled, randomized, double-blind, parallel-group trial compared the efficacy and safety of miconazole nitrate 0.25% in a zinc oxide/petrolatum base with that of the ointment ba...

journal_title：Pediatric dermatology

authors： Concannon P,Gisoldi E,Phillips S,Grossman R

更新日期：2001-03-01 00:00:00

abstract：:Keratitis ichthyosis deafness syndrome is a rare congenital ectodermal disorder. It appears to be genetically heterogeneous and may be caused by mutations in the connexin 26 (Cx26) gene (GJB2) or in the connexin 30 gene. It is characterized by the association of ichthyosis-like skin lesions, hearing loss, and vascular...

journal_title：Pediatric dermatology

authors： De Raeve L,Bonduelle M,Deconinck H,Roseeuw D,Stene JJ

更新日期：2008-07-01 00:00:00

abstract：:A newborn male Thai infant had numerous brownish red nodules of various sizes scattered over both palms and soles, left thigh, abdomen, chin, and left upper eyelid. An extremely large tumor mass was present on the right sole. Many lesions showed spontaneous ulceration. No extracutaneous involvement was found. All lesi...

journal_title：Pediatric dermatology

authors： Timpatanapong P,Rochanawutanon M,Siripoonya P,Nitidandhaprabhas P

更新日期：1989-03-01 00:00:00

abstract：:Cutaneous xanthomas develop as a result of lipid deposition in the dermis and may be a manifestation of various systemic diseases. The morphology and anatomic location of xanthomas are often a clue to the underlying cause. Xanthoma striatum palmare (XSP) is classically associated with dysbetalipoproteinemia and rarely...

journal_title：Pediatric dermatology

authors： Joner Mattias F,Escobar GF,Peruzzo J

更新日期：2020-09-01 00:00:00

abstract：:Papular epidermal nevus with "skyline" basal cell layer (PENS), a variant of epidermal nevus, was recently described in otherwise normal children. We describe herein a patient with multiple, typical PENS lesions associated with peculiar facies, bilateral Achilles tendon shortening, and mild psychomotor delay. The asso...

journal_title：Pediatric dermatology

authors： Rodríguez-Díaz E,Gonzalvo P,Colmenero I,Requena L,Hernández-Martín A,Torrelo A

更新日期：2013-07-01 00:00:00

abstract：:We present a 16-year-old girl with a 4-year history of chronic persistent erythema nodosum. Recurrently low serum iron values suggested the possibility of a malabsorption syndrome. The presence of antitransglutaminase and antiendomysium antibodies and the jejunal biopsy specimen findings showed an underlying celiac di...

journal_title：Pediatric dermatology

authors： Bartyik K,Várkonyi A,Kirschner A,Endreffy E,Túri S,Karg E

更新日期：2004-05-01 00:00:00

abstract：:Cutaneous tuberculosis is a rare form of extrapulmonary tuberculosis that accounts for 1% to 2% of cases. Childhood skin tuberculosis represents 18% to 82% of all cutaneous tuberculosis cases. Scrofuloderma and lupus vulgaris are the two most common clinical forms in children. An increase in the number of tuberculids,...

journal_title：Pediatric dermatology

authors： Sethuraman G,Ramesh V

更新日期：2013-01-01 00:00:00

abstract：:Over the years, the application and complications of radiofrequency ablation (RFA) in selective fetal reduction for complex pregnancies have been increasingly documented. Despite its rising use in the field of obstetrics and gynecology, the cutaneous complications of RFA have not been commonly reported. Here, we prese...

journal_title：Pediatric dermatology

authors： Law JY,Choi EC,Chandran NS

更新日期：2020-11-01 00:00:00

abstract：BACKGROUND/OBJECTIVES:Atypical and severe clinical manifestations of primary and recurrent herpes simplex virus (HSV) infections may present to a pediatric dermatologist for evaluation. The purpose of this study was to characterize the clinical features of the population diagnosed with HSV referred to a pediatric derma...

journal_title：Pediatric dermatology

authors： Gittler JK,Mu EW,Orlow SJ

更新日期：2017-07-01 00:00:00

abstract：BACKGROUND/OBJECTIVES:Stevens-Johnson syndrome (SJS) and toxic epidermal necrolysis (TEN) are medical emergencies. Mainstays of treatment include removal of the offending agent, supportive care, and wound care. The use of immunosuppressive agents such as corticosteroids and intravenous immunoglobulin (IVIg) is controve...

journal_title：Pediatric dermatology

authors： St John J,Ratushny V,Liu KJ,Bach DQ,Badri O,Gracey LE,Ho AW,Raff AB,Sugai DY,Schalock P,Kroshinsky D

更新日期：2017-09-01 00:00:00

abstract：:A 2-year-old boy had hundreds of discrete, small, flat yellow to brown colored papules distributed over the face, neck, and trunk. Biopsy revealed a well-demarcated infiltrate within the papillary dermis composed of histiocytes and some Touton giant cells and eosinophils. The cells were negative for protein S-100 and ...

journal_title：Pediatric dermatology

authors： Torrelo A,Juarez A,Hernández A,Colmenero I

更新日期：2009-03-01 00:00:00

abstract：:Subcutaneous fat necrosis (SFN) of the newborn is uncommon and usually occurs in the first weeks of life following a complicated delivery. The frequency with which hypercalcemia develops as a complication is uncertain. We report the clinical features of SFN in 11 patients seen between 1991 and 1998. Ten were born by c...

journal_title：Pediatric dermatology

authors： Burden AD,Krafchik BR

更新日期：1999-09-01 00:00:00

abstract：:Melanonychia striata in childhood is primarily due to congenital nevi, but melanoma should be excluded. We report a case in which dermoscopy was used in an attempt to avoid incisional biopsy. ...

journal_title：Pediatric dermatology

authors： Lazaridou E,Giannopoulou C,Fotiadou C,Demiri E,Ioannides D

更新日期：2013-11-01 00:00:00

abstract：:We evaluated the prevalence of acanthosis nigricans among urban youth. Youth (7-17 years) at nine pediatric practices completed surveys on demographics and family history of diabetes and had weight and height measured. Acanthosis nigricans was scored and digital photography of the neck performed. A total of 618 youth ...

journal_title：Pediatric dermatology

authors： Brickman WJ,Binns HJ,Jovanovic BD,Kolesky S,Mancini AJ,Metzger BE,Pediatric Practice Research Group.

更新日期：2007-11-01 00:00:00

abstract：:Verrucous perforating collagenoma is an extremely rare variant of acquired perforating dermatosis that has been seldom described in literature. We present the case of an 18-month-old boy who presented with an erythematous plaque with a central keratotic plug on the leg. Histopathology revealed transepidermal eliminati...

journal_title：Pediatric dermatology

authors： Aizman L,Gelman A,Marathe K

更新日期：2019-09-01 00:00:00

abstract：:Pemphigus refers to a group of potentially fatal blistering skin diseases that are often due to the deleterious effects of autoantibodies directed against desmosomal antigens. Although desmogleins have been mainly implicated as autoantigens in pemphigus, a steadily growing body of evidence suggests that other desmosom...

journal_title：Pediatric dermatology

authors： Geller S,Gat A,Harel A,Mashiah J,Zeeli T,Eming R,Ishii N,Hertl M,Hashimoto T,Sprecher E

更新日期：2016-01-01 00:00:00

abstract：:We describe a bullous-hemorrhagic reaction of the ear lobes in a child with nephrosis after levamisole intake. This drug is used in children as an alternative treatment of corticosteroid-responsive nephrotic syndrome. Histologic evaluation of a lesion revealed necrotizing vasculitis involving mainly the large vessels ...

journal_title：Pediatric dermatology

authors： Menni S,Pistritto G,Gianotti R,Ghio L,Edefonti A

更新日期：1997-11-01 00:00:00

abstract：:Phacomatosis pigmentovascularis is characterized by coexistent extensive cutaneous vascular (capillary) and pigmentary anomalies. We describe a 2-month-old infant presenting with classic features of phacomatosis pigmentovascularis 2b (phacomatosis cesioflammea). He was also found to have hitherto unreported associatio...

journal_title：Pediatric dermatology

authors： Singal A,Mittal H,Aggarwal A,Das S,Manchanda S

更新日期：2018-05-01 00:00:00

abstract：:Intralesional corticosteroid injections are frequently used to treat various musculoskeletal and dermatologic conditions, including keloid scarring. While a number of adverse events may be associated with these injections, hypopigmentation without atrophy is rare. We report a case of a pediatric patient with temporary...

journal_title：Pediatric dermatology

authors： Bjorklund KA,Fernandez Faith E

更新日期：2020-01-01 00:00:00

abstract：:Although the U.S. pediatric skin care market is a $1.7 billion industry, little is known regarding the usage pattern of skin care products in very young children. We have begun to recognize that common over-the-counter skin care products may have positive or negative effects on skin barrier function. Thus, knowing wha...

journal_title：Pediatric dermatology

authors： Gao X,Simpson EL

更新日期：2014-11-01 00:00:00

abstract：BACKGROUND:Spiny hyperkeratosis refers to a rare clinical phenotype characterized by nonfollicular keratotic projections and sometimes associated with other acquired and inherited conditions. We describe a case of congenital patterned spiny hyperkeratosis. METHODS:To identify the cause of this disorder, we used a comb...

journal_title：Pediatric dermatology

authors： Eskin-Schwartz M,Metzger Y,Peled A,Weissglas-Volkov D,Malchin N,Gat A,Vodo D,Mevorah B,Shomron N,Sprecher E,Sarig O

更新日期：2016-05-01 00:00:00

abstract：:We report a case of a young man with perforating folliculitis and cystic fibrosis with complications including chronic obstructive pulmonary disease, insulin dependent diabetes mellitus, and liver cirrhosis. We demonstrate increased TGF-β1 immunohistochemical staining in the perforating folliculitis lesions of our pat...

journal_title：Pediatric dermatology

authors： Tuttle MS,Kwon EJ,Tamburro J,Honda K

更新日期：2010-11-01 00:00:00

abstract：:One hundred and twenty-one children with plantar warts were treated with a topical preparation containing salicylic acid, 30%; podophyllin, 5%; and cantharidin, 1%. One hundred patients or their families were reached 6 months to 1 year later. This treatment was effective in 81 cases. ...

journal_title：Pediatric dermatology

authors： Coskey RJ

更新日期：1984-07-01 00:00:00

abstract：:Apocrine chromhidrosis is a rare disease frequently localized to the face or axillae, and rarely has been reported to occur around the breasts. We report a 15-year-old amateur figure skater who displayed localized chromhidrosis around her areolae. The most common precipitating event was exercise. She was treated topic...

journal_title：Pediatric dermatology

authors： Saff DM,Owens R,Kahn TA

更新日期：1995-03-01 00:00:00

abstract：:Phrynoderma is a distinctive form of follicular hyperkeratosis associated with nutritional deficiency. Although originally thought to represent vitamin A deficiency, several studies have demonstrated multiple etiologies. Characteristic skin lesions are hyperkeratotic papules that first appear on the extensor surfaces ...

journal_title：Pediatric dermatology

authors： Maronn M,Allen DM,Esterly NB

更新日期：2005-01-01 00:00:00

abstract：:Benign cephalic histiocytosis is a rare skin condition consisting of small tan papules on the face and upper trunk that is believed not to be associated with internal organ involvement. The infiltrating histiocytes are not Langerhans' cells (LCs). We report a 5-year-old girl who presented with diabetes insipidus 1 yea...

journal_title：Pediatric dermatology

authors： Weston WL,Travers SH,Mierau GW,Heasley D,Fitzpatrick J

更新日期：2000-07-01 00:00:00