Abstract:
:A 5-year-old girl developed cardiopulmonary arrest after crying. From the electrocardiogram and echocardiography, a left ventricular noncompaction (LVNC) with long QT syndrome (LQT) was suspected as the cause of the cardiopulmonary arrest, and treatment with a β-blocker and a calcium antagonist was then begun. A genetic screening of LQT-related genes revealed a previously reported heterozygous KCNQ1 mutation. The association of LVNC and LQT is an extremely rare condition, and long-term treatment based on the characteristics of both disorders is required. Also, the association of cardiomyopathy and LQT could become a new clinical entity in the future.
journal_name
Heart Vesselsjournal_title
Heart and vesselsauthors
Nakashima K,Kusakawa I,Yamamoto T,Hirabayashi S,Hosoya R,Shimizu W,Sumitomo Ndoi
10.1007/s00380-012-0235-8subject
Has Abstractpub_date
2013-01-01 00:00:00pages
126-9issue
1eissn
0910-8327issn
1615-2573journal_volume
28pub_type
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