Abstract:
:We report on a 16-year-old girl with muscular atrophy of a distal upper extremity (Hirayama disease). The disease progressed insidiously, and during our first examination, she exhibited weakness and wasting in the right hand, accompanied by cold paresis. No sensory disturbance was evident. A nerve conduction test revealed reduced compound muscle action potential of the ulnar and median nerves of the affected hand. However, conduction velocities were normal. An F-wave test of the right ulnar nerve indicated reduced frequency and prolonged minimum latency. Magnetic resonance imaging of the cervical spinal cord demonstrated abnormal signal intensity in the anterior horn, atrophy in the lower cervical cord, a forward shift of the lower cervical cord upon neck flexion, and flow voids in the epidural space. These clinical findings are typical of Hirayama disease. The use of a cervical collar did improve the patient's hand strength after 2 years. Pediatric neurologists should be aware of this disease, particularly in its early course, to diagnose it early, and to introduce a neck cervical collar as soon as possible after diagnosis.
journal_name
Pediatr Neuroljournal_title
Pediatric neurologyauthors
Hosokawa T,Fujieda M,Wakiguchi H,Oosaki Ydoi
10.1016/j.pediatrneurol.2010.03.015subject
Has Abstractpub_date
2010-08-01 00:00:00pages
151-3issue
2eissn
0887-8994issn
1873-5150pii
S0887-8994(10)00147-5journal_volume
43pub_type
杂志文章abstract::Transcranial magnetic stimulation and motor performance tests were used to study the correlation between corticospinal maturation and actual motor performance in a group of young school children (n = 10, mean age = 7 years, age range = 6-9 years). The results were compared with normal adults (n = 10, mean age = 24 yea...
journal_title:Pediatric neurology
pub_type: 临床试验,杂志文章
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更新日期:1998-09-01 00:00:00
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
pub_type: 杂志文章
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pub_type: 杂志文章,随机对照试验
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journal_title:Pediatric neurology
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/s0887-8994(99)00082-x
更新日期:1999-10-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/0887-8994(89)90013-1
更新日期:1989-01-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/s0887-8994(03)00270-4
更新日期:2003-10-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/s0887-8994(97)89979-1
更新日期:1997-04-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
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更新日期:2016-10-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2013.09.002
更新日期:2014-01-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章,评审
doi:10.1016/j.pediatrneurol.2015.01.016
更新日期:2015-06-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/0887-8994(92)90039-2
更新日期:1992-03-01 00:00:00
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pub_type: 临床试验,杂志文章
doi:10.1016/j.pediatrneurol.2008.04.007
更新日期:2008-08-01 00:00:00
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pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2011.04.007
更新日期:2011-09-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
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更新日期:2016-08-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 临床试验,杂志文章,随机对照试验
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更新日期:1985-01-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2009.05.009
更新日期:2009-11-01 00:00:00
abstract::Central nervous system manifestations of acute myeloid leukemia are rare at presentation. Acute cranial nerve findings on neurologic examination can be indications for brain imaging. Magnetic resonance imaging can highlight cranial nerves emerging from the brainstem, particularly if they are gadolinium-enhanced or thi...
journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2012.08.007
更新日期:2012-11-01 00:00:00
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journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2015.01.007
更新日期:2015-05-01 00:00:00
abstract::Serial examination of the cerebral hemispheres of 20 sudden infant death syndrome victims revealed high incidence of leukomalacia (40%), leptomeningeal glioneuronal heterotopias (70%) at the base of the cerebrum, and astrogliosis (65%) in the white matter and medulla reticular formation compared with 20 age-matched co...
journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/s0887-8994(98)00008-3
更新日期:1998-07-01 00:00:00
abstract:BACKGROUND:Concern exists regarding a possible harmful impact of vacuum extraction on the preterm newborn. We aimed to evaluate the long-term pediatric neurodevelopmental outcomes of the preterm offspring after vacuum extraction. METHODS:A population-based cohort analysis was performed comparing the risk for long-term...
journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2018.12.010
更新日期:2019-05-01 00:00:00
abstract::This report presents a new mutation in the first Japanese female infant with spinal muscular atrophy with respiratory distress type 1. She manifested the characteristic clinical features, including early-onset respiratory failure due to diaphragmatic paralysis and severe distal muscle weakness. Muscle biopsy in the fe...
journal_title:Pediatric neurology
pub_type: 杂志文章
doi:10.1016/j.pediatrneurol.2004.11.003
更新日期:2005-04-01 00:00:00